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Volumn 1, Issue 2, 2011, Pages 286-298

A consensus approach to the classification of pediatric pulmonary hypertensive vascular disease: Report from the PVRI pediatric taskforce, panama 2011

Author keywords

Pediatric patient; Pulmonary hypertension; Pulmonary hypertension in the newborn; Pulmonary vascular disease

Indexed keywords


EID: 84856385121     PISSN: 20458932     EISSN: 20458940     Source Type: Journal    
DOI: 10.4103/2045-8932.83456     Document Type: Article
Times cited : (211)

References (165)
  • 4
    • 85026307665 scopus 로고    scopus 로고
    • Aspectos Generales; Definición Clasificación y Epidemiología
    • Díaz G, Sandoval J, Sola A, editors, Bogotá: Editorial Médica Distribuna
    • Díaz G. Aspectos Generales; Definición Clasificación y Epidemiología. In: Díaz G, Sandoval J, Sola A, editors. Hipertensión Pulmonar en Niños. Bogotá: Editorial Médica Distribuna; 2011. p. 9-19.
    • (2011) Hipertensión Pulmonar En Niños , pp. 9-19
    • Díaz, G.1
  • 5
    • 38949188881 scopus 로고    scopus 로고
    • Pulmonary arterial hypertension in congenital cardiac disease--the need for refinement of the Evian-Venice classification
    • van Albada ME, Berger RM. Pulmonary arterial hypertension in congenital cardiac disease--the need for refinement of the Evian-Venice classification. Cardiol Young 2008;18:10-7.
    • (2008) Cardiol Young , vol.18 , pp. 10-17
    • Van Albada, M.E.1    Berger, R.M.2
  • 7
    • 38949135912 scopus 로고    scopus 로고
    • Classifying pulmonary hypertension in the setting of the congenitally malformed heart--cleaning up a dog’s dinner
    • Schulze-Neick I, Beghetti M. Classifying pulmonary hypertension in the setting of the congenitally malformed heart--cleaning up a dog’s dinner. Cardiol Young 2008;18:22-5.
    • (2008) Cardiol Young , vol.18 , pp. 22-25
    • Schulze-Neick, I.1    Beghetti, M.2
  • 8
    • 11844250659 scopus 로고    scopus 로고
    • The developmental origins of adult disease
    • Barker DJ. The developmental origins of adult disease. J Am Coll Nutr 2004;23 Suppl 6:588S-95.
    • J am Coll Nutr 2004;23 Suppl , vol.6 , pp. 588S-595S
    • Barker, D.J.1
  • 9
    • 0021339465 scopus 로고
    • Lung growth in health and disease
    • Reid LM. Lung growth in health and disease. Br J Dis Chest 1984;78: 113-34.
    • (1984) Br J Dis Chest , vol.78 , pp. 113-134
    • Reid, L.M.1
  • 10
    • 77951224752 scopus 로고    scopus 로고
    • Impaired vascular endothelial growth factor signaling in the pathogenesis of neonatal pulmonary vascular disease
    • Abman SH. Impaired vascular endothelial growth factor signaling in the pathogenesis of neonatal pulmonary vascular disease. Adv Exp Med Biol 2010;661:323-35.
    • (2010) Adv Exp Med Biol , vol.661 , pp. 323-335
    • Abman, S.H.1
  • 11
    • 23944502333 scopus 로고    scopus 로고
    • Alveolar capillary dysplasia: A six-year single center experience
    • Eulmesekian P, Cutz E, Parvez B, Bohn D, Adatia I. Alveolar capillary dysplasia: A six-year single center experience. J Perinat Med 2005;33: 347-52.
    • (2005) J Perinat Med , vol.33 , pp. 347-352
    • Eulmesekian, P.1    Cutz, E.2    Parvez, B.3    Bohn, D.4    Adatia, I.5
  • 12
    • 0005783599 scopus 로고
    • The normal pulmonary arterial pressure during the first year of life
    • Rowe R, James L. The normal pulmonary arterial pressure during the first year of life. J Pediatr 1957;51:1-4.
    • (1957) J Pediatr , vol.51 , pp. 1-4
    • Rowe, R.1    James, L.2
  • 13
    • 0018101775 scopus 로고
    • Hemodynamic responses to exercise in normal children
    • Lock J, Einzig S, Moller J. Hemodynamic responses to exercise in normal children. Am J Cardiol 1978;41:1278-84.
    • (1978) Am J Cardiol , vol.41 , pp. 1278-1284
    • Lock, J.1    Einzig, S.2    Moller, J.3
  • 14
    • 0027249487 scopus 로고
    • Pulmonary hypertension in childhood
    • Haworth SG. Pulmonary hypertension in childhood. Eur Respir J 1993;6:1037-43.
    • (1993) Eur Respir J , vol.6 , pp. 1037-1043
    • Haworth, S.G.1
  • 15
    • 77949459229 scopus 로고    scopus 로고
    • Maternal preeclampsia predicts the development of bronchopulmonary dysplasia
    • Hansen AR, Barnes CM, Folkman J, McElrath TF. Maternal preeclampsia predicts the development of bronchopulmonary dysplasia. J Pediatr 2010;156:532-6.
    • (2010) J Pediatr , vol.156 , pp. 532-536
    • Hansen, A.R.1    Barnes, C.M.2    Folkman, J.3    McElrath, T.F.4
  • 16
    • 0033537634 scopus 로고    scopus 로고
    • Prenatal features of ductus arteriosus constriction and restrictive foramen ovale in d-transposition of the great arteries
    • Maeno YV, Kamenir SA, Sinclair B, van der Velde ME, Smallhorn JF, Hornberger LK. Prenatal features of ductus arteriosus constriction and restrictive foramen ovale in d-transposition of the great arteries. Circulation 1999;99:1209-14.
    • (1999) Circulation , vol.99 , pp. 1209-1214
    • Maeno, Y.V.1    Kamenir, S.A.2    Sinclair, B.3    Van Der Velde, M.E.4    Smallhorn, J.F.5    Hornberger, L.K.6
  • 17
    • 77956419406 scopus 로고    scopus 로고
    • Pulmonary interstitial glycogenosis in the setting of lung growth abnormality: Radiographic and pathologic correlation
    • Castillo M, Vade A, Lim-Dunham JE, Masuda E, Massarani-Wafai R. Pulmonary interstitial glycogenosis in the setting of lung growth abnormality: Radiographic and pathologic correlation. Pediatr Radiol 2010;40:1562-5.
    • (2010) Pediatr Radiol , vol.40 , pp. 1562-1565
    • Castillo, M.1    Vade, A.2    Lim-Dunham, J.E.3    Masuda, E.4    Massarani-Wafai, R.5
  • 20
    • 1942501858 scopus 로고    scopus 로고
    • Open lung biopsy in neonatal and paediatric patients referred for extracorporeal membrane oxygenation (ECMO)
    • Inwald D, Brown K, Gensini F, Malone M, Goldman A. Open lung biopsy in neonatal and paediatric patients referred for extracorporeal membrane oxygenation (ECMO). Thorax 2004;59:328-33.
    • (2004) Thorax , vol.59 , pp. 328-333
    • Inwald, D.1    Brown, K.2    Gensini, F.3    Malone, M.4    Goldman, A.5
  • 21
    • 77951725470 scopus 로고    scopus 로고
    • Haploinsufficiencies of FOXF1 and FOXC2 genes associated with lethal alveolar capillary dysplasia and congenital heart disease
    • Yu S, Shao L, Kilbride H, Zwick DL. Haploinsufficiencies of FOXF1 and FOXC2 genes associated with lethal alveolar capillary dysplasia and congenital heart disease. Am J Med Genet A 2010;152:1257-62.
    • (2010) Am J Med Genet A , vol.152 , pp. 1257-1262
    • Yu, S.1    Shao, L.2    Kilbride, H.3    Zwick, D.L.4
  • 22
    • 66449113643 scopus 로고    scopus 로고
    • Genomic and genic deletions of the FOX gene cluster on 16q24.1 and inactivating mutations of FOXF1 cause alveolar capillary dysplasia and other malformations
    • Stankiewicz P, Sen P, Bhatt SS, Storer M, Xia Z, Bejjani BA, et al. Genomic and genic deletions of the FOX gene cluster on 16q24.1 and inactivating mutations of FOXF1 cause alveolar capillary dysplasia and other malformations. Am J Hum Genet 2009;84:780-91.
