Thymic involution and corticosterone level in Sandhoff disease model mice: New aspects the pathogenesis of GM2 gangliosidosis

Journal of Inherited Metabolic Disease

Volumn 34, Issue 5, 2011, Pages 1061-1068

  Matsuoka, Kazuhiko ^a   Tsuji, Daisuke ^a,c   Taki, Takao ^b   Itoh, Kohji ^a,c  

^a UNIVERSITY OF TOKUSHIMA   (Japan)

^b OTSUKA PHARMACEUTICAL CO LTD   (Japan)

^c NATIONAL INSTITUTE OF BIOMEDICAL INNOVATION   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

CASPASE 3; CASPASE 4; CASPASE 6; CASPASE 7; CASPASE 8; CASPASE 9; CORTICOSTERONE; INTERLEUKIN 1BETA CONVERTING ENZYME; LIPOCORTIN 5; PROPIDIUM IODIDE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; CELL COUNT; CELL STRUCTURE; CELL SURFACE; CONTROLLED STUDY; CORTICOSTERONE BLOOD LEVEL; DISEASE COURSE; DISEASE MARKER; ENZYME ACTIVATION; INVOLUTION; MOUSE; NICK END LABELING; NONHUMAN; PATHOGENESIS; PROTEIN BINDING; SANDHOFF DISEASE; THYMIC INVOLUTION; THYMOCYTE;

AGE FACTORS; ANIMALS; APOPTOSIS; ATROPHY; BETA-HEXOSAMINIDASE ALPHA CHAIN; CASPASES; CORTICOSTERONE; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; G(M2) GANGLIOSIDE; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; PHENOTYPE; SANDHOFF DISEASE; THYMUS GLAND;

EID: 82955203854     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-011-9316-6     Document Type: Article

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