-
1
-
-
0019423856
-
Sequence and organization of the human mitochondrial genome
-
Anderson S., Bankier A.T., Barrel B.G., De Bruijn M.H.L., Coulson A.R., Drouin J., Eperon I.C., Nierlich D.P., Roe B.A., Sanger F., Schreier P.H., Smith A.J., Staden R., Young I.G. Sequence and organization of the human mitochondrial genome. Nature 1981, 290:457-465.
-
(1981)
Nature
, vol.290
, pp. 457-465
-
-
Anderson, S.1
Bankier, A.T.2
Barrel, B.G.3
De Bruijn, M.H.L.4
Coulson, A.R.5
Drouin, J.6
Eperon, I.C.7
Nierlich, D.P.8
Roe, B.A.9
Sanger, F.10
Schreier, P.H.11
Smith, A.J.12
Staden, R.13
Young, I.G.14
-
2
-
-
0022545789
-
Treatment of mitochondrial myopathy due to complex III deficiency with vitamins K3 and C: a 31P-NMR follow-up study
-
Arogov Z., Bank W.J., Maris J., Eleff S., Kennaway N.G., Olson R.E., Chance B. Treatment of mitochondrial myopathy due to complex III deficiency with vitamins K3 and C: a 31P-NMR follow-up study. Ann. Neurol. 1986, 19:598.
-
(1986)
Ann. Neurol.
, vol.19
, pp. 598
-
-
Arogov, Z.1
Bank, W.J.2
Maris, J.3
Eleff, S.4
Kennaway, N.G.5
Olson, R.E.6
Chance, B.7
-
3
-
-
13944278132
-
Mitochondrial, oxidants and aging
-
Balaban R.S., Nemoto S., Finkel T. Mitochondrial, oxidants and aging. Cell 2005, 120:483-495.
-
(2005)
Cell
, vol.120
, pp. 483-495
-
-
Balaban, R.S.1
Nemoto, S.2
Finkel, T.3
-
4
-
-
4744357401
-
Chronic treatment of mitochondrial disease patients with dichloroacetate
-
Barshop B.A., Naviaux R.K., McGowan K.A., Levine F., Nyhan W.L., Loupis-Geller A., Haas R.H. Chronic treatment of mitochondrial disease patients with dichloroacetate. Mol. Genet. Metab. 2004, 83(1-2):138-149.
-
(2004)
Mol. Genet. Metab.
, vol.83
, Issue.1-2
, pp. 138-149
-
-
Barshop, B.A.1
Naviaux, R.K.2
McGowan, K.A.3
Levine, F.4
Nyhan, W.L.5
Loupis-Geller, A.6
Haas, R.H.7
-
5
-
-
0038051345
-
Mitochondria, oxidative damage, and inflammation in Parkinson's disease
-
Beal M.F. Mitochondria, oxidative damage, and inflammation in Parkinson's disease. Ann NY Acad Sci 2003, 991:120-131.
-
(2003)
Ann NY Acad Sci
, vol.991
, pp. 120-131
-
-
Beal, M.F.1
-
6
-
-
33745055953
-
Therapeutic potential of dichloroacetate for pyruvate dehydrogenase complex deficiency
-
Berendzen K., Theriaque D., Shuster J., Stacpoole P.W. Therapeutic potential of dichloroacetate for pyruvate dehydrogenase complex deficiency. Mitochondrion 2006, 6:126-135.
-
(2006)
Mitochondrion
, vol.6
, pp. 126-135
-
-
Berendzen, K.1
Theriaque, D.2
Shuster, J.3
Stacpoole, P.W.4
-
7
-
-
70349563151
-
Peripheral neuropathy in rats exposed to dichloroacetate
-
Calcutt N.A., Lopez V., Batusta A., Mizisin L., Cunha J.M., Shroads A.L., Mizisin A.P., Stacpoole P.W. Peripheral neuropathy in rats exposed to dichloroacetate. J Neuro Sci Exp Neurol 2009, 68:985-993.
-
(2009)
J Neuro Sci Exp Neurol
, vol.68
, pp. 985-993
-
-
Calcutt, N.A.1
Lopez, V.2
Batusta, A.3
Mizisin, L.4
Cunha, J.M.5
Shroads, A.L.6
Mizisin, A.P.7
Stacpoole, P.W.8
-
8
-
-
0037180245
-
Accumulation of mitochondrial DNA mutations in ageing, cancer, and mitochondrial disease: is there a common mechanism?
