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Volumn 43, Issue 12 SUPPL., 2004, Pages S5-S12

Clinical classification of pulmonary hypertension

(12)  Simonneau, Gerald a,m   Galiè, Nazzareno b   Rubin, Lewis J c   Langleben, David d   Seeger, Werner e   Domenighetti, Guido f   Gibbs, Simon g   Lebrec, Didier h   Speich, Rudolf i   Beghetti, Maurice j   Rich, Stuart k   Fishman, Alfred l  


Author keywords

activin receptor like kinase 1; ALK1; APAH; BMPR2; bone morphogenetic protein receptor type II; familial pulmonary arterial hypertension; FPAH; IPAH; pulmonary arterial hypertension related to risk factors or associated conditions

Indexed keywords

CARDIOVASCULAR RISK; CLINICAL EXAMINATION; CLINICAL FEATURE; CLINICAL PRACTICE; CONFERENCE PAPER; DISEASE ASSOCIATION; DISEASE CLASSIFICATION; DRUG APPROVAL; DRUG SCREENING; EMBOLISM; EUROPE; FOOD AND DRUG ADMINISTRATION; FRANCE; GENETIC ASSOCIATION; GENETIC DISORDER; HEMANGIOMATOSIS; HEMATOLOGIC DISEASE; HUMAN; HYPOXEMIA; LUNG ARTERIOVENOUS SHUNT; LUNG CAPILLARY; METABOLIC DISORDER; PATHOPHYSIOLOGY; PRACTICE GUIDELINE; PREVALENCE; PRIORITY JOURNAL; PULMONARY HYPERTENSION; RESPIRATORY SYSTEM; RESPIRATORY TRACT DISEASE; RISK ASSESSMENT; RISK FACTOR; THROMBOSIS; TREATMENT INDICATION; UNITED STATES; VEIN OCCLUSION;

EID: 2942522878     PISSN: 07351097     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jacc.2004.02.037     Document Type: Conference Paper
Times cited : (1606)

References (71)
  • 2
    • 0023615359 scopus 로고
    • Primary pulmonary hypertension: A national prospective study
    • Rich S., Dantzer D.R., Ayres S.M., et al. Primary pulmonary hypertension a national prospective study. Ann Intern Med. 107:1987;216-228
    • (1987) Ann Intern Med , vol.107 , pp. 216-228
    • Rich, S.1    Dantzer, D.R.2    Ayres, S.M.3
  • 4
    • 0034804681 scopus 로고    scopus 로고
    • Clinical classification of pulmonary hypertension
    • Fishman A.P. Clinical classification of pulmonary hypertension. Clin Chest Med. 22:2001;385-391
    • (2001) Clin Chest Med , vol.22 , pp. 385-391
    • Fishman, A.P.1
  • 5
    • 0034814769 scopus 로고    scopus 로고
    • Risk factors for pulmonary arterial hypertension
    • Humbert M., Nunes H., Sitbon O., et al. Risk factors for pulmonary arterial hypertension. Clin Chest Med. 22:2001;459-475
    • (2001) Clin Chest Med , vol.22 , pp. 459-475
    • Humbert, M.1    Nunes, H.2    Sitbon, O.3
  • 6
    • 0030031888 scopus 로고    scopus 로고
    • A comparison of continuous intravenous epoprostenol (prostacyclin) with conventional therapy for primary pulmonary hypertension
    • Barst R.J., Rubin L.J., Long W.A. A comparison of continuous intravenous epoprostenol (prostacyclin) with conventional therapy for primary pulmonary hypertension. N Engl J Med. 334:1996;296-302
    • (1996) N Engl J Med , vol.334 , pp. 296-302
    • Barst, R.J.1    Rubin, L.J.2    Long, W.A.3
  • 7
    • 17144452827 scopus 로고    scopus 로고
    • Continuous intravenous epoprostenol for pulmonary hypertension due to the scleroderma spectrum of disease. a randomized, controlled trial
    • Badesch D.B., Tapson V.F., McGoon M.D., et al. Continuous intravenous epoprostenol for pulmonary hypertension due to the scleroderma spectrum of disease. A randomized, controlled trial. Ann Intern Med. 132:2000;425-434
    • (2000) Ann Intern Med , vol.132 , pp. 425-434
    • Badesch, D.B.1    Tapson, V.F.2    McGoon, M.D.3
  • 8
    • 0030853952 scopus 로고    scopus 로고
    • A randomized controlled trial of epoprostenol therapy for severe congestive heart failure: The Flolan International Randomized Survival Trial (FIRST)