    • (2009) Am J Hum Genet , vol.84 , pp. 780-791
    • Stankiewicz, P.1    Sen, P.2    Bhatt, S.S.3    Storer, M.4    Xia, Z.5    Bejjani, B.A.6
  • 23
    • 74249115602 scopus 로고    scopus 로고
    • Genetic factors in esophageal atresia, tracheo-esophageal fistula and the VACTERL association: Roles for FOXF1 and the 16q24.1 FOX transcription factor gene cluster, and review of the literature
    • Shaw-Smith C. Genetic factors in esophageal atresia, tracheo-esophageal fistula and the VACTERL association: Roles for FOXF1 and the 16q24.1 FOX transcription factor gene cluster, and review of the literature. Eur J Med Genet 2010;53:6-13.
    • (2010) Eur J Med Genet , vol.53 , pp. 6-13
    • Shaw-Smith, C.1
  • 24
    • 0031971430 scopus 로고    scopus 로고
    • Familial persistent pulmonary hypertension of the newborn resulting from misalignment of the pulmonary vessels (Cogenital alveolar capillary dysplasia)
    • Vassal HB, Malone M, Petros AJ, Winter RM. Familial persistent pulmonary hypertension of the newborn resulting from misalignment of the pulmonary vessels (cogenital alveolar capillary dysplasia). J Med Genet 1998;35:58-60.
    • (1998) J Med Genet , vol.35 , pp. 58-60
    • Vassal, H.B.1    Malone, M.2    Petros, A.J.3    Winter, R.M.4
  • 25
    • 2342613573 scopus 로고    scopus 로고
    • Defective lung vascular development and fatal respiratory distress in endothelial NO synthase-deficient mice: A model of alveolar capillary dysplasia?
    • Han RN, Babaei S, Robb M, Lee T, Ridsdale R, Ackerley C, et al. Defective lung vascular development and fatal respiratory distress in endothelial NO synthase-deficient mice: A model of alveolar capillary dysplasia? Circ Res 2004;94:1115-23.
    • (2004) Circ Res , vol.94 , pp. 1115-1123
    • Han, R.N.1    Babaei, S.2    Robb, M.3    Lee, T.4    Ridsdale, R.5    Ackerley, C.6
  • 26
    • 0015056364 scopus 로고
    • Lung hypoplasia in congenital diaphragmatic hernia: A quantitative study of airway, artery, and alveolar development
    • Kitagawa M, Hislop A, Boyden EA, Reid L. Lung hypoplasia in congenital diaphragmatic hernia: A quantitative study of airway, artery, and alveolar development. Br J Surg 1971;58:342-6.
    • (1971) Br J Surg , vol.58 , pp. 342-346
    • Kitagawa, M.1    Hislop, A.2    Boyden, E.A.3    Reid, L.4
  • 27
    • 0019940287 scopus 로고
    • Pulmonary hypoplasia in Down’s syndrome
    • Cooney TP, Thurlbeck WM. Pulmonary hypoplasia in Down’s syndrome. N Engl J Med 1982;307:1170-3.
    • (1982) N Engl J Med , vol.307 , pp. 1170-1173
    • Cooney, T.P.1    Thurlbeck, W.M.2
  • 29
    • 0018392854 scopus 로고
    • Pulmonary hypoplasia: Lung weight and radial alveolar count as criteria of diagnosis
    • Askenazi SS, Perlman M. Pulmonary hypoplasia: Lung weight and radial alveolar count as criteria of diagnosis. Arch Dis Child 1979;54:614-8.
    • (1979) Arch Dis Child , vol.54 , pp. 614-618
    • Askenazi, S.S.1    Perlman, M.2
  • 30
    • 0021277307 scopus 로고
    • Pulmonary vascular disease in fatal meconium aspiration
    • Murphy JD, Vawter GF, Reid LM. Pulmonary vascular disease in fatal meconium aspiration. J Pediatr 1984;104:758-62.
    • (1984) J Pediatr , vol.104 , pp. 758-762
    • Murphy, J.D.1    Vawter, G.F.2    Reid, L.M.3
  • 31
    • 0021217265 scopus 로고
    • The structural basis of PPHN
    • Geggel RL, Reid LM. The structural basis of PPHN. Clin Perinatol 1984;11:525-49.
    • (1984) Clin Perinatol , vol.11 , pp. 525-549
    • Geggel, R.L.1    Reid, L.M.2
  • 32
    • 0017283225 scopus 로고
    • Persistent fetal circulation: Newly recognized structural features
    • Haworth SG, Reid L. Persistent fetal circulation: Newly recognized structural features. J Pediatr 1976;88:614-20.
    • (1976) J Pediatr , vol.88 , pp. 614-620
    • Haworth, S.G.1    Reid, L.2
  • 33
    • 75149175193 scopus 로고    scopus 로고
    • NKX2 1 mutations leading to surfactant protein promoter dysregulation cause interstitial lung disease in “Brain-Lung-Thyroid Syndrome.”
    • Guillot L, Carre A, Szinnai G, Castanet M, Tron E, Jaubert F, et al. NKX2 1 mutations leading to surfactant protein promoter dysregulation cause interstitial lung disease in “Brain-Lung-Thyroid Syndrome.” Hum Mutat 2010;31:E1146-62.
    • (2010) Hum Mutat , vol.31 , pp. E1146-E1162
    • Guillot, L.1    Carre, A.2    Szinnai, G.3    Castanet, M.4    Tron, E.5    Jaubert, F.6
  • 34
    • 60549094652 scopus 로고    scopus 로고
    • Thyroid transcription factor-1 (TTF-1/Nkx2.1/TITF1) gene regulation in the lung
    • Boggaram V. Thyroid transcription factor-1 (TTF-1/Nkx2.1/TITF1) gene regulation in the lung. Clin Sci (Lond) 2009;116:27-35.
    • (2009) Clin Sci (Lond) , vol.116 , pp. 27-35
    • Boggaram, V.1
  • 35
    • 0026611008 scopus 로고
    • Low-dose inhalational nitric oxide in persistent pulmonary hypertension of the newborn
    • Kinsella JP, Neish SR, Shaffer E, Abman SH. Low-dose inhalational nitric oxide in persistent pulmonary hypertension of the newborn. Lancet 1992;340:819-20.
    • (1992) Lancet , vol.340 , pp. 819-820
    • Kinsella, J.P.1    Neish, S.R.2    Shaffer, E.3    Abman, S.H.4
  • 36
    • 0029069107 scopus 로고
    • Recent developments in the pathophysiology and treatment of persistent pulmonary hypertension of the newborn
    • Kinsella JP, Abman SH. Recent developments in the pathophysiology and treatment of persistent pulmonary hypertension of the newborn. J Pediatr 1995;126:853-64.
    • (1995) J Pediatr , vol.126 , pp. 853-864
    • Kinsella, J.P.1    Abman, S.H.2
  • 37
    • 0025696993 scopus 로고
    • Role of endothelium-derived relaxing factor during transition of pulmonary circulation at birth
    • Abman SH, Chatfield BA, Hall SL, McMurtry IF. Role of endothelium-derived relaxing factor during transition of pulmonary circulation at birth. Am J Physiol 1990;259:H1921-7.
    • (1990) Am J Physiol , vol.259 , pp. H1921-H1927
    • Abman, S.H.1    Chatfield, B.A.2    Hall, S.L.3    McMurtry, I.F.4
  • 39
    • 77949471213 scopus 로고    scopus 로고
    • Neonatal pulmonary hypertension
    • Steinhorn RH. Neonatal pulmonary hypertension. Pediatr Crit Care Med 2010;11 Suppl 2:S79-84.
    • (2010) Pediatr Crit Care Med , Issue.11 , pp. S79-S84
    • Steinhorn, R.H.1
  • 40
    • 68949208474 scopus 로고    scopus 로고
    • Pulmonary hypertension associated with congenital diaphragmatic hernia
    • Thebaud B, Tibboel D. Pulmonary hypertension associated with congenital diaphragmatic hernia. Cardiol Young 2009;19 Suppl 1:49-53.
    • (2009) Cardiol Young , Issue.19 , pp. 49-53
    • Thebaud, B.1    Tibboel, D.2
  • 41
    • 20444449178 scopus 로고    scopus 로고
    • Pulmonary vasodilator therapy in congenital diaphragmatic hernia: Acute, late, and chronic pulmonary hypertension
    • Kinsella JP, Ivy DD, Abman SH. Pulmonary vasodilator therapy in congenital diaphragmatic hernia: Acute, late, and chronic pulmonary hypertension. Semin Perinatol 2005;29:123-8.
