The podocyte as a target: Cyclosporin A in the management of the nephrotic syndrome caused by WT1 mutations

European Journal of Pediatrics

Volumn 170, Issue 11, 2011, Pages 1377-1383

  Stefanidis, Constantinos J ^a   Querfeld, Uwe ^b  

^a P AND A KYRIAKOU CHILDREN S HOSPITAL   (Greece)

^b CHARITÉ UNIVERSITÄTSMEDIZIN BERLIN   (Germany)

Author keywords

Cyclosporin A; Denys Drash syndrome; Frasier syndrome; Steroid resistant nephrotic syndrome; Wilms' tumour suppressor gene (WT1) mutations; WT1 associated glomerulopathies

Indexed keywords

CYCLOSPORIN A; DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR; INTERLEUKIN 10; PREDNISONE; WT1 PROTEIN;

APOPTOSIS; CELL DEATH; CHROMOSOME 11P; DENYS DRASH SYNDROME; DIFFUSE MESANGIAL GLOMERULOSCLEROSIS; DRUG EFFECT; DRUG TARGETING; FOCAL GLOMERULOSCLEROSIS; FRASIER SYNDROME; GENE MUTATION; GLOMERULOPATHY; HUMAN; INTRON; NEPHROBLASTOMA; PODOCYTE; PRIORITY JOURNAL; PROTEIN FUNCTION; REVIEW; TREATMENT RESPONSE;

AGE FACTORS; ANGIOTENSIN-CONVERTING ENZYME INHIBITORS; CHILD, PRESCHOOL; CYCLOSPORINE; DENYS-DRASH SYNDROME; DRUG RESISTANCE; DRUG THERAPY, COMBINATION; FEMALE; FRASIER SYNDROME; GENES, WILMS TUMOR; HUMANS; IMMUNOSUPPRESSIVE AGENTS; INFANT; INFANT, NEWBORN; MALE; METHYLPREDNISOLONE; MOLECULAR TARGETED THERAPY; MUTATION; NEPHROTIC SYNDROME; PODOCYTES;

EID: 82655189962     PISSN: 03406199     EISSN: 14321076     Source Type: Journal    
DOI: 10.1007/s00431-011-1397-6     Document Type: Review

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