    • Califf R.M., Adams K.F., McKenna W.J., et al. A randomized controlled trial of epoprostenol therapy for severe congestive heart failure the Flolan International Randomized Survival Trial (FIRST). Am Heart J. 134:1997;44-54
    • (1997) Am Heart J , vol.134 , pp. 44-54
    • Califf, R.M.1    Adams, K.F.2    McKenna, W.J.3
  • 9
    • 0022655351 scopus 로고
    • Pulmonary vascular occlusion and fibrosing mediastinitis
    • Berry D.F., Buccigrossi D., Peabody J., et al. Pulmonary vascular occlusion and fibrosing mediastinitis. Chest. 89:1986;296-301
    • (1986) Chest , vol.89 , pp. 296-301
    • Berry, D.F.1    Buccigrossi, D.2    Peabody, J.3
  • 11
    • 0021751145 scopus 로고
    • Long-term course of pulmonary arterial pressure in chronic obstructive pulmonary disease
    • Weitzenblum E., Sautegeau A., Ehrhart M., et al. Long-term course of pulmonary arterial pressure in chronic obstructive pulmonary disease. Am Rev Respir Dis. 130:1984;993-998
    • (1984) Am Rev Respir Dis , vol.130 , pp. 993-998
    • Weitzenblum, E.1    Sautegeau, A.2    Ehrhart, M.3
  • 12
    • 0019460452 scopus 로고
    • Long-term domiciliary oxygen therapy in hypoxic cor pulmonale complicating bronchitis and emphysema
    • British Medical Research Council Party. Long-term domiciliary oxygen therapy in hypoxic cor pulmonale complicating bronchitis and emphysema. Lancet. 1:1981;681-685
    • (1981) Lancet , vol.1 , pp. 681-685
  • 13
    • 0018885920 scopus 로고
    • Continuous or nocturnal oxygen therapy in hypoxemic chronic obstructive lung disease
    • Nocturnal Oxygen Therapy Trial Group. Continuous or nocturnal oxygen therapy in hypoxemic chronic obstructive lung disease. Ann Intern Med. 93:1980;391-398
    • (1980) Ann Intern Med , vol.93 , pp. 391-398
  • 14
    • 0242721247 scopus 로고    scopus 로고
    • Pulmonary endarterectomy: Experience and lessons learned in 1,500 cases
    • Jamieson S.W., Kapelanski D.P., Sakahibara N., et al. Pulmonary endarterectomy experience and lessons learned in 1, 500 cases. Ann Thorac Surg. 76:2003;1457-1464
    • (2003) Ann Thorac Surg , vol.76 , pp. 1457-1464
    • Jamieson, S.W.1    Kapelanski, D.P.2    Sakahibara, N.3
  • 15
    • 0025293720 scopus 로고
    • Chronic major-vessel thromboembolic pulmonary hypertension
    • Moser K.M., Auger W.R., Fedullo P.F. Chronic major-vessel thromboembolic pulmonary hypertension. Circulation. 81:1990;1735-1743
    • (1990) Circulation , vol.81 , pp. 1735-1743
    • Moser, K.M.1    Auger, W.R.2    Fedullo, P.F.3
  • 16
    • 0028557158 scopus 로고
    • Surgical management of unresolved pulmonary embolism. a personal series of 72 patients
    • Simonneau G., Azarian R., Brenot F., et al. Surgical management of unresolved pulmonary embolism. A personal series of 72 patients. Chest. 107:1995;52s-55s
    • (1995) Chest , vol.107
    • Simonneau, G.1    Azarian, R.2    Brenot, F.3
  • 18
    • 0029665252 scopus 로고    scopus 로고
    • Human alvéolar capillaries undergo angiogenesis in pulmonary veno-occlusive disease
    • Schraufnagel D.E., Sekosan M., McGee T., et al. Human alvéolar capillaries undergo angiogenesis in pulmonary veno-occlusive disease. Eur Respir J. 9:1996;346-350
    • (1996) Eur Respir J , vol.9 , pp. 346-350
    • Schraufnagel, D.E.1    Sekosan, M.2    McGee, T.3
  • 19
    • 0035818316 scopus 로고    scopus 로고
    • Effects of the dual endothelin-receptor antagonist bosentan in patients with pulmonary hypertension: A randomised placebo-controlled study