-
Chinnery P.F., Samuels D.C., Elson J., Turnbull D.M. Accumulation of mitochondrial DNA mutations in ageing, cancer, and mitochondrial disease: is there a common mechanism?. Lancet 2002, 360(9342):1323-1325.
-
(2002)
Lancet
, vol.360
, Issue.9342
, pp. 1323-1325
-
-
Chinnery, P.F.1
Samuels, D.C.2
Elson, J.3
Turnbull, D.M.4
-
9
-
-
0018221514
-
Dichloroacetate as treatment for congenital lactic acidosis
-
Coude F.X., Saudbray J.M., DeMaugre F., Marsac C., Leroux J.P., Charpentier C. Dichloroacetate as treatment for congenital lactic acidosis. N. Engl. J. Med. 1978, 299(24):1365-1366.
-
(1978)
N. Engl. J. Med.
, vol.299
, Issue.24
, pp. 1365-1366
-
-
Coude, F.X.1
Saudbray, J.M.2
DeMaugre, F.3
Marsac, C.4
Leroux, J.P.5
Charpentier, C.6
-
10
-
-
33750223196
-
-
Informa Healthcare, Oxon, United Kingdom
-
DiMauro S., Hirano M., Schon E.A. Mitochondrial Medicine 2006, Informa Healthcare, Oxon, United Kingdom.
-
(2006)
Mitochondrial Medicine
-
-
DiMauro, S.1
Hirano, M.2
Schon, E.A.3
-
11
-
-
1942537035
-
Dichloroacetate therapy attenuates the blood lactate response to submaximal exercise in patients with defects in mitochondrial energy metabolism
-
Duncan G.E., Perkins L.A., Theriaque D.W., Neiberger R.E., Stacpoole P.W. Dichloroacetate therapy attenuates the blood lactate response to submaximal exercise in patients with defects in mitochondrial energy metabolism. J. Clin. Endocrinol. Metab. 2004, 89(4):1733-1738.
-
(2004)
J. Clin. Endocrinol. Metab.
, vol.89
, Issue.4
, pp. 1733-1738
-
-
Duncan, G.E.1
Perkins, L.A.2
Theriaque, D.W.3
Neiberger, R.E.4
Stacpoole, P.W.5
-
12
-
-
67949102053
-
Recent progress in the biology and physiology of sirtuins
-
Finkel T., Deng C.X., Mostoslavsky R. Recent progress in the biology and physiology of sirtuins. Nature 2009, 460(7255):587-591.
-
(2009)
Nature
, vol.460
, Issue.7255
, pp. 587-591
-
-
Finkel, T.1
Deng, C.X.2
Mostoslavsky, R.3
-
13
-
-
0036398010
-
Coenzyme Q10 and idebenone in the therapy of respiratory chain disorders: rationale and comparative benefits
-
Geromel V., Darin N., Chretien D., Bénit P., DeLonlay P., Rötig A., Munnich A., Rustin P. Coenzyme Q10 and idebenone in the therapy of respiratory chain disorders: rationale and comparative benefits. Molecular Genetics and Metabolism 2002, 77:21-30.
-
(2002)
Molecular Genetics and Metabolism
, vol.77
, pp. 21-30
-
-
Geromel, V.1
Darin, N.2
Chretien, D.3
Bénit, P.4
DeLonlay, P.5
Rötig, A.6
Munnich, A.7
Rustin, P.8
-
14
-
-
78149325680
-
A randomized trial of coenzyme Q10 in mitochondrial disorders
-
Glover E.I., Martin J., Maher A., Thornhill R.E., Moran G.R., Tarnopolsky M.A. A randomized trial of coenzyme Q10 in mitochondrial disorders. Muscle Nerve 2010, 42(5):739-748.
-
(2010)
Muscle Nerve
, vol.42
, Issue.5
, pp. 739-748
-
-
Glover, E.I.1
Martin, J.2
Maher, A.3
Thornhill, R.E.4
Moran, G.R.5
Tarnopolsky, M.A.6
-
16
-
-
34248175243
-
The evidence basis for coenzyme Q therapy in oxidative phosphorylation disease
-
Haas R.H. The evidence basis for coenzyme Q therapy in oxidative phosphorylation disease. Mitochondrion 2007, 7S:S136-S145.
