Coenzyme Q10 and idebenone in the therapy of respiratory chain diseases: Rationale and comparative benefits

Molecular Genetics and Metabolism

Volumn 77, Issue 1-2, 2002, Pages 21-30

  Geromel, Vanna ^a   Darin, Niklas ^a   Chrétien, Dominique ^a   Bénit, Paule ^a   DeLonlay, Pascale ^a   Rötig, Agnès ^a   Munnich, Arnold ^a   Rustin, Pierre ^a  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

Antioxidant; Coenzyme Q10; Idebenone; Mitochondria; Therapy; Ubiquinone

Indexed keywords

ANTIOXIDANT; IDEBENONE; UBIDECARENONE; BENZOQUINONE DERIVATIVE; DRUG DERIVATIVE; UBIQUINONE;

ANTIOXIDANT ACTIVITY; ARTICLE; CARDIOMYOPATHY; CELLULAR DISTRIBUTION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DRUG ACTIVITY; DRUG EFFECT; DRUG STRUCTURE; ELECTRON TRANSPORT; ENZYME DEFICIENCY; ENZYME REPLACEMENT; ENZYME SYNTHESIS; FRIEDREICH ATAXIA; HUMAN; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL RESPIRATION; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; RESPIRATORY CHAIN; TISSUE DISTRIBUTION; BIOLOGICAL MODEL; METABOLISM; MITOCHONDRIAL MYOPATHY; MITOCHONDRION; REVIEW;

ANTIOXIDANTS; BENZOQUINONES; ELECTRON TRANSPORT; FRIEDREICH ATAXIA; HUMANS; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MITOCHONDRIAL MYOPATHIES; MODELS, BIOLOGICAL; OXIDATIVE STRESS; UBIQUINONE;

EID: 0036398010     PISSN: 10967192     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1096-7192(02)00145-2     Document Type: Review

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