Neuromuscular defects and breathing disorders in a new mouse model of spinal muscular atrophy

Neurobiology of Disease

Volumn 38, Issue 1, 2010, Pages 125-135

  Michaud, Magali ^a   Arnoux, Thomas ^a   Bielli, Serena ^a   Durand, Estelle ^b   Rotrou, Yann ^b   Jablonka, Sibylle ^c   Robert, Fabrice ^a   Giraudon Paoli, Marc ^a   Riessland, Markus ^d   Mattei, Marie Geneviève ^e   Andriambeloson, Emile ^f   Wirth, Brunhilde ^d   Sendtner, Michael ^c   Gallego, Jorge ^b   Pruss, Rebecca M ^a   Bordet, Thierry ^a  

^a Trophos   (France)

^b INSERM   (France)

^c UNIVERSITY OF WÜRZBURG   (Germany)

^d UNIVERSITY OF COLOGNE   (Germany)

^e AIX MARSEILLE UNIVERSITY   (France)

^f Neurofit   (France)

Author keywords

Behavior; Breathing disorders; Development; Motor neuron disease; Mouse model; Neurodegeneration; Neuromuscular junction; Spinal muscular atrophy; Survival motor neuron gene

Indexed keywords

SURVIVAL MOTOR NEURON PROTEIN; SURVIVAL MOTOR NEURON PROTEIN 2;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APNEA; ARTICLE; BREATHING DISORDER; BREATHING RATE; CONTROLLED STUDY; DISEASE MODEL; DISEASE SEVERITY; FEMALE; MALE; MEDICAL RESEARCH; MOUSE; NERVE DEGENERATION; NEUROMUSCULAR DISEASE; NEUROMUSCULAR JUNCTION DISORDER; NONHUMAN; PARALYSIS; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; RESPIRATORY FAILURE; SPINAL MUSCULAR ATROPHY; SURVIVAL RATE;

ANIMALS; DIAPHRAGM; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; GENES, LETHAL; GENETIC PREDISPOSITION TO DISEASE; HUMANS; MICE; MICE, TRANSGENIC; MUSCULAR ATROPHY, SPINAL; NEUROMUSCULAR JUNCTION; NEUROMUSCULAR JUNCTION DISEASES; RESPIRATORY INSUFFICIENCY; RESPIRATORY PARALYSIS; SURVIVAL OF MOTOR NEURON 2 PROTEIN;

EID: 77649186396     PISSN: 09699961     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nbd.2010.01.006     Document Type: Article

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