    • Channick R.N., Simonneau G., Sitbon O., et al. Effects of the dual endothelin-receptor antagonist bosentan in patients with pulmonary hypertension a randomised placebo-controlled study. Lancet. 358:2001;1119-1123
    • (2001) Lancet , vol.358 , pp. 1119-1123
    • Channick, R.N.1    Simonneau, G.2    Sitbon, O.3
  • 20
    • 0037149718 scopus 로고    scopus 로고
    • Bosentan therapy for pulmonary arterial hypertension
    • Rubin L.J., Badesch D.B., Barst R.J., et al. Bosentan therapy for pulmonary arterial hypertension. N Engl J Med. 346:2002;896-903
    • (2002) N Engl J Med , vol.346 , pp. 896-903
    • Rubin, L.J.1    Badesch, D.B.2    Barst, R.J.3
  • 21
    • 0037086133 scopus 로고    scopus 로고
    • Continuous subcutaneous infusion of treprostinil, a prostacyclin analogue, in patients with pulmonary arterial hypertension: A double-blind randomized controlled trial
    • Simonneau G., Barst R.J., Galie N., et al. Continuous subcutaneous infusion of treprostinil, a prostacyclin analogue, in patients with pulmonary arterial hypertension a double-blind randomized controlled trial. Am J Respir Crit Care Med. 165:2002;800-804
    • (2002) Am J Respir Crit Care Med , vol.165 , pp. 800-804
    • Simonneau, G.1    Barst, R.J.2    Galie, N.3
  • 22
    • 0036682273 scopus 로고    scopus 로고
    • Inhaled iloprost in severe pulmonary hypertension
    • Olschewski H., Simonneau G., Galie N., et al. Inhaled iloprost in severe pulmonary hypertension. N Engl J Med. 347:2002;322-327
    • (2002) N Engl J Med , vol.347 , pp. 322-327
    • Olschewski, H.1    Simonneau, G.2    Galie, N.3
  • 23
    • 0033817459 scopus 로고    scopus 로고
    • Heterozygous germ-line mutations in BMPR2, encoding a TGF-β receptor, cause familial primary pulmonary hypertension
    • Lane KB, Machado RD, Pauciulo, et al., for the International PPH Consortium. Heterozygous germ-line mutations in BMPR2, encoding a TGF-β receptor, cause familial primary pulmonary hypertension. Nat Genet 2000;26:81-4
    • (2000) Nat Genet , vol.26 , pp. 81-84
    • Lane, K.B.1    Machado, R.D.2    Pauciulo3
  • 24
    • 0033623296 scopus 로고    scopus 로고
    • Sporadic primary pulmonary hypertension is associated with germline mutations of the gene encoding BMPR-II, a receptor member of the TGF-β family
    • Thomson J.R., Machado R.D., Pauciulo M.W., et al. Sporadic primary pulmonary hypertension is associated with germline mutations of the gene encoding BMPR-II, a receptor member of the TGF-β family. J Med Genet. 37:2000;741-745
    • (2000) J Med Genet , vol.37 , pp. 741-745
    • Thomson, J.R.1    MacHado, R.D.2    Pauciulo, M.W.3
  • 25
    • 0035797529 scopus 로고    scopus 로고
    • Mutation in the gene for bone morphogenetic protein receptor II as a cause of primary pulmonary hypertension in a large kindred
    • Newman J.H., Wheeler L., Lane K.B., et al. Mutation in the gene for bone morphogenetic protein receptor II as a cause of primary pulmonary hypertension in a large kindred. N Engl J Med. 345:2001;319-324
    • (2001) N Engl J Med , vol.345 , pp. 319-324
    • Newman, J.H.1    Wheeler, L.2    Lane, K.B.3
  • 26
    • 18544376034 scopus 로고    scopus 로고
    • BMPR2 germline mutations in pulmonary hypertension associated with fenfluramine derivatives
    • Humbert M., Deng Z., Simonneau G., et al. BMPR2 germline mutations in pulmonary hypertension associated with fenfluramine derivatives. Eur Respir J. 20:2002;518-523
    • (2002) Eur Respir J , vol.20 , pp. 518-523
    • Humbert, M.1    Deng, Z.2    Simonneau, G.3
  • 27
    • 0037445221 scopus 로고    scopus 로고