    • (2005) Semin Perinatol , vol.29 , pp. 123-128
    • Kinsella, J.P.1    Ivy, D.D.2    Abman, S.H.3
  • 42
    • 68949205610 scopus 로고    scopus 로고
    • Neonates with congenital cardiac defects and pulmonary hypertension
    • Chang AC, Macrae D. Neonates with congenital cardiac defects and pulmonary hypertension. Cardiol Young 2009;19 Suppl 1:4-7.
    • (2009) Cardiol Young , Issue.19 , pp. 4-7
    • Chang, A.C.1    Macrae, D.2
  • 43
    • 33646343464 scopus 로고    scopus 로고
    • Oral sildenafil in infants with persistent pulmonary hypertension of the newborn: A pilot randomized blinded study
    • Baquero H, Soliz A, Neira F, Venegas ME, Sola A. Oral sildenafil in infants with persistent pulmonary hypertension of the newborn: A pilot randomized blinded study. Pediatrics 2006;117:1077-83.
    • (2006) Pediatrics , vol.117 , pp. 1077-1083
    • Baquero, H.1    Soliz, A.2    Neira, F.3    Venegas, M.E.4    Sola, A.5
  • 44
    • 52449099616 scopus 로고    scopus 로고
    • Pulmonary hemodynamics in children living at high altitudes
    • Peñaloza D, Sime F, Ruiz L. Pulmonary hemodynamics in children living at high altitudes. High Alt Med Biol 2008;9:199-207.
    • (2008) High Alt Med Biol , vol.9 , pp. 199-207
    • Peñaloza, D.1    Sime, F.2    Ruiz, L.3
  • 45
    • 84871312589 scopus 로고    scopus 로고
    • Hipertensión Pulmonar en Niños a Moderada Altura en Hipertensión Pulmonar en Niños
    • Díaz G, Sandoval J, Sola A, editors, Bogotá: Editorial Médica Distribuna
    • Díaz G, Márquez A. Hipertensión Pulmonar en Niños a Moderada Altura en Hipertensión Pulmonar en Niños. In: Díaz G, Sandoval J, Sola A, editors. Hipertensión Pulmonar en Niños. Bogotá: Editorial Médica Distribuna; 2011. p. 266-84.
    • (2011) Hipertensión Pulmonar En Niños , pp. 266-284
    • Díaz, G.1    Márquez, A.2
  • 46
    • 0015053728 scopus 로고
    • Pulmonary arterial pressure in newborn infants in high altitude
    • Gamboa R, Marticorena E. Pulmonary arterial pressure in newborn infants in high altitude. Arch Inst Biol Andina 1971;4:55-66.
    • (1971) Arch Inst Biol Andina , vol.4 , pp. 55-66
    • Gamboa, R.1    Marticorena, E.2
  • 47
    • 62249199804 scopus 로고    scopus 로고
    • Treatment and survival in children with pulmonary arterial hypertension: The UK Pulmonary Hypertension Service for Children 2001-2006
    • Haworth SG, Hislop AA. Treatment and survival in children with pulmonary arterial hypertension: The UK Pulmonary Hypertension Service for Children 2001-2006. Heart 2009;95:312-7.
    • (2009) Heart , vol.95 , pp. 312-317
    • Haworth, S.G.1    Hislop, A.A.2
  • 48
    • 77953302009 scopus 로고    scopus 로고
    • Pulmonary hypertension associated with congenital heart disease: Pulmonary vascular disease: The global perspective
    • Adatia I, Kothari SS, Feinstein JA. Pulmonary hypertension associated with congenital heart disease: Pulmonary vascular disease: The global perspective. Chest 2010;137 Suppl 6:52S-61.
    • (2010) Chest , Issue.137 , pp. 52S-61S
    • Adatia, I.1    Kothari, S.S.2    Feinstein, J.A.3
  • 49
    • 34548823784 scopus 로고    scopus 로고
    • The Swiss registry for pulmonary arterial hypertension: The paediatric experience
    • Fasnacht MS, Tolsa JF, Beghetti M. The Swiss registry for pulmonary arterial hypertension: The paediatric experience. Swiss Med Wkly 2007;137:510-3.
    • (2007) Swiss Med Wkly , vol.137 , pp. 510-513
    • Fasnacht, M.S.1    Tolsa, J.F.2    Beghetti, M.3
  • 50
    • 70649086962 scopus 로고    scopus 로고
    • Pulmonary venous hypertension or pulmonary hypertension due to left heart disease
    • Adatia I, Mullen M, Kulik TJ. Pulmonary venous hypertension or pulmonary hypertension due to left heart disease. Prog Pediatr Cardiol 2009;27:35-42.
    • (2009) Prog Pediatr Cardiol , vol.27 , pp. 35-42
    • Adatia, I.1    Mullen, M.2    Kulik, T.J.3
  • 51
    • 70649115363 scopus 로고    scopus 로고
    • Pulmonary arterial hypertension associated with congenital heart disease
    • Kulik T, Mullen M, Adatia I. Pulmonary arterial hypertension associated with congenital heart disease. Prog Pediatr Cardiol 2009;27:25-33.
    • (2009) Prog Pediatr Cardiol , vol.27 , pp. 25-33
    • Kulik, T.1    Mullen, M.2    Adatia, I.3
  • 52
  • 53
    • 77952296235 scopus 로고    scopus 로고
    • Late-onset pulmonary arterial hypertension after a successful atrial or arterial switch procedure for transposition of the great arteries
    • Cordina R, Celermajer D. Late-onset pulmonary arterial hypertension after a successful atrial or arterial switch procedure for transposition of the great arteries. Pediatr Cardiol 2010;31:238-41.
    • (2010) Pediatr Cardiol , vol.31 , pp. 238-241
    • Cordina, R.1    Celermajer, D.2
  • 54
    • 0027264802 scopus 로고
    • Pulmonary vascular disease in neonates with transposition of the great arteries and intact ventricular septum
    • Kumar A, Taylor G, Sandor G, Patterson M. Pulmonary vascular disease in neonates with transposition of the great arteries and intact ventricular septum. Br Heart J 1993;69:442-5.
    • (1993) Br Heart J , vol.69 , pp. 442-445
    • Kumar, A.1    Taylor, G.2    Sandor, G.3    Patterson, M.4
  • 55
    • 0028295389 scopus 로고
    • Progressive pulmonary hypertension after the arterial switch procedure
    • Sreeram N, Petros A, Peart I, Arnold R. Progressive pulmonary hypertension after the arterial switch procedure. Am J Cardiol 1994;73:620-1.
    • (1994) Am J Cardiol , vol.73 , pp. 620-621
    • Sreeram, N.1    Petros, A.2    Peart, I.3    Arnold, R.4
  • 57
    • 34548730338 scopus 로고    scopus 로고
    • Long-term effect of bosentan in adults versus children with pulmonary arterial hypertension associated with systemic-to-pulmonary shunt: Does the beneficial effect persist?
    • van Loon RL, Hoendermis ES, Duffels MG, Vonk-Noordegraaf A, Mulder BJ, Hillege HL, et al. Long-term effect of bosentan in adults versus children with pulmonary arterial hypertension associated with systemic-to-pulmonary shunt: Does the beneficial effect persist? Am Heart J 2007;154:776-82.
    • (2007) Am Heart J , vol.154 , pp. 776-782
    • Van Loon, R.L.1    Hoendermis, E.S.2    Duffels, M.G.3    Vonk-Noordegraaf, A.4    Mulder, B.J.5    Hillege, H.L.6
  • 58
    • 37549036735 scopus 로고    scopus 로고
    • Twenty-year experience with heart transplantation for infants and children with restrictive cardiomyopathy: 1986-2006
    • Bograd AJ, Mital S, Schwarzenberger JC, Mosca RS, Quaegebeur JM, Addonizio LJ, et al. Twenty-year experience with heart transplantation for infants and children with restrictive cardiomyopathy: 1986-2006. Am J Transplant 2008;8:201-7.
    • (2008) Am J Transplant , vol.8 , pp. 201-207
    • Bograd, A.J.1    Mital, S.2    Schwarzenberger, J.C.3    Mosca, R.S.4    Quaegebeur, J.M.5    Addonizio, L.J.6
  • 59
    • 79951813191 scopus 로고    scopus 로고
    • Initial experience with sildenafil, bosentan, and nitric oxide for pediatric cardiomyopathy patients with elevated pulmonary vascular resistance before and after orthotopic heart transplantation
    • Daftari B, Alejos JC, Perens G. Initial experience with sildenafil, bosentan, and nitric oxide for pediatric cardiomyopathy patients with elevated pulmonary vascular resistance before and after orthotopic heart transplantation. J Transplant 2010;2010:656984.
