Suppression of calbindin-D28k expression exacerbates SCA1 phenotype in a disease mouse model

Cerebellum

Volumn 11, Issue 3, 2012, Pages 718-732

  Vig, Parminder J S ^a   Wei, Jinrong ^a   Shao, Qingmei ^a   Lopez, Maripar E ^a   Halperin, Rebecca ^b   Gerber, Jill ^c  

^a UNIVERSITY OF MISSISSIPPI SCHOOL OF MEDICINE   (United States)

^b ARIZONA STATE UNIVERSITY   (United States)

^c TRANSLATIONAL GENOMICS RESEARCH INSTITUTE   (United States)

Author keywords

Ataxin 1; Calcium binding proteins; Neurodegeneration; Purkinje cells; Spinocerebellar ataxia

Indexed keywords

CALBINDIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CALCIUM HOMEOSTASIS; CONTROLLED STUDY; DOWN REGULATION; ENZYME REPRESSION; GENE EXPRESSION PROFILING; HETEROZYGOSITY; IMMUNOBLOTTING; IMMUNOREACTIVITY; INTERNEURON; MALE; MOTOR COORDINATION; MOUSE; NONHUMAN; PATHOGENESIS; PHENOTYPE; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; PROTEIN LOCALIZATION; SIGNAL TRANSDUCTION; SPINOCEREBELLAR ATAXIA TYPE 1; SPINOCEREBELLAR DEGENERATION; TRANSCRIPTION REGULATION; TRANSGENE;

ANIMALS; BEHAVIOR, ANIMAL; BLOTTING, WESTERN; CALCIUM-BINDING PROTEIN, VITAMIN D-DEPENDENT; CELL MEMBRANE; CELL NUCLEUS; CYTOSOL; DNA FOOTPRINTING; FEMALE; IMMUNOHISTOCHEMISTRY; MALE; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICROARRAY ANALYSIS; MUTATION; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; PARVALBUMINS; PHENOTYPE; POLYMERASE CHAIN REACTION; POSTURAL BALANCE; PSYCHOMOTOR PERFORMANCE; SPINOCEREBELLAR ATAXIAS;

EID: 84864706637     PISSN: 14734222     EISSN: 14734230     Source Type: Journal    
DOI: 10.1007/s12311-011-0323-9     Document Type: Article

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