    • Pulmonary veno-occlusive disease caused by an inherited mutation in bone morphogenetic protein receptor II
    • Runo J.R., Vnencak-Jones C.L., Prince M., et al. Pulmonary veno-occlusive disease caused by an inherited mutation in bone morphogenetic protein receptor II. Am J Respir Crit Care Med. 167:2003;889-894
    • (2003) Am J Respir Crit Care Med , vol.167 , pp. 889-894
    • Runo, J.R.1    Vnencak-Jones, C.L.2    Prince, M.3
  • 28
    • 0036844311 scopus 로고    scopus 로고
    • Pulmonary hypertension in scleroderma spectrum of disease: Lack of bone morphogenetic protein receptor-2 mutations
    • Morse J.H., Barst R.J., Horn E., et al. Pulmonary hypertension in scleroderma spectrum of disease lack of bone morphogenetic protein receptor-2 mutations. J Rheumatol. 29:2002;2379-2381
    • (2002) J Rheumatol , vol.29 , pp. 2379-2381
    • Morse, J.H.1    Barst, R.J.2    Horn, E.3
  • 29
    • 0034776773 scopus 로고    scopus 로고
    • Serotonin transporter overexpression is responsible for pulmonary artery smooth muscle hyperplasia in primary pulmonary hypertension
    • Eddahibi S., Humbert M., Fadel E., et al. Serotonin transporter overexpression is responsible for pulmonary artery smooth muscle hyperplasia in primary pulmonary hypertension. J Clin Invest. 108:2001;1141-1150
    • (2001) J Clin Invest , vol.108 , pp. 1141-1150
    • Eddahibi, S.1    Humbert, M.2    Fadel, E.3
  • 30
    • 0000171286 scopus 로고
    • Ueber sklerose der lungen arterie
    • Romberg E. Ueber sklerose der lungen arterie. Dtsch Archiv Klin Med. 48:1891;197-206
    • (1891) Dtsch Archiv Klin Med , vol.48 , pp. 197-206
    • Romberg, E.1
  • 31
    • 50449119090 scopus 로고
    • Primary pulmonary hypertension. Clinical and hemodynamic study
    • Dresdale D.T., Schultz M., Michtom R.J. Primary pulmonary hypertension. Clinical and hemodynamic study. Am J Med. 11:1951;686-705
    • (1951) Am J Med , vol.11 , pp. 686-705
    • Dresdale, D.T.1    Schultz, M.2    Michtom, R.J.3
  • 32
    • 2942574709 scopus 로고    scopus 로고
    • Pathologic assessment of vasculopathies in pulmonary hypertension
    • Pietra GG, Capron F, Stewart S, et al. Pathologic assessment of vasculopathies in pulmonary hypertension. J Am Coll Cardiol 2004;43 Suppl S:25S-32S
    • (2004) J Am Coll Cardiol , Issue.43 SUPPL. S
    • Pietra, G.G.1    Capron, F.2    Stewart, S.3
  • 33
    • 0017721482 scopus 로고
    • Pulmonary veno-occlusive disease: Report of a case with pseudoangiomatous features
    • Daroca P.J., Mansfield R.E., Ichinose H. Pulmonary veno-occlusive disease report of a case with pseudoangiomatous features. Am J Surg Pathol. 12:1977;349-355
    • (1977) Am J Surg Pathol , vol.12 , pp. 349-355
    • Daroca, P.J.1    Mansfield, R.E.2    Ichinose, H.3
  • 34
    • 0003029141 scopus 로고    scopus 로고
    • The pathology of primary pulmonary hypertension
    • L.J. Rubin, & S. Rich. New York, NY: Marcel Dekker
    • Pietra G.G. The pathology of primary pulmonary hypertension. Rubin L.J., Rich S. Primary Pulmonary Hypertension: Lung Biology in Health and Disease. 1997;19-61 Marcel Dekker, New York, NY
    • (1997) Primary Pulmonary Hypertension: Lung Biology in Health and Disease , pp. 19-61
    • Pietra, G.G.1
  • 35
    • 0031799904 scopus 로고    scopus 로고
    • Pulmonary edema complicating continuous intravenous prostacyclin in pulmonary capillary hemangiomatosis
    • Humbert M., Maitre S., Capron F., et al. Pulmonary edema complicating continuous intravenous prostacyclin in pulmonary capillary hemangiomatosis. Am J Crit Care Med. 157:1998;1681-1685