    • (2010) J Transplant , vol.2010
    • Daftari, B.1    Alejos, J.C.2    Perens, G.3
  • 60
    • 20444491226 scopus 로고    scopus 로고
    • The Fontan circulation: A challenge to William Harvey?
    • de Leval MR. The Fontan circulation: A challenge to William Harvey? Nat Clin Pract Cardiovasc Med 2005;2:202-8.
    • (2005) Nat Clin Pract Cardiovasc Med , vol.2 , pp. 202-208
    • De Leval, M.R.1
  • 62
    • 0038078913 scopus 로고    scopus 로고
    • Basal pulmonary vascular resistance and nitric oxide responsiveness late after Fontan-type operation
    • Khambadkone S, Li J, de Leval MR, Cullen S, Deanfield JE, Redington AN. Basal pulmonary vascular resistance and nitric oxide responsiveness late after Fontan-type operation. Circulation 2003;107:3204-8.
    • (2003) Circulation , vol.107 , pp. 3204-3208
    • Khambadkone, S.1    Li, J.2    De Leval, M.R.3    Cullen, S.4    Deanfield, J.E.5    Redington, A.N.6
  • 63
    • 84055182266 scopus 로고    scopus 로고
    • What limits cardiac performance during exercise in normal subjects and in healthy fontan patients?
    • La Gerche A, Gewillig M. What limits cardiac performance during exercise in normal subjects and in healthy fontan patients? Int J Pediatr 2010;2010.pii:791291.
    • (2010) Int J Pediatr , vol.2010
    • La Gerche, A.1    Gewillig, M.2
  • 64
    • 46849112004 scopus 로고    scopus 로고
    • Effect of sildenafil on haemodynamic response to exercise and exercise capacity in Fontan patients
    • Giardini A, Balducci A, Specchia S, Gargiulo G, Bonvicini M, Picchio FM. Effect of sildenafil on haemodynamic response to exercise and exercise capacity in Fontan patients. Eur Heart J 2008;29:1681-7.
    • (2008) Eur Heart J , vol.29 , pp. 1681-1687
    • Giardini, A.1    Balducci, A.2    Specchia, S.3    Gargiulo, G.4    Bonvicini, M.5    Picchio, F.M.6
  • 65
    • 21044449937 scopus 로고    scopus 로고
    • Beneficial effect of oral sildenafil therapy on childhood pulmonary arterial hypertension: Twelve-month clinical trial of a single-drug, open-label, pilot study
    • Humpl T, Reyes JT, Holtby H, Stephens D, Adatia I. Beneficial effect of oral sildenafil therapy on childhood pulmonary arterial hypertension: Twelve-month clinical trial of a single-drug, open-label, pilot study. Circulation 2005;111:3274-80.
    • (2005) Circulation , vol.111 , pp. 3274-3280
    • Humpl, T.1    Reyes, J.T.2    Holtby, H.3    Stephens, D.4    Adatia, I.5
  • 66
    • 23744452438 scopus 로고    scopus 로고
    • Bosentan induces clinical, exercise and hemodynamic improvement in a pre-transplant patient with plastic bronchitis after Fontan operation
    • Apostolopoulou SC, Papagiannis J, Rammos S. Bosentan induces clinical, exercise and hemodynamic improvement in a pre-transplant patient with plastic bronchitis after Fontan operation. J Heart Lung Transplant 2005;24:1174-6.
    • (2005) J Heart Lung Transplant , vol.24 , pp. 1174-1176
    • Apostolopoulou, S.C.1    Papagiannis, J.2    Rammos, S.3
  • 67
    • 33751176882 scopus 로고    scopus 로고
    • Resolution of protein-losing enteropathy and normalization of mesenteric Doppler flow with sildenafil after Fontan
    • Uzun O, Wong JK, Bhole V, Stumper O. Resolution of protein-losing enteropathy and normalization of mesenteric Doppler flow with sildenafil after Fontan. Ann Thorac Surg 2006;82:e39-40.
    • (2006) Ann Thorac Surg , vol.82 , pp. e39-e40
    • Uzun, O.1    Wong, J.K.2    Bhole, V.3    Stumper, O.4
  • 69
    • 84871323689 scopus 로고    scopus 로고
    • Does High altitude protect against irreversible pulmonary hypertension?
    • Heath A, Stewart K, Mendes J, Ramirez M, Freudenthal F. Does High altitude protect against irreversible pulmonary hypertension? PVRI Rev 2010;2:131-3.
    • (2010) PVRI Rev , vol.2 , pp. 131-133
    • Heath, A.1    Stewart, K.2    Mendes, J.3    Ramirez, M.4    Freudenthal, F.5
  • 71
    • 0000399371 scopus 로고
    • The Heart and pulmonary circulation in children at high altitudes: Physiological, anatomical, and clinical observations
    • Penaloza D, Arias-Stella J, Sime F, Recavarren S, Marticorena E. The Heart and pulmonary circulation in children at high altitudes: physiological, anatomical, and clinical observations. Pediatrics 1964;34:568-82.
    • (1964) Pediatrics , vol.34 , pp. 568-582
    • Penaloza, D.1    Arias-Stella, J.2    Sime, F.3    Recavarren, S.4    Marticorena, E.5
  • 72
    • 33947606593 scopus 로고    scopus 로고
    • The heart and pulmonary circulation at high altitudes: Healthy highlanders and chronic mountain sickness
    • Penaloza D, Arias-Stella J. The heart and pulmonary circulation at high altitudes: Healthy highlanders and chronic mountain sickness. Circulation 2007;115:1132-46.
    • (2007) Circulation , vol.115 , pp. 1132-1146
    • Penaloza, D.1    Arias-Stella, J.2
  • 73
    • 39049158819 scopus 로고    scopus 로고
    • Chronic lung disease after premature birth
    • Cutz E, Chiasson D. Chronic lung disease after premature birth. N Engl J Med 2008;358:743-5; author reply 745-6.
    • (2008) N Engl J Med , vol.358 , pp. 743-745
    • Cutz, E.1    Chiasson, D.2
  • 74
  • 75
    • 15544380502 scopus 로고    scopus 로고
    • Lung vascular development: Implications for the pathogenesis of bronchopulmonary dysplasia
    • Stenmark KR, Abman SH. Lung vascular development: Implications for the pathogenesis of bronchopulmonary dysplasia. Annu Rev Physiol 2005;67:623-61.
    • (2005) Annu Rev Physiol , vol.67 , pp. 623-661
    • Stenmark, K.R.1    Abman, S.H.2
  • 76
    • 0037300312 scopus 로고    scopus 로고
    • Pathology of new bronchopulmonary dysplasia
    • Coalson JJ. Pathology of new bronchopulmonary dysplasia. Semin Neonatol 2003;8:73-81.
    • (2003) Semin Neonatol , vol.8 , pp. 73-81
    • Coalson, J.J.1
  • 77
    • 33745936044 scopus 로고    scopus 로고
    • Definitions and diagnostic criteria for bronchopulmonary dysplasia
    • Bancalari E, Claure N. Definitions and diagnostic criteria for bronchopulmonary dysplasia. Semin Perinatol 2006;30:164-70.
    • (2006) Semin Perinatol , vol.30 , pp. 164-170
    • Bancalari, E.1    Claure, N.2
  • 78
    • 35848952935 scopus 로고    scopus 로고
    • Chronic lung disease after premature birth
    • Baraldi E, Filippone M. Chronic lung disease after premature birth. N Engl J Med 2007;357:1946-55.
    • (2007) N Engl J Med , vol.357 , pp. 1946-1955
    • Baraldi, E.1    Filippone, M.2
  • 79
    • 36849067910 scopus 로고    scopus 로고
    • Pulmonary artery hypertension in formerly premature infants with bronchopulmonary dysplasia: Clinical features and outcomes in the surfactant era
    • Khemani E, McElhinney DB, Rhein L, Andrade O, Lacro RV, Thomas KC, et al. Pulmonary artery hypertension in formerly premature infants with bronchopulmonary dysplasia: Clinical features and outcomes in the surfactant era. Pediatrics 2007;120:1260-9.
    • (2007) Pediatrics , vol.120 , pp. 1260-1269
    • Khemani, E.1    McElhinney, D.B.2    Rhein, L.3    Rade, O.4    Lacro, R.V.5    Thomas, K.C.6
  • 80
    • 58549120752 scopus 로고    scopus 로고
    • Treatment of pulmonary hypertension in children with chronic lung disease with newer oral therapies
    • Krishnan U, Krishnan S, Gewitz M. Treatment of pulmonary hypertension in children with chronic lung disease with newer oral therapies. Pediatr Cardiol 2008;29:1082-6.
