Loss of expression of neutrophil proteinase-3: A factor contributing to thrombotic risk in paroxysmal nocturnal hemoglobinuria

Haematologica

Volumn 96, Issue 7, 2011, Pages 954-962

  Jankowska, Anna M ^a   Szpurka, Hadrian ^a   Calabro, Mark ^b   Mohan, Sanjay ^a   Schade, Andrew E ^a,c   Clemente, Michael ^a   Silverstein, Roy L ^a,b   Maciejewski, Jaroslaw P ^a  

^a TAUSSIG CANCER INSTITUTE   (United States)

^b LERNER RESEARCH INSTITUTE   (United States)

^c Division of Pathology   (United States)

Author keywords

CD177; Paroxysmal nocturnal hemoglobinuria; PR3; Thrombosis

Indexed keywords

CELL ANTIGEN; MYELOBLASTIN; NEUTROPHIL ANTIGEN 2A; PROTEINASE ACTIVATED RECEPTOR 1; SERINE PROTEINASE INHIBITOR; THROMBIN; UNCLASSIFIED DRUG;

ARTICLE; CARBOXY TERMINAL SEQUENCE; CLINICAL ARTICLE; CONTROLLED STUDY; CYTOPLASM; ENZYME BLOOD LEVEL; ENZYME LINKED IMMUNOSORBENT ASSAY; FLOW CYTOMETRY; HUMAN; HUMAN CELL; IN VITRO STUDY; LIPID RAFT; PAROXYSMAL NOCTURNAL HEMOGLOBINURIA; PHENOTYPE; PROTEIN EXPRESSION; RISK ASSESSMENT; THROMBOCYTE ACTIVATION; THROMBOCYTE AGGREGATION; THROMBOSIS; WESTERN BLOTTING;

BLOOD PLATELETS; CYTOPLASM; GENE EXPRESSION REGULATION, ENZYMOLOGIC; GPI-LINKED PROTEINS; HEMOGLOBINURIA, PAROXYSMAL; HUMANS; ISOANTIGENS; MEMBRANE MICRODOMAINS; MEMBRANE PROTEINS; MYELOBLASTIN; RECEPTORS, CELL SURFACE; THROMBIN; THROMBOPHILIA;

EID: 79959962456     PISSN: 03906078     EISSN: 15928721     Source Type: Journal    
DOI: 10.3324/haematol.2010.029298     Document Type: Article

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