Cytoskeletal defects in Bmpr2-associated pulmonary arterial hypertension

American Journal of Physiology - Lung Cellular and Molecular Physiology

Volumn 302, Issue 5, 2012, Pages

  Johnson, Jennifer A ^a   Hemnes, Anna R ^a   Perrien, Daniel S ^a   Schuster, Manfred ^b   Robinson, Linda J ^a   Gladson, Santhi ^a   Loibner, Hans ^b   Bai, Susan ^a   Blackwell, Tom R ^a   Tada, Yuji ^c   Harral, Julie W ^c   Talati, Megha ^a   Lane, Kirk B ^a   Fagan, Karen A ^c   West, James ^a  

^a VANDERBILT UNIVERSITY MEDICAL CENTER   (United States)

^b Apeiron Biologics Forschungs und Entwicklungsgesellschaft MbH   (Austria)

^c UNIVERSITY OF COLORADO   (United States)

Author keywords

Bone morphogenic protein receptor type 2; Cytoskeleton; Rho GTPase

Indexed keywords

ANGIOTENSIN CONVERTING ENZYME 2; BONE MORPHOGENETIC PROTEIN RECEPTOR 2; RAC1 PROTEIN;

ANIMAL CELL; ANIMAL CELL CULTURE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; CYTOSKELETON; CYTOSKELETON DEFECT; ENZYME ACTIVATION; FEMALE; GENE EXPRESSION; GENE MUTATION; HISTOPATHOLOGY; LUNG ENDOTHELIUM; MALE; MICROVASCULAR ENDOTHELIAL CELL; MOUSE; NONHUMAN; PRIORITY JOURNAL; PULMONARY HYPERTENSION; STABLE TRANSFECTION;

AMINO ACID SUBSTITUTION; ANIMALS; BLOOD PRESSURE; BONE MORPHOGENETIC PROTEIN RECEPTORS, TYPE II; CELLS, CULTURED; CYTOSKELETON; ENDOTHELIAL CELLS; ENZYME ACTIVATION; FEMALE; GENE EXPRESSION PROFILING; HEART VENTRICLES; HUMANS; HYPERTENSION, PULMONARY; LUNG; MALE; MICE; MICE, TRANSGENIC; MICROVESSELS; NEUROPEPTIDES; OLIGONUCLEOTIDE ARRAY SEQUENCE ANALYSIS; PEPTIDYL-DIPEPTIDASE A; PHOSPHORYLATION; RAC GTP-BINDING PROTEINS; RECOMBINANT PROTEINS;

EID: 84863279449     PISSN: 10400605     EISSN: 15221504     Source Type: Journal    
DOI: 10.1152/ajplung.00202.2011     Document Type: Article

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