    • (2008) Pediatr Cardiol , vol.29 , pp. 1082-1086
    • Krishnan, U.1    Krishnan, S.2    Gewitz, M.3
  • 81
    • 51649104383 scopus 로고    scopus 로고
    • Pulmonary vein stenosis: Prematurity and associated conditions
    • Drossner DM, Kim DW, Maher KO, Mahle WT. Pulmonary vein stenosis: Prematurity and associated conditions. Pediatrics 2008;122:e656-61.
    • (2008) Pediatrics , vol.122 , pp. e656-e661
    • Drossner, D.M.1    Kim, D.W.2    Maher, K.O.3    Mahle, W.T.4
  • 82
    • 72049098170 scopus 로고    scopus 로고
    • Pulmonary vein stenosis: The UK, Ireland and Sweden collaborative study
    • Seale AN, Webber SA, Uemura H, Partridge J, Roughton M, Ho SY, et al. Pulmonary vein stenosis: The UK, Ireland and Sweden collaborative study. Heart 2009;95:1944-9.
    • (2009) Heart , vol.95 , pp. 1944-1949
    • Seale, A.N.1    Webber, S.A.2    Uemura, H.3    Partridge, J.4    Roughton, M.5    Ho, S.Y.6
  • 83
    • 60549109238 scopus 로고    scopus 로고
    • Effects of long-term sildenafil treatment for pulmonary hypertension in infants with chronic lung disease
    • Mourani PM, Sontag MK, Ivy DD, Abman SH. Effects of long-term sildenafil treatment for pulmonary hypertension in infants with chronic lung disease. J Pediatr 2009;154:379-84.
    • (2009) J Pediatr , vol.154 , pp. 379-384
    • Mourani, P.M.1    Sontag, M.K.2    Ivy, D.D.3    Abman, S.H.4
  • 84
    • 77956108380 scopus 로고    scopus 로고
    • Childhood idiopathic pulmonary arterial hypertension: A national cohort study
    • Moledina S, Hislop AA, Foster H, Schulze-Neick I, Haworth SG. Childhood idiopathic pulmonary arterial hypertension: A national cohort study. Heart 2010;96:1401-6.
    • (2010) Heart , vol.96 , pp. 1401-1406
    • Moledina, S.1    Hislop, A.A.2    Foster, H.3    Schulze-Neick, I.4    Haworth, S.G.5
  • 85
    • 77953067153 scopus 로고    scopus 로고
    • Clinical outcomes of pulmonary arterial hypertension in patients carrying an ACVRL1 (ALK1) mutation
    • Girerd B, Montani D, Coulet F, Sztrymf B, Yaici A, Jais X, et al. Clinical outcomes of pulmonary arterial hypertension in patients carrying an ACVRL1 (ALK1) mutation. Am J Respir Crit Care Med 2010;181:851-61.
    • (2010) Am J Respir Crit Care Med , vol.181 , pp. 851-861
    • Girerd, B.1    Montani, D.2    Coulet, F.3    Sztrymf, B.4    Yaici, A.5    Jais, X.6
  • 86
    • 77950627120 scopus 로고    scopus 로고
    • Characteristics and prospective 2-year follow-up of children with pulmonary arterial hypertension in France
    • Fraisse A, Jais X, Schleich JM, di Filippo S, Maragnes P, Beghetti M, et al. Characteristics and prospective 2-year follow-up of children with pulmonary arterial hypertension in France. Arch Cardiovasc Dis 2010;103:66-74.
    • (2010) Arch Cardiovasc Dis , vol.103 , pp. 66-74
    • Fraisse, A.1    Jais, X.2    Schleich, J.M.3    Di Filippo, S.4    Maragnes, P.5    Beghetti, M.6
  • 88
    • 58749089092 scopus 로고    scopus 로고
    • Pulmonary hypertension, heart failure and neutropenia due to diazoxide therapy
    • Yildizdas D, Erdem S, Kucukosmanoglu O, Yilmaz M, Yuksel B. Pulmonary hypertension, heart failure and neutropenia due to diazoxide therapy. Adv Ther 2008;25:515-9.
    • (2008) Adv Ther , vol.25 , pp. 515-519
    • Yildizdas, D.1    Erdem, S.2    Kucukosmanoglu, O.3    Yilmaz, M.4    Yuksel, B.5
  • 91
    • 0015306854 scopus 로고
    • Fatal pulmonary hypertension from intravenous injection of methylphenidate (Ritalin) tablets
    • Lewman LV. Fatal pulmonary hypertension from intravenous injection of methylphenidate (Ritalin) tablets. Hum Pathol 1972;3:67-70.
    • (1972) Hum Pathol , vol.3 , pp. 67-70
    • Lewman, L.V.1
  • 92
    • 3142583632 scopus 로고    scopus 로고
    • Fatal pulmonary arterial hypertension associated with phenylpropanolamine exposure
    • Barst RJ, Abenhaim L. Fatal pulmonary arterial hypertension associated with phenylpropanolamine exposure. Heart 2004;90:e42.
    • (2004) Heart , vol.42 , pp. 90
    • Barst, R.J.1    Abenhaim, L.2
  • 93
    • 4444370312 scopus 로고    scopus 로고
    • Abnormal pericyte recruitment as a cause for pulmonary hypertension in Adams-Oliver syndrome
    • Patel MS, Taylor GP, Bharya S, Al-Sanna’a N, Adatia I, Chitayat D, et al. Abnormal pericyte recruitment as a cause for pulmonary hypertension in Adams-Oliver syndrome. Am J Med Genet 2004;129A:294-9.
    • (2004) Am J Med Genet , vol.129 , pp. 294-299
    • Patel, M.S.1    Taylor, G.P.2    Bharya, S.3    Al-Sanna’a, N.4    Adatia, I.5    Chitayat, D.6
  • 95
    • 68049105183 scopus 로고    scopus 로고
    • Adams-Oliver syndrome: Additions to the clinical features and possible role of BMP pathway
    • Baskar S, Kulkarni ML, Kulkarni AM, Vittalrao S, Kulkarni PM. Adams-Oliver syndrome: Additions to the clinical features and possible role of BMP pathway. Am J Med Genet A 2009;149:1678-84.
    • (2009) Am J Med Genet A , vol.149 , pp. 1678-1684
    • Baskar, S.1    Kulkarni, M.L.2    Kulkarni, A.M.3    Vittalrao, S.4    Kulkarni, P.M.5
  • 99
    • 34250820489 scopus 로고    scopus 로고
    • Increased incidence of idiopathic persistent pulmonary hypertension in Down syndrome neonates
    • Cua CL, Blankenship A, North AL, Hayes J, Nelin LD. Increased incidence of idiopathic persistent pulmonary hypertension in Down syndrome neonates. Pediatr Cardiol 2007;28:250-4.
    • (2007) Pediatr Cardiol , vol.28 , pp. 250-254
    • Cua, C.L.1    Blankenship, A.2    North, A.L.3    Hayes, J.4    Nelin, L.D.5
  • 100
    • 0015907889 scopus 로고
    • Progressive pulmonary hypertension in children with portal hypertension
    • Levine OR, Harris RC, Blanc WA, Mellins RB. Progressive pulmonary hypertension in children with portal hypertension. J Pediatr 1973;83:964-72.
    • (1973) J Pediatr , vol.83 , pp. 964-972
    • Levine, O.R.1    Harris, R.C.2    Blanc, W.A.3    Mellins, R.B.4
  • 101
    • 35848971004 scopus 로고    scopus 로고
    • Type 1 neurofibromatosis complicated by pulmonary artery hypertension: A case report
    • Simeoni S, Puccetti A, Chilosi M, Tinazzi E, Prati D, Corrocher R, et al. Type 1 neurofibromatosis complicated by pulmonary artery hypertension: A case report. J Med Invest 2007;54:354-8.
    • (2007) J Med Invest , vol.54 , pp. 354-358
    • Simeoni, S.1    Puccetti, A.2    Chilosi, M.3    Tinazzi, E.4    Prati, D.5    Corrocher, R.6
  • 102
    • 35448991256 scopus 로고    scopus 로고
    • Is pulmonary arterial hypertension in neurofibromatosis type 1 secondary to a plexogenic arteriopathy?
    • Stewart DR, Cogan JD, Kramer MR, Miller WT Jr, Christiansen LE, Pauciulo MW, et al. Is pulmonary arterial hypertension in neurofibromatosis type 1 secondary to a plexogenic arteriopathy? Chest 2007;132:798-808.