-
(2007)
Mitochondrion
, vol.7 S
-
-
Haas, R.H.1
-
17
-
-
0023883150
-
Deletions of muscle mitochondrial DNA in patients with mitochondrial myopathies
-
Holt I.J., Harding A.E., Morgan Huges J.A. Deletions of muscle mitochondrial DNA in patients with mitochondrial myopathies. Nature 1988, 321:717-719.
-
(1988)
Nature
, vol.321
, pp. 717-719
-
-
Holt, I.J.1
Harding, A.E.2
Morgan Huges, J.A.3
-
18
-
-
33646202306
-
Dichloroacetate causes toxic neuropathy in MELAS: a randomized, controlled clinical trial
-
Kaufmann P., Engelstad K., Wei Y., Jhung S., Sano M.C., Shungu D.C., Millar W.S., Hong X., Gooch C.L., Mao X., Pascual J.M., Hirano M., Stacpoole P.W., DiMauro S., Di Vivo D.C. Dichloroacetate causes toxic neuropathy in MELAS: a randomized, controlled clinical trial. Neurology 2006, 66:324-330.
-
(2006)
Neurology
, vol.66
, pp. 324-330
-
-
Kaufmann, P.1
Engelstad, K.2
Wei, Y.3
Jhung, S.4
Sano, M.C.5
Shungu, D.C.6
Millar, W.S.7
Hong, X.8
Gooch, C.L.9
Mao, X.10
Pascual, J.M.11
Hirano, M.12
Stacpoole, P.W.13
DiMauro, S.14
Di Vivo, D.C.15
-
19
-
-
70249116820
-
Phase II trial of CoQ10 for ALS finds insufficient evidence to justify phase III
-
Kaufmann P., Thompson J.L.P., Levy G., Buchsbaum R., Shefner J., Krivickas L.S., Katz J., Rollins Y., Barohn R.J., Jackson C.E., Tiryaki E., Lomen-Hoerth C., Armon C., Tandan R., Rudnicki S.A., Rezania K., Sufit R., Pestronk A., Novella S.P., Heiman-Patterson T., Kasarskis E.J., Pioro E.P., Montes J., Arbing R., Vecchio D., Barsdorf A., Mitsumoto H., Levin B. Phase II trial of CoQ10 for ALS finds insufficient evidence to justify phase III. Ann. Neurol. 2009, 66:235-244.
-
(2009)
Ann. Neurol.
, vol.66
, pp. 235-244
-
-
Kaufmann, P.1
Thompson, J.L.P.2
Levy, G.3
Buchsbaum, R.4
Shefner, J.5
Krivickas, L.S.6
Katz, J.7
Rollins, Y.8
Barohn, R.J.9
Jackson, C.E.10
Tiryaki, E.11
Lomen-Hoerth, C.12
Armon, C.13
Tandan, R.14
Rudnicki, S.A.15
Rezania, K.16
Sufit, R.17
Pestronk, A.18
Novella, S.P.19
Heiman-Patterson, T.20
Kasarskis, E.J.21
Pioro, E.P.22
Montes, J.23
Arbing, R.24
Vecchio, D.25
Barsdorf, A.26
Mitsumoto, H.27
Levin, B.28
more..
-
20
-
-
0029035721
-
Treatment of lactic acidosis: a review
-
Kerr D.S. Treatment of lactic acidosis: a review. Int Pediatr 1995, 10:75-81.
-
(1995)
Int Pediatr
, vol.10
, pp. 75-81
-
-
Kerr, D.S.1
-
21
-
-
0034642154
-
A placebo-controlled crossover trial of creatine in mitochondrial diseases
-
Klopstock T., Querner V., Schmidt F., Gekeler F., Walter M., Hartard M., Henning M., Gasser T., Pongratz D., Straube A., Dieterich M., Müller-Felber W. A placebo-controlled crossover trial of creatine in mitochondrial diseases. Neurology 2000, 55(11):1748-1751.
