Early-onset, slow progression of cone photoreceptor dysfunction and degeneration in CNG channel subunit CNGB3 deficiency

Investigative Ophthalmology and Visual Science

Volumn 52, Issue 6, 2011, Pages 3557-3566

  Xu, Jianhua ^a   Morris, Lynsie ^a   Fliesler, Steven J ^b,c,d   Sherry, David M ^a,e,f   Ding, Xi Qin ^a  

^a UNIVERSITY OF OKLAHOMA COLLEGE OF MEDICINE   (United States)

^b VA WESTERN NEW YORK HEALTHCARE SYSTEM   (United States)

^c UNIVERSITY AT BUFFALO   (United States)

^d SUNY EYE INSTITUTE   (United States)

^e Oklahoma Center for Neuroscience   (United States)

^f UNIVERSITY OF OKLAHOMA HEALTH SCIENCES CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CONE OPSIN; CYCLIC NUCLEOTIDE GATED CHANNEL; CYCLIC NUCLEOTIDE GATED CHANNEL B3; LECTIN; RETINA S ANTIGEN; TRANSDUCIN; UNCLASSIFIED DRUG; CNGB3 PROTEIN, MOUSE; OPSIN;

ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; CONFOCAL MICROSCOPY; CONTROLLED STUDY; DISEASE COURSE; ELECTRORETINOGRAPHY; IMMUNOHISTOCHEMISTRY; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; RETINA CONE; RETINA DEGENERATION; RETINA ROD OUTER SEGMENT; TRANSMISSION ELECTRON MICROSCOPY; WESTERN BLOTTING; ANIMAL; C57BL MOUSE; ELECTRON MICROSCOPY; FLUORESCENT ANTIBODY TECHNIQUE; GENETICS; METABOLISM; MOUSE MUTANT; PATHOLOGY; POLYACRYLAMIDE GEL ELECTROPHORESIS; ULTRASTRUCTURE;

ANIMALS; ARRESTIN; BLOTTING, WESTERN; CYCLIC NUCLEOTIDE-GATED CATION CHANNELS; ELECTROPHORESIS, POLYACRYLAMIDE GEL; ELECTRORETINOGRAPHY; FLUORESCENT ANTIBODY TECHNIQUE, INDIRECT; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICROSCOPY, CONFOCAL; MICROSCOPY, ELECTRON; OPSINS; RETINAL CONE PHOTORECEPTOR CELLS; RETINAL DEGENERATION; TRANSDUCIN;

EID: 79960785268     PISSN: 01460404     EISSN: 15525783     Source Type: Journal    
DOI: 10.1167/iovs.10-6358     Document Type: Article

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