    • (1998) Am J Crit Care Med , vol.157 , pp. 1681-1685
    • Humbert, M.1    Maitre, S.2    Capron, F.3
  • 36
    • 0036190042 scopus 로고    scopus 로고
    • Pulmonary arterial hypertension; Thin-section CT predictors of epoprostenol failure
    • Resten A., Maitre S., Musset D., et al. Pulmonary arterial hypertension; thin-section CT predictors of epoprostenol failure. Radiology. 222:2002;782-788
    • (2002) Radiology , vol.222 , pp. 782-788
    • Resten, A.1    Maitre, S.2    Musset, D.3
  • 37
    • 24844474079 scopus 로고    scopus 로고
    • Significant occlusive lesions of pulmonary veins are in common with pulmonary hypertension (PH) associated to connective tissue (CTD)
    • (abstr)
    • Dorfmüller P., Humbert M., Sanchez O., et al. Significant occlusive lesions of pulmonary veins are in common with pulmonary hypertension (PH) associated to connective tissue (CTD). (abstr) Am J Crit Care Med. 167:2003;A694
    • (2003) Am J Crit Care Med , vol.167 , pp. 694
    • Dorfmüller, P.1    Humbert, M.2    Sanchez, O.3
  • 38
    • 0028302671 scopus 로고
    • Pulmonary veno-occlusive disease: Another vascular disorder associated with human immunodeficiency virus infection?
    • Ruchelli E.D., Nojadera G., Rutstein R.M., et al. Pulmonary veno-occlusive disease another vascular disorder associated with human immunodeficiency virus infection? Arch Pathol Lab Med. 118:1994;664-666
    • (1994) Arch Pathol Lab Med , vol.118 , pp. 664-666
    • Ruchelli, E.D.1    Nojadera, G.2    Rutstein, R.M.3
  • 39
    • 0028804735 scopus 로고
    • Pulmonary veno-occlusive disease in a HIV-infected intravenous drug abuser
    • Escamilla R., Hermant C., Berjaud K.L., et al. Pulmonary veno-occlusive disease in a HIV-infected intravenous drug abuser. Eur Respir J. 8:1995;1982-1984
    • (1995) Eur Respir J , vol.8 , pp. 1982-1984
    • Escamilla, R.1    Hermant, C.2    Berjaud, K.L.3
  • 40
    • 0017676686 scopus 로고
    • Familial pulmonary veno-occlusive disease: A case report
    • Woordes C.G., Kuipers J.R.G., Elema J.D., et al. Familial pulmonary veno-occlusive disease a case report. Thorax. 32:1977;763-766
    • (1977) Thorax , vol.32 , pp. 763-766
    • Woordes, C.G.1    Kuipers, J.R.G.2    Elema, J.D.3
  • 41
    • 0023681905 scopus 로고
    • Familial pulmonary capillary hemangiomatosis resulting in primary pulmonary hypertension
    • Langleben D., Heneghan J.M., Batten A.P., et al. Familial pulmonary capillary hemangiomatosis resulting in primary pulmonary hypertension. Ann Intern Med. 109:1988;106-109
    • (1988) Ann Intern Med , vol.109 , pp. 106-109
    • Langleben, D.1    Heneghan, J.M.2    Batten, A.P.3
  • 42
    • 0034118327 scopus 로고    scopus 로고
    • Anorexigens and pulmonary hypertension in the United States: Results from the Surveillance of North American Pulmonary Hypertension
    • Rich S., Rubin L., Walker A.L., et al. Anorexigens and pulmonary hypertension in the United States results from the Surveillance of North American Pulmonary Hypertension. Chest. 117:2000;870-874
    • (2000) Chest , vol.117 , pp. 870-874
    • Rich, S.1    Rubin, L.2    Walker, A.L.3
  • 43
    • 19944407650 scopus 로고    scopus 로고
    • Temporal trends in the number of reported cases of pulmonary hypertension and use of anorexigens, antidepressants and amphetamines, between 1998 and 2001
    • In press
    • Langleben D, Walker AB, Korelitz JJ, et al. Temporal trends in the number of reported cases of pulmonary hypertension and use of anorexigens, antidepressants and amphetamines, between 1998 and 2001 (abstr). Am J Crit Care Med 2004. In press