-
(2000)
Neurology
, vol.55
, Issue.11
, pp. 1748-1751
-
-
Klopstock, T.1
Querner, V.2
Schmidt, F.3
Gekeler, F.4
Walter, M.5
Hartard, M.6
Henning, M.7
Gasser, T.8
Pongratz, D.9
Straube, A.10
Dieterich, M.11
Müller-Felber, W.12
-
22
-
-
20144387513
-
Creatine has no beneficial effect on skeletal muscle energy metabolism in patients with single mitochondrial DNA deletions: a placebo-controlled, double-blind 31P-MRS crossover study
-
Kornblum C., Schröder R., Müller K., Vorgerd M., Eggers J., Bogdanow M., Papassotiropoulos A., Fabian K., Klockgether T., Zange J. Creatine has no beneficial effect on skeletal muscle energy metabolism in patients with single mitochondrial DNA deletions: a placebo-controlled, double-blind 31P-MRS crossover study. Eur. J. Neurol. 2005, 12(4):300-309.
-
(2005)
Eur. J. Neurol.
, vol.12
, Issue.4
, pp. 300-309
-
-
Kornblum, C.1
Schröder, R.2
Müller, K.3
Vorgerd, M.4
Eggers, J.5
Bogdanow, M.6
Papassotiropoulos, A.7
Fabian, K.8
Klockgether, T.9
Zange, J.10
-
23
-
-
79961209470
-
Phase 3 trial of coenzyme
-
Kurtz, TL, for the CoQ10 Trial Investigators, United Mitochondrial Disease Foundation, Indianapolis, IN, June 24-28
-
Phase 3 trial of coenzyme. Q10 in genetic mitochondrial diseases 2008, Kurtz, TL, for the CoQ10 Trial Investigators, United Mitochondrial Disease Foundation, Indianapolis, IN, June 24-28.
-
(2008)
Q10 in genetic mitochondrial diseases
-
-
-
24
-
-
0037426430
-
Cerebellar ataxia and coenzyme Q10 deficiency
-
Lamperti C., Naini A., Hirano M., De Vivo D.C., Bertini E., Servidei S., Valeriani M., Lynch D., Banwell B., Berg M., Dubrovsky T., Chiriboga C., Angelini C., Pegoraro E., DiMauro S. Cerebellar ataxia and coenzyme Q10 deficiency. Neurology 2003, 60:1206-1208.
-
(2003)
Neurology
, vol.60
, pp. 1206-1208
-
-
Lamperti, C.1
Naini, A.2
Hirano, M.3
De Vivo, D.C.4
Bertini, E.5
Servidei, S.6
Valeriani, M.7
Lynch, D.8
Banwell, B.9
Berg, M.10
Dubrovsky, T.11
Chiriboga, C.12
Angelini, C.13
Pegoraro, E.14
DiMauro, S.15
-
25
-
-
33646684516
-
New insights into structure and function of mitochondria and their role in aging and disease
-
Lenaz G., Baracca A., Fato R., Genova M.L., Solaini G. New insights into structure and function of mitochondria and their role in aging and disease. Antioxid. Redox Signal. 2006, 8(3-4):417-437.
-
(2006)
Antioxid. Redox Signal.
, vol.8
, Issue.3-4
, pp. 417-437
-
-
Lenaz, G.1
Baracca, A.2
Fato, R.3
Genova, M.L.4
Solaini, G.5
-
26
-
-
0037241026
-
The effect of short-term dimethylglycine treatment on oxygen consumption in cytochrome oxidase deficiency: a double-blind randomized crossover clinical trial
-
Liet J.M., Pelletier V., Robinson B.H., Laryea M.D., Wendel U., Morneau S., Morin C., Mitchell G., Lacroix J. The effect of short-term dimethylglycine treatment on oxygen consumption in cytochrome oxidase deficiency: a double-blind randomized crossover clinical trial. J. Pediatr. 2003, 142(1):62-66.
-
(2003)
J. Pediatr.
, vol.142
, Issue.1
, pp. 62-66
-
-
Liet, J.M.1
Pelletier, V.2
Robinson, B.H.3
Laryea, M.D.4
Wendel, U.5
Morneau, S.6
Morin, C.7
Mitchell, G.8
Lacroix, J.9
-
27
-
-
77949440226
-
Coenzyme Q10 in neuromuscular and neurodegenerative disorders
-
Mancuso M., Orsucci D., Volpi L., Calsolaro V., Siciliano G. Coenzyme Q10 in neuromuscular and neurodegenerative disorders. Curr. Drug Targets 2010, 11(1):111-121.