    • (2007) Chest , vol.132 , pp. 798-808
    • Stewart, D.R.1    Cogan, J.D.2    Kramer, M.R.3    Miller, W.T.4    Christiansen, L.E.5    Pauciulo, M.W.6
  • 104
    • 0034934303 scopus 로고    scopus 로고
    • Von Recklinghausen disease complicated by pulmonary hypertension
    • Aoki Y, Kodama M, Mezaki T, Ogawa R, Sato M, Okabe M, et al. von Recklinghausen disease complicated by pulmonary hypertension. Chest 2001;119:1606-8.
    • (2001) Chest , vol.119 , pp. 1606-1608
    • Aoki, Y.1    Kodama, M.2    Mezaki, T.3    Ogawa, R.4    Sato, M.5
  • 106
    • 79951966690 scopus 로고    scopus 로고
    • Cantu syndrome: Report of nine new cases and expansion of the clinical phenotype
    • Scurr I, Wilson L, Lees M, Robertson S, Kirk E, Turner A, et al. Cantu syndrome: Report of nine new cases and expansion of the clinical phenotype. Am J Med Genet A 2011;155:508-18.
    • (2011) Am J Med Genet A , vol.155 , pp. 508-518
    • Scurr, I.1    Wilson, L.2    Lees, M.3    Robertson, S.4    Kirk, E.5    Turner, A.6
  • 107
    • 0034663734 scopus 로고    scopus 로고
    • Pulmonary vascular disease in Down’s syndrome with complete atrioventricular septal defect
    • Suzuki K, Yamaki S, Mimori S, Murakami Y, Mori K, Takahashi Y, et al. Pulmonary vascular disease in Down’s syndrome with complete atrioventricular septal defect. Am J Cardiol 2000;86:434-7.
    • (2000) Am J Cardiol , vol.86 , pp. 434-437
    • Suzuki, K.1    Yamaki, S.2    Mimori, S.3    Murakami, Y.4    Mori, K.5    Takahashi, Y.6
  • 108
    • 56149098789 scopus 로고    scopus 로고
    • Aberrant catalytic cycle and impaired lipid transport into intracellular vesicles in ABCA3 mutants associated with nonfatal pediatric interstitial lung disease
    • Matsumura Y, Ban N, Inagaki N. Aberrant catalytic cycle and impaired lipid transport into intracellular vesicles in ABCA3 mutants associated with nonfatal pediatric interstitial lung disease. Am J Physiol Lung Cell Mol Physiol 2008;295:L698-707.
    • (2008) Am J Physiol Lung Cell Mol Physiol , vol.295 , pp. L698-L707
    • Matsumura, Y.1    Ban, N.2    Inagaki, N.3
  • 111
    • 58149517227 scopus 로고    scopus 로고
    • Pulmonary thromboembolism in childhood: A single-center experience from Turkey
    • Tavil B, Kuskonmaz B, Kiper N, Cetin M, Gumruk F, Gurgey A. Pulmonary thromboembolism in childhood: A single-center experience from Turkey. Heart Lung 2009;38:56-65.
    • (2009) Heart Lung , vol.38 , pp. 56-65
    • Tavil, B.1    Kuskonmaz, B.2    Kiper, N.3    Cetin, M.4    Gumruk, F.5    Gurgey, A.6
  • 112
    • 0025324674 scopus 로고
    • Cor pulmonale as a complication of methylmalonic acidemia and homocystinuria (Cbl-C type)
    • Brandstetter Y, Weinhouse E, Splaingard ML, Tang TT. Cor pulmonale as a complication of methylmalonic acidemia and homocystinuria (Cbl-C type). Am J Med Genet 1990;36:167-71.
    • (1990) Am J Med Genet , vol.36 , pp. 167-171
    • Brandstetter, Y.1    Weinhouse, E.2    Splaingard, M.L.3    Tang, T.T.4
  • 113
    • 33646731980 scopus 로고    scopus 로고
    • Calcified pulmonary thromboembolism in a child with sickle cell disease: Value of multidetector CT in patients with acute chest syndrome
    • Staser JA, Alam T, Applegate K. Calcified pulmonary thromboembolism in a child with sickle cell disease: Value of multidetector CT in patients with acute chest syndrome. Pediatr Radiol 2006;36:561-3.
    • (2006) Pediatr Radiol , vol.36 , pp. 561-563
    • Staser, J.A.1    Alam, T.2    Applegate, K.3
  • 115
    • 0013941886 scopus 로고
    • Thromboembolic complications in primary endocardial fibroelastosis
    • Branch GL, Castle RF. Thromboembolic complications in primary endocardial fibroelastosis. J Pediatr 1966;69:250-8.
    • (1966) J Pediatr , vol.69 , pp. 250-258
    • Branch, G.L.1    Castle, R.F.2
  • 116
    • 77953297958 scopus 로고    scopus 로고
    • Pulmonary thromboendarterectomy in adolescents and young adults
    • Johnson JN, Driscoll DJ, McGregor CG. Pulmonary thromboendarterectomy in adolescents and young adults. Pediatr Pulmonol 2010;45:614-8.
    • (2010) Pediatr Pulmonol , vol.45 , pp. 614-618
    • Johnson, J.N.1    Driscoll, D.J.2    McGregor, C.G.3
  • 117
    • 0032710578 scopus 로고    scopus 로고
    • Unilateral right pulmonary thromboendarterectomy for chronic embolism: A successful procedure in an infant
    • discussion 57
    • Lambert V, Durand P, Devictor D, Planche C, Serraf A. Unilateral right pulmonary thromboendarterectomy for chronic embolism: A successful procedure in an infant. J Thorac Cardiovasc Surg 1999;118:953-4; discussion 57.
    • (1999) J Thorac Cardiovasc Surg , vol.118 , pp. 953-954
    • Lambert, V.1    Durand, P.2    Devictor, D.3    Planche, C.4    Serraf, A.5
  • 119
    • 0034913531 scopus 로고    scopus 로고
    • Potential genetic contributions to control of the pulmonary circulation and ventilation at high altitude
    • Fagan KA, Weil JV. Potential genetic contributions to control of the pulmonary circulation and ventilation at high altitude. High Alt Med Biol 2001;2:165-71.
    • (2001) High Alt Med Biol , vol.2 , pp. 165-171
    • Fagan, K.A.1    Weil, J.V.2
  • 121
    • 0346121613 scopus 로고    scopus 로고
    • High-altitude pulmonary hypertension: A pathophysiological entity to different diseases
    • Maggiorini M, Leon-Velarde F. High-altitude pulmonary hypertension: A pathophysiological entity to different diseases. Eur Respir J 2003;22: 1019-25.
    • (2003) Eur Respir J , vol.22 , pp. 1019-1025
    • Maggiorini, M.1    Leon-Velarde, F.2
  • 122
    • 0022365957 scopus 로고
    • Increased lung vasoreactivity in children from Leadville, Colorado, after recovery from high-altitude pulmonary edema
    • Fasules JW, Wiggins JW, Wolfe RR. Increased lung vasoreactivity in children from Leadville, Colorado, after recovery from high-altitude pulmonary edema. Circulation 1985;72:957-62.
    • (1985) Circulation , vol.72 , pp. 957-962
    • Fasules, J.W.1    Wiggins, J.W.2    Wolfe, R.R.3
  • 123
    • 0037252298 scopus 로고    scopus 로고
    • High-altitude pulmonary edema at moderate altitude (< 2,400 m; 7,870 feet): A series of 52 patients
    • Gabry AL, Ledoux X, Mozziconacci M, Martin C. High-altitude pulmonary edema at moderate altitude (< 2,400 m; 7,870 feet): A series of 52 patients. Chest 2003;123:49-53.
    • (2003) Chest , vol.123 , pp. 49-53
    • Gabry, A.L.1    Ledoux, X.2    Mozziconacci, M.3    Martin, C.4
  • 124
    • 9644262373 scopus 로고    scopus 로고
    • High-altitude pulmonary edema in children with underlying cardiopulmonary disorders and pulmonary hypertension living at altitude
    • Das BB, Wolfe RR, Chan KC, Larsen GL, Reeves JT, Ivy D. High-altitude pulmonary edema in children with underlying cardiopulmonary disorders and pulmonary hypertension living at altitude. Arch Pediatr Adolesc Med 2004;158:1170-6.
    • (2004) Arch Pediatr Adolesc Med , vol.158 , pp. 1170-1176
    • Das, B.B.1    Wolfe, R.R.2    Chan, K.C.3    Larsen, G.L.4    Reeves, J.T.5    Ivy, D.6
  • 125
    • 0034884265 scopus 로고    scopus 로고
    • Pulmonary edema in 6 children with Down syndrome during travel to moderate altitudes
    • Durmowicz AG. Pulmonary edema in 6 children with Down syndrome during travel to moderate altitudes. Pediatrics 2001;108:443-7.