    • (2004) Am J Crit Care Med
    • Langleben, D.1    Walker, A.B.2    Korelitz, J.J.3
  • 45
    • 0037441758 scopus 로고    scopus 로고
    • Pulmonary hypertension in sickle cell disease: Cardiac catheterization results and survival
    • Castro O., Hoque M., Brown B.D. Pulmonary hypertension in sickle cell disease cardiac catheterization results and survival. Blood. 101:2003;1257-1261
    • (2003) Blood , vol.101 , pp. 1257-1261
    • Castro, O.1    Hoque, M.2    Brown, B.D.3
  • 46
    • 0042805260 scopus 로고    scopus 로고
    • Hemolytic anemia-associated pulmonary hypertension of sickle cell disease and the nitric oxide/arginine pathway
    • Jison M.L., Gladwin M.T. Hemolytic anemia-associated pulmonary hypertension of sickle cell disease and the nitric oxide/arginine pathway. Am J Respir Crit Care Med. 168:2003;3-4
    • (2003) Am J Respir Crit Care Med , vol.168 , pp. 3-4
    • Jison, M.L.1    Gladwin, M.T.2
  • 47
    • 0035665831 scopus 로고    scopus 로고
    • Pulmonary complications of sickle cell anemia. a need for increased recognition, treatment and research
    • Minter K.R., Gladwin M.T. Pulmonary complications of sickle cell anemia. A need for increased recognition, treatment and research. Am J Respir Crit Care Med. 164:2001;2016-2019
    • (2001) Am J Respir Crit Care Med , vol.164 , pp. 2016-2019
    • Minter, K.R.1    Gladwin, M.T.2
  • 48
    • 0042890574 scopus 로고    scopus 로고
    • Pulmonary arterial hypertension in previously splenectomized patients with β-thalassemic disorders
    • Atichartakarn V., Likittanasombat K., Chuncharunee S., et al. Pulmonary arterial hypertension in previously splenectomized patients with β-thalassemic disorders. Int J Hematol. 78:2003;139-145
    • (2003) Int J Hematol , vol.78 , pp. 139-145
    • Atichartakarn, V.1    Likittanasombat, K.2    Chuncharunee, S.3
  • 49
    • 0027535077 scopus 로고
    • Pulmonary hypertension secondary to thrombocytosis in a patient with myeloid metaplasia
    • Marvin K.S., Spellberg R.D. Pulmonary hypertension secondary to thrombocytosis in a patient with myeloid metaplasia. Chest. 103:1993;642-644
    • (1993) Chest , vol.103 , pp. 642-644
    • Marvin, K.S.1    Spellberg, R.D.2
  • 50
    • 0025782856 scopus 로고
    • Pulmonary hypertension associated with long-standing thrombocytosis
    • Rostagno C., Prisco D., Abbate R., et al. Pulmonary hypertension associated with long-standing thrombocytosis. Chest. 99:1991;1303-1305
    • (1991) Chest , vol.99 , pp. 1303-1305
    • Rostagno, C.1    Prisco, D.2    Abbate, R.3
  • 51
    • 0345390838 scopus 로고    scopus 로고
    • Pulmonary hypertension in patients with myelofibrosis secondary to myeloproliferative diseases
    • Garcia-Manero G., Schuster S.J., Patrick H., et al. Pulmonary hypertension in patients with myelofibrosis secondary to myeloproliferative diseases. Am J Hematol. 60:1999;130-135
    • (1999) Am J Hematol , vol.60 , pp. 130-135
    • Garcia-Manero, G.1    Schuster, S.J.2    Patrick, H.3
  • 52
    • 0034832857 scopus 로고    scopus 로고
    • Unexplained pulmonary hypertension in chronic myeloproliferative disorders
    • Dingli D., Utz J.P., Krowka M.J., et al. Unexplained pulmonary hypertension in chronic myeloproliferative disorders. Chest. 120:2001;801-808
    • (2001) Chest , vol.120 , pp. 801-808
    • Dingli, D.1    Utz, J.P.2    Krowka, M.J.3
  • 53
    • 0018819647 scopus 로고
    • Type 1 glycogen storage disease with focal nodular hyperplasia of the liver and vasoconstrictive pulmonary hypertension