-
(2010)
Curr. Drug Targets
, vol.11
, Issue.1
, pp. 111-121
-
-
Mancuso, M.1
Orsucci, D.2
Volpi, L.3
Calsolaro, V.4
Siciliano, G.5
-
28
-
-
0027336477
-
Coenzyme Q10 with multiple vitamins is generally ineffective in treatment of mitochondrial disease
-
Matthews P.M., Ford B., Dandurand R.J., Eidelman D.H., O'Connor D., Sherwin A., Karpati G., Andermann F., Arnold D.L. Coenzyme Q10 with multiple vitamins is generally ineffective in treatment of mitochondrial disease. Neurology 1993, 43:884-890.
-
(1993)
Neurology
, vol.43
, pp. 884-890
-
-
Matthews, P.M.1
Ford, B.2
Dandurand, R.J.3
Eidelman, D.H.4
O'Connor, D.5
Sherwin, A.6
Karpati, G.7
Andermann, F.8
Arnold, D.L.9
-
29
-
-
0035836740
-
Familial cerebellar ataxia with muscle Q10 deficiency
-
Musumeci O., Naini A., Slonim A.E., Skavin N., Hadjigeorgiou G.L., Krawiecki N., Weissman B.M., Tsao C.Y., Mendell J.R., Shanske S., De Vivo D.C., Hirano M., DiMauro S. Familial cerebellar ataxia with muscle Q10 deficiency. Neurology 2001, 56:849-855.
-
(2001)
Neurology
, vol.56
, pp. 849-855
-
-
Musumeci, O.1
Naini, A.2
Slonim, A.E.3
Skavin, N.4
Hadjigeorgiou, G.L.5
Krawiecki, N.6
Weissman, B.M.7
Tsao, C.Y.8
Mendell, J.R.9
Shanske, S.10
De Vivo, D.C.11
Hirano, M.12
DiMauro, S.13
-
30
-
-
0141610413
-
Muscle coenzyme Q deficiency in familial mitochondrial encephalopathy
-
Ogasahara S., Engel A.G., Frens D., Mack D. Muscle coenzyme Q deficiency in familial mitochondrial encephalopathy. Proc Natl Acad Sci USA 1989, 86:2379-2382.
-
(1989)
Proc Natl Acad Sci USA
, vol.86
, pp. 2379-2382
-
-
Ogasahara, S.1
Engel, A.G.2
Frens, D.3
Mack, D.4
-
31
-
-
0029066771
-
The treatment of mitochondrial myopathies and encephalomyopathies
-
Peterson P.L. The treatment of mitochondrial myopathies and encephalomyopathies. Biochim. Biophys. Acta 1995, 1271:275-280.
-
(1995)
Biochim. Biophys. Acta
, vol.1271
, pp. 275-280
-
-
Peterson, P.L.1
-
33
-
-
33847000236
-
Beneficial effects of creatine, CoQ10, and lipoic acid in mitochondrial disorders
-
Rodriguez M.C., MacDonald J.R., Mahoney D.J., Parise G., Beal M.F., Tarnopolsky M.A. Beneficial effects of creatine, CoQ10, and lipoic acid in mitochondrial disorders. Nuscle Nerve 2007, 35(2):235-242.
-
(2007)
Nuscle Nerve
, vol.35
, Issue.2
, pp. 235-242
-
-
Rodriguez, M.C.1
MacDonald, J.R.2
Mahoney, D.J.3
Parise, G.4
Beal, M.F.5
Tarnopolsky, M.A.6
-
34
-
-
33847000236
-
Beneficial effects of creatine, CoQ10 and lipoic acid in mitochondrial disorders
-
Rodriguez M.C., MacDonald J.R., Mahoney D.J., Parise G., Beal M.F., Tarnopolsky M.A. Beneficial effects of creatine, CoQ10 and lipoic acid in mitochondrial disorders. Muscle Nerve 2007, 35:235-242.
