Failure of lower motor neuron radial outgrowth precedes retrograde degeneration in a feline model of spinal muscular atrophy

Journal of Comparative Neurology

Volumn 520, Issue 8, 2012, Pages 1737-1750

  Wakeling, Erin N ^a   Joussemet, Béatrice ^b   Costiou, Patrick ^c   Fanuel, Dominique ^c   Moullier, Philippe ^b,d,e   Barkats, Martine ^b   Fyfe, John C ^f  

^a MICHIGAN STATE UNIVERSITY   (United States)

^b INSERM   (France)

^c LUNAM UNIVERSITÉ   (France)

^d UNIVERSITY OF FLORIDA   (United States)

^e GÉNÉTHON   (France)

^f Association Internationale d'Informatique Médicale ^*  (United States)

Author keywords

Motor neuron; Neurodegeneration; Spinal muscular atrophy

Indexed keywords

ACTION POTENTIAL; AMPLITUDE MODULATION; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; CARPI RADIALIS MUSCLE; CAT; COMPOUND MOTOR ACTION POTENTIAL; CONTROLLED STUDY; DISEASE DURATION; ELECTROMYOGRAPHY; INNERVATION; LOWER MOTOR NEURON; MOTONEURON; MUSCLE; NERVE FIBER GROWTH; NEUROPATHOLOGY; NONHUMAN; ONSET AGE; PATHOLOGICAL ANATOMY; PERIKARYON; PRIORITY JOURNAL; QUADRICEPS FEMORIS MUSCLE; SOLEUS MUSCLE; SPINAL MUSCULAR ATROPHY; VENTRAL ROOT;

ACTION POTENTIALS; ANIMALS; CATS; CELL ENLARGEMENT; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; ELECTROMYOGRAPHY; LUMBOSACRAL REGION; MICROSCOPY, CONFOCAL; MOTOR NEURONS; MUSCLE, SKELETAL; MUSCULAR ATROPHY, SPINAL; RETROGRADE DEGENERATION; RNA-BINDING PROTEINS;

EID: 84859308664     PISSN: 00219967     EISSN: 10969861     Source Type: Journal    
DOI: 10.1002/cne.23010     Document Type: Article

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