Type 1 neurofibromatosis complicated by pulmonary artery hypertension: A case report

Journal of Medical Investigation

Volumn 54, Issue 3-4, 2007, Pages 354-358

  Simeoni, Sara ^a   Puccetti, Antonio ^b   Chilosi, Marco ^a   Tinazzi, Elisa ^a   Prati, Daniele ^c   Corrocher, Roberto ^a   Lunardi, Claudio ^a  

^a UNIVERSITY OF VERONA   (Italy)

^b G GASLINI INSTITUTE   (Italy)

^c UNIVERSITY HOSPITAL OF VERONA   (Italy)

Author keywords

Bone morphogenetic protein receptor 2; Neurofibromatosis type 1; Pulmonary artery hypertension

Indexed keywords

BONE MORPHOGENETIC PROTEIN RECEPTOR 2; BOSENTAN; DIURETIC AGENT; SILDENAFIL; WARFARIN; BMPR2 PROTEIN, HUMAN; UNCLASSIFIED DRUG;

ADULT; ARTERY INTIMA PROLIFERATION; ARTICLE; CASE REPORT; CAUCASIAN; DISEASE ASSOCIATION; DYSPNEA; FEMALE; FIBROSIS; GENETIC ANALYSIS; HISTOLOGY; HUMAN; HUMAN TISSUE; HYPERTROPHY; LUNG PARENCHYMA; NEUROFIBROMATOSIS; PULMONARY HYPERTENSION; SCREENING; TRANSTHORACIC ECHOCARDIOGRAPHY; VASCULAR DISEASE; GENETICS; MIDDLE AGED; NUCLEOTIDE SEQUENCE; PATHOLOGY;

BONE MORPHOGENETIC PROTEIN RECEPTORS, TYPE II; DNA MUTATIONAL ANALYSIS; FEMALE; HUMANS; HYPERTENSION, PULMONARY; MIDDLE AGED; NEUROFIBROMATOSIS 1;

EID: 35848971004     PISSN: 13431420     EISSN: None     Source Type: Journal    
DOI: 10.2152/jmi.54.354     Document Type: Article

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