-
(2007)
Muscle Nerve
, vol.35
, pp. 235-242
-
-
Rodriguez, M.C.1
MacDonald, J.R.2
Mahoney, D.J.3
Parise, G.4
Beal, M.F.5
Tarnopolsky, M.A.6
-
35
-
-
0027436331
-
Rules of evidence and clinical recommendations for the management of patients
-
Sackett D.L. Rules of evidence and clinical recommendations for the management of patients. Can. J. Cardiol. 1993, 9:487-489.
-
(1993)
Can. J. Cardiol.
, vol.9
, pp. 487-489
-
-
Sackett, D.L.1
-
36
-
-
40849111674
-
Age-dependent metabolism of dichloroacetate in rats: possible relevance to human toxicity
-
Shroads A.L., Guo X., Dixit V., Liu H.-P., James M.O., Stacpoole P.W. Age-dependent metabolism of dichloroacetate in rats: possible relevance to human toxicity. J Pharmacol Exper Ther 2008, 324:1163-1171.
-
(2008)
J Pharmacol Exper Ther
, vol.324
, pp. 1163-1171
-
-
Shroads, A.L.1
Guo, X.2
Dixit, V.3
Liu, H.-P.4
James, M.O.5
Stacpoole, P.W.6
-
37
-
-
79955826967
-
The dichloroacetate dilemma: environmental hazard vs. therapeutic goldmine - both or neither?
-
Stacpoole P.W. The dichloroacetate dilemma: environmental hazard vs. therapeutic goldmine - both or neither?. Environ. Health Perspect. 2011, 119(2):155-158.
-
(2011)
Environ. Health Perspect.
, vol.119
, Issue.2
, pp. 155-158
-
-
Stacpoole, P.W.1
-
38
-
-
40849131523
-
Evaluation of long-term treatment of children with congenital lactic acidosis with dichloroacetate
-
Stacpoole P.W., Gilbert L.R., Neiberger R.E., Carney P.R., Valenstein E., Theriaque D.W., Shuster J.J. Evaluation of long-term treatment of children with congenital lactic acidosis with dichloroacetate. Pediatrics 2008, 121:e1223-e1228.
-
(2008)
Pediatrics
, vol.121
-
-
Stacpoole, P.W.1
Gilbert, L.R.2
Neiberger, R.E.3
Carney, P.R.4
Valenstein, E.5
Theriaque, D.W.6
Shuster, J.J.7
-
39
-
-
33646830260
-
A controlled clinical trial of dichloroacetate for treatment of congenital lactic acidosis in children
-
Stacpoole P.W., Kerr D.S., Barnes C., Bunch S.T., Carney P.R., Fennell E.M., Felitsyn.N.M, Gilmore R.L., Greer M., Henderson G.N., Hutson A.D., Neiberger R.E., O'Brien R.G., Perkins L.A., Quisling R.G., Shroads A.L., Shuster J.J., Silverstein J.H., Theriaque D.W., Valenstein E. A controlled clinical trial of dichloroacetate for treatment of congenital lactic acidosis in children. Pediatrics 2006, 117:1519-1531.
-
(2006)
Pediatrics
, vol.117
, pp. 1519-1531
-
-
Stacpoole, P.W.1
Kerr, D.S.2
Barnes, C.3
Bunch, S.T.4
Carney, P.R.5
Fennell, E.M.6
Felitsyn, N.M.7
Gilmore, R.L.8
Greer, M.9
Henderson, G.N.10
Hutson, A.D.11
Neiberger, R.E.12
O'Brien, R.G.13
Perkins, L.A.14
Quisling, R.G.15
Shroads, A.L.16
Shuster, J.J.17
Silverstein, J.H.18
Theriaque, D.W.19
Valenstein, E.20
more..
-
40
-
-
0031926903
-
Pharmacokinetics, metabolism and toxicology of dichloroacetate
-
Stacpoole P.W., Henderson G.N., Yan Z., Cornett R., James M.O. Pharmacokinetics, metabolism and toxicology of dichloroacetate. Drug Metab. Rev. 1998, 30:499-539.
-
(1998)
Drug Metab. Rev.
