Increased copper levels in in vitro and in vivo models of Niemann-Pick C disease

BioMetals

Volumn 25, Issue 4, 2012, Pages 777-786

  Vázquez, Mary Carmen ^a   Martínez, Pablo ^a   Alvarez, Alejandra R ^b   González, Mauricio ^c,d,e   Zanlungo, Silvana ^a,d  

^a PONTIFICIA UNIVERSIDAD CATÓLICA DE CHILE   (Chile)

^b PONTIFICIA UNIVERSIDAD CATÓLICA DE CHILE   (Chile)

^c UNIVERSITY OF CHILE   (Chile)

^d FONDAP Center for Genome Regulation (CGR)   (Chile)

^e Center for Mathematical Modeling   (Chile)

Author keywords

Ceruloplasmin; Copper; Liver; Niemann Pick type C

Indexed keywords

CERULOPLASMIN; COPPER;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CEREBELLUM; CONTROLLED STUDY; COPPER BLOOD LEVEL; GENE; GENE MUTATION; HEPATOMA CELL; HOMEOSTASIS; HUMAN; HUMAN CELL; IN VITRO STUDY; IN VIVO STUDY; MALE; MOUSE; NIEMANN PICK DISEASE; NONHUMAN; NPC1 GENE; NPC2 GENE; PHENOTYPE; PROTEIN BINDING; PROTEIN BLOOD LEVEL; RAT;

ANIMALIA; EPICOCCUM; MUS;

EID: 84864951534     PISSN: 09660844     EISSN: 15728773     Source Type: Journal    
DOI: 10.1007/s10534-012-9546-6     Document Type: Article

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