    • Pizzo C.J. Type 1 glycogen storage disease with focal nodular hyperplasia of the liver and vasoconstrictive pulmonary hypertension. Pediatrics. 65:1980;341-343
    • (1980) Pediatrics , vol.65 , pp. 341-343
    • Pizzo, C.J.1
  • 54
    • 0029121574 scopus 로고
    • Genetic basis of glycogen storage disease type I: Prevalent mutations at the glucose-6-phosphatase locus
    • Lei K.J., Chen Y.T., Chen H. Genetic basis of glycogen storage disease type I prevalent mutations at the glucose-6-phosphatase locus. Am J Hum Genet. 57:1995;766-771
    • (1995) Am J Hum Genet , vol.57 , pp. 766-771
    • Lei, K.J.1    Chen, Y.T.2    Chen, H.3
  • 55
    • 0035989333 scopus 로고    scopus 로고
    • Pulmonary arterial hypertension and type-I-glycogen-storage disease: The serotonin hypothesis
    • Humbert M., Labrune P., Sitbon O., et al. Pulmonary arterial hypertension and type-I-glycogen-storage disease the serotonin hypothesis. Eur Respir J. 20:2002;59-65
    • (2002) Eur Respir J , vol.20 , pp. 59-65
    • Humbert, M.1    Labrune, P.2    Sitbon, O.3
  • 56
    • 0030317958 scopus 로고    scopus 로고
    • Pulmonary hypertension developing after alglucerase therapy in two patients with type 1 Gaucher disease complicated by the hepatopulmonary syndrome
    • Dawson A., Elias D.J., Rubenson D., et al. Pulmonary hypertension developing after alglucerase therapy in two patients with type 1 Gaucher disease complicated by the hepatopulmonary syndrome. Ann Intern Med. 125:1996;901-912
    • (1996) Ann Intern Med , vol.125 , pp. 901-912
    • Dawson, A.1    Elias, D.J.2    Rubenson, D.3
  • 57
    • 0036130082 scopus 로고    scopus 로고
    • Bone morphogenetic protein receptor-2 mutations in pulmonary hypertension
    • Morse J.H. Bone morphogenetic protein receptor-2 mutations in pulmonary hypertension. Chest. 121:2002;50S-53S
    • (2002) Chest , vol.121
    • Morse, J.H.1
  • 58
    • 0014565337 scopus 로고
    • Pulmonary hypertension in patients with pulmonary arteriovenous fistulae
    • Sapru R.P., Hutchison D.C., Hall J.I. Pulmonary hypertension in patients with pulmonary arteriovenous fistulae. Br Heart J. 31:1969;559-569
    • (1969) Br Heart J , vol.31 , pp. 559-569
    • Sapru, R.P.1    Hutchison, D.C.2    Hall, J.I.3
  • 59
    • 0015374630 scopus 로고
    • Familial pulmonary hypertension and multiple abnormalities of large systemic arteries in Osler's disease
    • Trell E., Johansson B.W., Linell F., et al. Familial pulmonary hypertension and multiple abnormalities of large systemic arteries in Osler's disease. Am J Med. 53:1972;50-63
    • (1972) Am J Med , vol.53 , pp. 50-63
    • Trell, E.1    Johansson, B.W.2    Linell, F.3
  • 60
    • 0035797556 scopus 로고    scopus 로고
    • Clinical and molecular genetic features of pulmonary hypertension in patients with hereditary hemorrhagic telangiectasia
    • Trembath R.C., Thomson J.R., Machado R.D., et al. Clinical and molecular genetic features of pulmonary hypertension in patients with hereditary hemorrhagic telangiectasia. N Engl J Med. 345:2001;325-334
    • (2001) N Engl J Med , vol.345 , pp. 325-334
    • Trembath, R.C.1    Thomson, J.R.2    MacHado, R.D.3
  • 61
    • 2442519516 scopus 로고    scopus 로고
    • Endoglin germline mutation in a patient with hereditary haemorrhagic telangiectasia and dexfenfluramine associated pulmonary arterial hypertension
    • In press
    • Chaouat A, Coulet F, Favre C, et al. Endoglin germline mutation in a patient with hereditary haemorrhagic telangiectasia and dexfenfluramine associated pulmonary arterial hypertension. Thorax 2004. In press