    • (2001) Pediatrics , vol.108 , pp. 443-447
    • Durmowicz, A.G.1
  • 127
    • 70649098154 scopus 로고    scopus 로고
    • Non-congenital heart disease associated pediatric pulmonary arterial hypertension
    • Ivy DD, Feinstein JA, Humpl T, Rosenzweig EB. Non-congenital heart disease associated pediatric pulmonary arterial hypertension. Prog Pediatr Cardiol 2009;27:13-23.
    • (2009) Prog Pediatr Cardiol , vol.27 , pp. 13-23
    • Ivy, D.D.1    Feinstein, J.A.2    Humpl, T.3    Rosenzweig, E.B.4
  • 129
    • 33745714464 scopus 로고    scopus 로고
    • Progressive vacuolating glycine leukoencephalopathy with pulmonary hypertension
    • del Toro M, Arranz JA, Macaya A, Riudor E, Raspall M, Moreno A, et al. Progressive vacuolating glycine leukoencephalopathy with pulmonary hypertension. Ann Neurol 2006;60:148-52.
    • (2006) Ann Neurol , vol.60 , pp. 148-152
    • Del Toro, M.1    Arranz, J.A.2    Macaya, A.3    Riudor, E.4    Raspall, M.5    Moreno, A.6
  • 130
    • 77953550230 scopus 로고    scopus 로고
    • Echocardiographic study of paediatric patients with mucopolysaccharidosis
    • Leal GN, de Paula AC, Leone C, Kim CA. Echocardiographic study of paediatric patients with mucopolysaccharidosis. Cardiol Young 2010;20:254-61.
    • (2010) Cardiol Young , vol.20 , pp. 254-261
    • Leal, G.N.1    De Paula, A.C.2    Leone, C.3    Kim, C.A.4
  • 131
    • 70349883809 scopus 로고    scopus 로고
    • Efficacy of oral sildenafil in a beraprost-treated patient with severe pulmonary hypertension secondary to type I glycogen storage disease
    • Ueno M, Murakami T, Takeda A, Kubota M. Efficacy of oral sildenafil in a beraprost-treated patient with severe pulmonary hypertension secondary to type I glycogen storage disease. Circ J 2009;73:1965-8.
    • (2009) Circ J , vol.73 , pp. 1965-1968
    • Ueno, M.1    Murakami, T.2    Takeda, A.3    Kubota, M.4
  • 132
    • 67649739164 scopus 로고    scopus 로고
    • Portopulmonary hypertension associated with congenital absence of the portal vein treated with bosentan
    • Hino T, Hayashida A, Okahashi N, Wada N, Watanabe N, Obase K, et al. Portopulmonary hypertension associated with congenital absence of the portal vein treated with bosentan. Intern Med 2009;48:597-600.
    • (2009) Intern Med , vol.48 , pp. 597-600
    • Hino, T.1    Hayashida, A.2    Okahashi, N.3    Wada, N.4    Watanabe, N.5    Obase, K.6
  • 133
    • 42949138363 scopus 로고    scopus 로고
    • Pulmonary hypertension in patients with congenital portosystemic venous shunt: A previously unrecognized association
    • Ohno T, Muneuchi J, Ihara K, Yuge T, Kanaya Y, Yamaki S, et al. Pulmonary hypertension in patients with congenital portosystemic venous shunt: A previously unrecognized association. Pediatrics 2008;121:e892-9.
    • (2008) Pediatrics , vol.121 , pp. e892-e899
    • Ohno, T.1    Muneuchi, J.2    Ihara, K.3    Yuge, T.4    Kanaya, Y.5    Yamaki, S.6
  • 135
  • 136
    • 77955550089 scopus 로고    scopus 로고
    • Primary pulmonary arterial hypertension and autoimmune polyendocrine syndrome in a pediatric patient
    • Alghamdi MH, Steinraths M, Panagiotopoulos C, Potts JE, Sandor GG. Primary pulmonary arterial hypertension and autoimmune polyendocrine syndrome in a pediatric patient. Pediatr Cardiol 2010;31:872-4.
    • (2010) Pediatr Cardiol , vol.31 , pp. 872-874
    • Alghamdi, M.H.1    Steinraths, M.2    Panagiotopoulos, C.3    Potts, J.E.4    Sandor, G.G.5
  • 137
    • 84862833515 scopus 로고    scopus 로고
    • Clinical analysis of pulmonary arterial hypertension secondary to connective tissue disease in children
    • Xing Y, Song HM, Wu XY, He YY, Wei M. Clinical analysis of pulmonary arterial hypertension secondary to connective tissue disease in children. Zhonghua Er Ke Za Zhi 2008;46:822-6.
    • (2008) Zhonghua Er Ke Za Zhi , vol.46 , pp. 822-826
    • Xing, Y.1    Song, H.M.2    Wu, X.Y.3    He, Y.Y.4    Wei, M.5
  • 138
    • 0016207339 scopus 로고
    • Editorial: Progressive pulmonary hypertension in children with portal hypertension
    • Haworth SG, Hislop A, Reid L. Editorial: Progressive pulmonary hypertension in children with portal hypertension. J Pediatr 1974;84:783-5.
    • (1974) J Pediatr , vol.84 , pp. 783-785
    • Haworth, S.G.1    Hislop, A.2    Reid, L.3
  • 139
    • 0026584609 scopus 로고
    • Association of pulmonary hypertension with congenital portal hypertension in a child
    • Silver MM, Bohn D, Shawn DH, Shuckett B, Eich G, Rabinovitch M. Association of pulmonary hypertension with congenital portal hypertension in a child. J Pediatr 1992;120:321-9.
    • (1992) J Pediatr , vol.120 , pp. 321-329
    • Silver, M.M.1    Bohn, D.2    Shawn, D.H.3    Shuckett, B.4    Eich, G.5    Rabinovitch, M.6
  • 140
    • 0007694758 scopus 로고
    • Primary pulmonary hypertension with coexisting portal hypertension. A retrospective study of six cases
    • Naeye RL. “Primary” pulmonary hypertension with coexisting portal hypertension. A retrospective study of six cases. Circulation 1960;22: 376-84.
    • (1960) Circulation , vol.22 , pp. 376-384
    • Naeye, R.L.1
  • 142
    • 0019222076 scopus 로고
    • Idiopathic pulmonary hypertension associated with nodular pulmonary infiltrates and portal venous thrombosis
    • Bower JS, Dantzker DR, Naylor B. Idiopathic pulmonary hypertension associated with nodular pulmonary infiltrates and portal venous thrombosis. Chest 1980;78:111-3.
    • (1980) Chest , vol.78 , pp. 111-113
    • Bower, J.S.1    Dantzker, D.R.2    Naylor, B.3
  • 143
    • 0020621906 scopus 로고
    • Primary pulmonary hypertension: An unusual case associated with extrahepatic portal hypertension
    • Cohen MD, Rubin LJ, Taylor WE, Cuthbert JA. Primary pulmonary hypertension: An unusual case associated with extrahepatic portal hypertension. Hepatology 1983;3:588-92.
    • (1983) Hepatology , vol.3 , pp. 588-592
    • Cohen, M.D.1    Rubin, L.J.2    Taylor, W.E.3    Cuthbert, J.A.4
  • 145
    • 0023676719 scopus 로고
    • Nodular regenerative hyperplasia of the liver associated with primary pulmonary hypertension
    • Yutani C, Imakita M, Ishibashi-Ueda H, Okubo S, Naito M, Kunieda T. Nodular regenerative hyperplasia of the liver associated with primary pulmonary hypertension. Hum Pathol 1988;19:726-31.
    • (1988) Hum Pathol , vol.19 , pp. 726-731
    • Yutani, C.1    Imakita, M.2    Ishibashi-Ueda, H.3    Okubo, S.4    Naito, M.5    Kunieda, T.6
  • 146
    • 0024728014 scopus 로고
    • Multiple focal nodular hyperplasia of the liver associated with vascular malformations of various organs and neoplasia of the brain: A new syndrome
    • Wanless IR, Albrecht S, Bilbao J, Frei JV, Heathcote EJ, Roberts EA, et al. Multiple focal nodular hyperplasia of the liver associated with vascular malformations of various organs and neoplasia of the brain: A new syndrome. Mod Pathol 1989;2:456-62.