, vol.30
, pp. 499-539
-
-
Stacpoole, P.W.1
Henderson, G.N.2
Yan, Z.3
Cornett, R.4
James, M.O.5
-
41
-
-
0031440630
-
Treatment of congenital lactic acidosis with dichloroacetate
-
Stacpoole P.W., Barnes C.L., Hurbanis M.D., Cannon S.L., Kerr D.S. Treatment of congenital lactic acidosis with dichloroacetate. Arch. Dis. Child. 1997, 77:535-541.
-
(1997)
Arch. Dis. Child.
, vol.77
, pp. 535-541
-
-
Stacpoole, P.W.1
Barnes, C.L.2
Hurbanis, M.D.3
Cannon, S.L.4
Kerr, D.S.5
-
42
-
-
0024452528
-
The pharmacology of dichloroacetate
-
Stacpoole P.W. The pharmacology of dichloroacetate. Metabolism 1989, 38:1124-1144.
-
(1989)
Metabolism
, vol.38
, pp. 1124-1144
-
-
Stacpoole, P.W.1
-
43
-
-
49249087500
-
Short-term effects of coenzyme Q10 in progressive supranuclear palsy: a randomized, placebo-controlled trial
-
Stamelou M., Reuss A., Pilatus U., Magerkurth J., Niklowitz P., Eggert K.M., Krisp A., Menke T., Schade-Brittinger C., Oertel W.H., Höglinger G.U. Short-term effects of coenzyme Q10 in progressive supranuclear palsy: a randomized, placebo-controlled trial. Movement Disorders 2008, 23(7):942-949.
-
(2008)
Movement Disorders
, vol.23
, Issue.7
, pp. 942-949
-
-
Stamelou, M.1
Reuss, A.2
Pilatus, U.3
Magerkurth, J.4
Niklowitz, P.5
Eggert, K.M.6
Krisp, A.7
Menke, T.8
Schade-Brittinger, C.9
Oertel, W.H.10
Höglinger, G.U.11
-
44
-
-
0030731246
-
A randomized, controlled trial of creatine monohydrate in patients with mitochondrial cytopathies
-
Tarnopolsky M.A., Roy B.D., MacDonald J.R. A randomized, controlled trial of creatine monohydrate in patients with mitochondrial cytopathies. Muscle Nerve 1997, 20(12):1502-1509.
-
(1997)
Muscle Nerve
, vol.20
, Issue.12
, pp. 1502-1509
-
-
Tarnopolsky, M.A.1
Roy, B.D.2
MacDonald, J.R.3
-
45
-
-
85009226418
-
A randomized, placebo-controlled trial of coenzyme Q10 and remacemide in Huntington's disease
-
The Huntington Study Group
-
The Huntington Study Group A randomized, placebo-controlled trial of coenzyme Q10 and remacemide in Huntington's disease. Neurology 2001, 57:397-404.
-
(2001)
Neurology
, vol.57
, pp. 397-404
-
-
-
46
-
-
77956802394
-
Safety and tolerability of high-dosage coenzyme Q10 in Huntington's disease and healthy subjects
-
The Huntington Study Group
-
The Huntington Study Group Safety and tolerability of high-dosage coenzyme Q10 in Huntington's disease and healthy subjects. Mov. Disord. 2010, 25(12):1924-1928.
-
(2010)
Mov. Disord.
, vol.25
, Issue.12
, pp. 1924-1928
-
-
-
47
-
-
1642287689
-
Metabolism and function of coenzyme Q
-
Turunen M., Olsson Dallner G. Metabolism and function of coenzyme Q. Biochim. Biophys. Acta 2004, 1660:171-199.
-
(2004)
Biochim. Biophys. Acta
, vol.1660
, pp. 171-199
-
-
Turunen, M.1
Olsson, D.G.2
-
48
-
-
0024242545
-
Mitochondrial DNA mutation associated with Leber's hereditary optic neuropathy
-
Wallace D.C., Singh G., Lott M.T., Hodge J.A., Schurr T.G., Lezza A.M., Elsas L.J., Nikoskelainen E.K. Mitochondrial DNA mutation associated with Leber's hereditary optic neuropathy. Science 1988, 242:1427-1430.
-
(1988)
Science
, vol.242
, pp. 1427-1430
-
-
Wallace, D.C.1
Singh, G.2
Lott, M.T.3
Hodge, J.A.4
Schurr, T.G.5
Lezza, A.M.6
Elsas, L.J.7
Nikoskelainen, E.K.8
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