    • (2004) Thorax
    • Chaouat, A.1    Coulet, F.2    Favre, C.3
  • 62
    • 0002569461 scopus 로고
    • Die angeboren defects des kammerscheidewand des herzen]
    • Eisenmenger V. Die angeboren defects des kammerscheidewand des herzen]. Z Klin Med. 32:1897;1-28
    • (1897) Z Klin Med , vol.32 , pp. 1-28
    • Eisenmenger, V.1
  • 63
    • 70449220431 scopus 로고
    • The Eisenmenger syndrome or pulmonary hypertension with reversed central shunt
    • Wood P. The Eisenmenger syndrome or pulmonary hypertension with reversed central shunt. Br Med J. 2:1958;701-709
    • (1958) Br Med J , vol.2 , pp. 701-709
    • Wood, P.1
  • 64
    • 0027398136 scopus 로고
    • Second natural history study of congenital heart defects. Results of treatment of patients with ventricular septal defects
    • Kidd L., Driscoll D., Gersony W., et al. Second natural history study of congenital heart defects. Results of treatment of patients with ventricular septal defects. Circulation. 87:1993;138-151
    • (1993) Circulation , vol.87 , pp. 138-151
    • Kidd, L.1    Driscoll, D.2    Gersony, W.3
  • 65
    • 0026562479 scopus 로고
    • Familial pulmonary hypertension: Immunogenetic findings in four Caucasian kindreds
    • Morse J.H., Barst R.J., Fotino M. Familial pulmonary hypertension immunogenetic findings in four Caucasian kindreds. Am Rev Respir Dis. 145:1992;787-792
    • (1992) Am Rev Respir Dis , vol.145 , pp. 787-792
    • Morse, J.H.1    Barst, R.J.2    Fotino, M.3
  • 66
    • 0032402278 scopus 로고    scopus 로고
    • Eisenmenger syndrome. Factors relating to deterioration and death
    • Daliento L., Somerville J., Presbitero P., et al. Eisenmenger syndrome. Factors relating to deterioration and death. Eur Heart J. 19:1998;1845-1855
    • (1998) Eur Heart J , vol.19 , pp. 1845-1855
    • Daliento, L.1    Somerville, J.2    Presbitero, P.3
  • 67
    • 0017864964 scopus 로고
    • Chronic cor pulmonale in pulmonary sarcoidosis
    • Battesti J.P., Georges R., Basset F., et al. Chronic cor pulmonale in pulmonary sarcoidosis. Thorax. 33:1978;76-84
    • (1978) Thorax , vol.33 , pp. 76-84
    • Battesti, J.P.1    Georges, R.2    Basset, F.3
  • 68
    • 0026458211 scopus 로고
    • Pulmonary vascular involvement in sarcoidosis: A report of 40 autopsy cases
    • Takemura T., Matsui Y., Saiki S., et al. Pulmonary vascular involvement in sarcoidosis a report of 40 autopsy cases. Hum Pathol. 23:1992;1216-1223
    • (1992) Hum Pathol , vol.23 , pp. 1216-1223
    • Takemura, T.1    Matsui, Y.2    Saiki, S.3
  • 70
    • 0030904181 scopus 로고    scopus 로고
    • Prognosis value of pulmonary hypertension in patients with chronic interstitial lung disease referred for lung or heart-lung transplantation
    • Harari S., Simonneau G., De Juli E., et al. Prognosis value of pulmonary hypertension in patients with chronic interstitial lung disease referred for lung or heart-lung transplantation. J Heart Lung Transplant. 16:1997;460-463
    • (1997) J Heart Lung Transplant , vol.16 , pp. 460-463
    • Harari, S.1    Simonneau, G.2    De Juli, E.3
  • 71
    • 0030032626 scopus 로고    scopus 로고
    • Pulmonary histiocytosis X: Pulmonary function and exercise pathophysiology
    • Craussman R.S., Jennings C.A., Tuder R.M., et al. Pulmonary histiocytosis X pulmonary function and exercise pathophysiology. Am J Respir Crit Care Med. 153:1996;426-435
    • (1996) Am J Respir Crit Care Med , vol.153 , pp. 426-435
    • Craussman, R.S.1    Jennings, C.A.2    Tuder, R.M.3


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.