    • (1989) Mod Pathol , vol.2 , pp. 456-462
    • Wanless, I.R.1    Albrecht, S.2    Bilbao, J.3    Frei, J.V.4    Heathcote, E.J.5    Roberts, E.A.6
  • 147
    • 0026316778 scopus 로고
    • Primary pulmonaryy hypertension in a patient with systemic-onset juvenile arthritis
    • Padeh S, Laxer RM, Silver MM, Silverman ED. Primary pulmonaryy hypertension in a patient with systemic-onset juvenile arthritis. Arthritis Rheum 1991;34:1575-9.
    • (1991) Arthritis Rheum , vol.34 , pp. 1575-1579
    • Padeh, S.1    Laxer, R.M.2    Silver, M.M.3    Silverman, E.D.4
  • 149
    • 0031042776 scopus 로고    scopus 로고
    • Primary antiphospholipid syndrome and pulmonary hypertension with prolonged survival. A case report
    • Nagai H, Yasuma K, Katsuki T, Shimakura A, Usuda K, Nakamura Y, et al. Primary antiphospholipid syndrome and pulmonary hypertension with prolonged survival. A case report. Angiology 1997;48:183-7.
    • (1997) Angiology , vol.48 , pp. 183-187
    • Nagai, H.1    Yasuma, K.2    Katsuki, T.3    Shimakura, A.4    Usuda, K.5    Nakamura, Y.6
  • 151
    • 78650661141 scopus 로고    scopus 로고
    • Severe pulmonary hypertension in a young patient with end-stage renal disease on chronic hemodialysis
    • Sharma S, Kirpalani AL, Kulkarni A. Severe pulmonary hypertension in a young patient with end-stage renal disease on chronic hemodialysis. Ann Pediatr Cardiol 2010;3:184-6.
    • (2010) Ann Pediatr Cardiol , vol.3 , pp. 184-186
    • Sharma, S.1    Kirpalani, A.L.2    Kulkarni, A.3
  • 152
    • 0038555346 scopus 로고    scopus 로고
    • Pulmonary hypertension in patients with end-stage renal disease
    • Yigla M, Nakhoul F, Sabag A, Tov N, Gorevich B, Abassi Z, et al. Pulmonary hypertension in patients with end-stage renal disease. Chest 2003;123:1577-82.
    • (2003) Chest , vol.123 , pp. 1577-1582
    • Yigla, M.1    Nakhoul, F.2    Sabag, A.3    Tov, N.4    Gorevich, B.5    Abassi, Z.6
  • 153
    • 67149120620 scopus 로고    scopus 로고
    • Pulmonary hypertension in peritoneal dialysis patients: Prevalence and risk factors
    • Unal A, Sipahioglu M, Oguz F, Kaya M, Kucuk H, Tokgoz B, et al. Pulmonary hypertension in peritoneal dialysis patients: Prevalence and risk factors. Perit Dial Int 2009;29:191-8.
    • (2009) Perit Dial Int , vol.29 , pp. 191-198
    • Unal, A.1    Sipahioglu, M.2    Oguz, F.3    Kaya, M.4    Kucuk, H.5    Tokgoz, B.6
  • 154
    • 0345732496 scopus 로고    scopus 로고
    • Pulmonary hypertension in patients with chronic renal failure: Role of parathyroid hormone and pulmonary artery calcifications
    • Amin M, Fawzy A, Hamid MA, Elhendy A. Pulmonary hypertension in patients with chronic renal failure: Role of parathyroid hormone and pulmonary artery calcifications. Chest 2003;124:2093-7.
    • (2003) Chest , vol.124 , pp. 2093-2097
    • Amin, M.1    Fawzy, A.2    Hamid, M.A.3    Elhendy, A.4
  • 156
    • 84952845539 scopus 로고    scopus 로고
    • Pulmonary veno-occlusive disease
    • Freedom RM, Yoo SJ, Mikailian H, Williams WG, editors, New York: Futura
    • Adatia I. Pulmonary veno-occlusive disease. In: Freedom RM, Yoo SJ, Mikailian H, Williams WG, editors. The natural and modified history of congenital heart disease. New York: Futura; 2004. p. 513.
    • (2004) The Natural and Modified History of Congenital Heart Disease , pp. 513
    • Adatia, I.1
  • 157
    • 77954440147 scopus 로고    scopus 로고
    • Pulmonary hypertension secondary to partial pulmonary venous obstruction in a child with Cantú syndrome
    • Kobayashi D, Cook, A, Williams D. Pulmonary hypertension secondary to partial pulmonary venous obstruction in a child with Cantú syndrome. Pediatr Radiol 2010;45:727-9.
    • (2010) Pediatr Radiol , vol.45 , pp. 727-729
    • Kobayashi, D.1    Cook, A.2    Williams, D.3
  • 158
    • 67651120137 scopus 로고    scopus 로고
    • Premature foetal closure of the arterial duct: Clinical presentations and outcome
    • Gewillig M, Brown SC, De Catte L, Debeer A, Eyskens B, Cossey V, et al. Premature foetal closure of the arterial duct: Clinical presentations and outcome. Eur Heart J 2009;30:1530-6.
    • (2009) Eur Heart J , vol.30 , pp. 1530-1536
    • Gewillig, M.1    Brown, S.C.2    De Catte, L.3    Debeer, A.4    Eyskens, B.5    Cossey, V.6
  • 159
    • 0029873317 scopus 로고    scopus 로고
    • Persistent pulmonary artery hypertension of the newborn and smoking and aspirin and nonsteroidal anti inflammatory drug consumption during pregnancy
    • Van Marter LJ, Leviton A, Allred EN, Pagano M, Sullivan KF, Cohen A, et al. Persistent pulmonary artery hypertension of the newborn and smoking and aspirin and nonsteroidal anti inflammatory drug consumption during pregnancy. Pediatrics 1996;97:658-63.
    • (1996) Pediatrics , vol.97 , pp. 658-663
    • Van Marter, L.J.1    Leviton, A.2    Allred, E.N.3    Pagano, M.4    Sullivan, K.F.5    Cohen, A.6
  • 160
    • 1842558513 scopus 로고    scopus 로고
    • Maternal diclofenac sodium ingestion and severe neonatal pulmonary hypertension
    • Siu KL, Lee WH. Maternal diclofenac sodium ingestion and severe neonatal pulmonary hypertension. J Paediatr Child Health 2004;40:152-3.
    • (2004) J Paediatr Child Health , vol.40 , pp. 152-153
    • Siu, K.L.1    Lee, W.H.2
  • 162
    • 0035120389 scopus 로고    scopus 로고
    • Analysis of nonsteroidal anti-inflammatory drugs in meconium and its relation to persistent pulmonary hypertension of the newborn
    • Alano MA, Ngougmna E, Ostrea EM Jr, Konduri GG. Analysis of nonsteroidal anti-inflammatory drugs in meconium and its relation to persistent pulmonary hypertension of the newborn. Pediatrics 2001;107:519-23.
    • (2001) Pediatrics , vol.107 , pp. 519-523
    • Alano, M.A.1    Ngougmna, E.2    Ostrea, E.M.3    Konduri, G.G.4
  • 163
    • 0031872072 scopus 로고    scopus 로고
    • Severe pulmonary hypertension in a neonate caused by premature closure of the ductus arteriosus following maternal treatment with diclofenac: A case report
    • Zender M, Klinge J, Kruger C, Singer H, Scharf J. Severe pulmonary hypertension in a neonate caused by premature closure of the ductus arteriosus following maternal treatment with diclofenac: A case report. J Perinat Med 1998;26:231-4.
    • (1998) J Perinat Med , vol.26 , pp. 231-234
    • Zender, M.1    Klinge, J.2    Kruger, C.3    Singer, H.4    Scharf, J.5
  • 164
    • 0033020333 scopus 로고    scopus 로고
    • Premature in utero closure of the ductus arteriosus following maternal ingestion of sodium diclofenac
    • Mas C, Menahem S. Premature in utero closure of the ductus arteriosus following maternal ingestion of sodium diclofenac. Aust N Z J Obstet Gynaecol 1999;39:106-7.
    • (1999) Aust N Z J Obstet Gynaecol , vol.39 , pp. 106-107
    • Mas, C.1    Menahem, S.2
  • 165
    • 0033801071 scopus 로고    scopus 로고
    • Persistent pulmonary hypertension after maternal naproxen ingestion in a term newborn: A case report
    • Talati AJ, Salim MA, Korones SB. Persistent pulmonary hypertension after maternal naproxen ingestion in a term newborn: A case report. Am J Perinatol 2000;17:69-71.
    • (2000) Am J Perinatol , vol.17 , pp. 69-71
    • Talati, A.J.1    Salim, M.A.2    Korones, S.B.3


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