Is pulmonary arterial hypertension in neurofibromatosis type 1 secondary to a plexogenic arteriopathy?

Chest

Volumn 132, Issue 3, 2007, Pages 798-808

  Stewart, Douglas R ^a   Cogan, Joy D ^b   Kramer, Mordechai R ^c   Miller Jr , Wallace T ^d   Christiansen, Leif E ^e   Pauciulo, Michael W ^f   Messiaen, Ludwine M ^g   Tu, George S ^h   Thompson, William H ⁱ   Pyeritz, Reed E ^d   Ryu, Jay H ^j   Nichols, William C ^f   Kodama, Makoto ^k   Meyrick, Barbara O ^b   Ross, David J ^l  

^a NATIONAL HUMAN GENOME RESEARCH INSTITUTE   (United States)

^b VANDERBILT UNIVERSITY MEDICAL CENTER   (United States)

^c RABIN MEDICAL CENTER   (Israel)

^d UNIVERSITY OF PENNSYLVANIA   (United States)

^e St Joseph's Hospital   (United States)

^f CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^g UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^h Lung Center of Nevada   (United States)

ⁱ UNIVERSITY OF WASHINGTON   (United States)

^j MAYO CLINIC   (United States)

^k NIIGATA UNIVERSITY   (Japan)

^l UNIVERSITY OF CALIFORNIA   (United States)

more..

Author keywords

Bone morphogenic protein 2; Mosaic perfusion pattern of lung attenuation; Neurofibromatosis type 1; Plexiform arteriopathy; Vasculopathy

Indexed keywords

BMPR2 PROTEIN, HUMAN; BONE MORPHOGENETIC PROTEIN RECEPTOR 2; UNCLASSIFIED DRUG;

ADULT; AGED; ARTICLE; CASE REPORT; FEMALE; GENETICS; HUMAN; MALE; MIDDLE AGED; MUTATION; NEUROFIBROMATOSIS; PATHOLOGY; PHYSIOLOGY; PULMONARY HYPERTENSION; RADIOGRAPHY; TUMOR SUPPRESSOR GENE;

ADULT; AGED; BONE MORPHOGENETIC PROTEIN RECEPTORS, TYPE II; FEMALE; GENES, NEUROFIBROMATOSIS 1; HUMANS; HYPERTENSION, PULMONARY; MALE; MIDDLE AGED; MUTATION; NEUROFIBROMATOSIS 1;

EID: 35448991256     PISSN: 00123692     EISSN: 19313543     Source Type: Journal    
DOI: 10.1378/chest.06-3017     Document Type: Article

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