Pathological characteristics of skeletal muscle in Ullrich's disease with collagen VI deficiency

Neuromuscular Disorders

Volumn 13, Issue 4, 2003, Pages 310-316

  Higuchi, Itsuro ^a   Horikiri, Takashi ^a   Niiyama, Takahito ^a   Suehara, Masahito ^b   Shiraishi, Tadafumi ^a   Hu, Jing ^a   Uchida, Yuichi ^a   Saito, Akiko ^a   Nakagawa, Masanori ^a   Arimura, Kimiyoshi ^a   Osame, Mitsuhiro ^a  

^a KAGOSHIMA UNIVERSITY   (Japan)

^b National Hospital Organization Okinawa National Hospital   (Japan)

Author keywords

Collagen VI; Maturation; Myosin heavy chain; Regeneration; Thrombomodulin; Triple helical domain; Ullrich's disease

Indexed keywords

BIOLOGICAL MARKER; COLLAGEN TYPE 6; DESMIN; MONOCLONAL ANTIBODY; MYOSIN HEAVY CHAIN; NERVE CELL ADHESION MOLECULE; SCLEROPROTEIN; THROMBOMODULIN;

ADULT; ARTICLE; CASE REPORT; COLLAGEN DEFECT; DIAGNOSTIC PROCEDURE; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; IMMUNOREACTIVITY; MALE; MUSCLE CELL; MUSCLE REGENERATION; MYOPATHY; NEWBORN; PRIORITY JOURNAL; PROTEIN EXPRESSION; TURNER SYNDROME;

EID: 0041525512     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0960-8966(02)00282-1     Document Type: Article

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