SerpinB1 in cystic fibrosis airway fluids: Quantity, molecular form and mechanism of elastase inhibition

European Respiratory Journal

Volumn 37, Issue 5, 2011, Pages 1083-1090

  Cooley, J ^a   Sontag, M K ^c   Accurso, F J ^d   Remold O'Donnell, E ^a,b  

^a BOSTON CHILDREN S HOSPITAL   (United States)

^b HARVARD MEDICAL SCHOOL   (United States)

^c Global Health and Health Disparities   (United States)

^d UNIVERSITY OF COLORADO SCHOOL OF MEDICINE   (United States)

Author keywords

Cystic fibrosis; Elastase; Neutrophil serine proteases; Protease inhibitors; Serpin

Indexed keywords

ALPHA 1 ANTITRYPSIN; ELASTASE; SERINE PROTEINASE INHIBITOR; SERPINEB1; UNCLASSIFIED DRUG;

ADOLESCENT; ARTICLE; CHEMICAL STRUCTURE; CHILD; CLINICAL ARTICLE; COMPLEX FORMATION; CONTROLLED STUDY; CYSTIC FIBROSIS; DRUG MECHANISM; ENZYME ACTIVITY; ENZYME BINDING; ENZYME INHIBITION; FRAGMENTATION REACTION; HUMAN; LUNG LAVAGE; MICROENVIRONMENT; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN CLEAVAGE; SCHOOL CHILD; STOICHIOMETRY; SURVIVAL TIME;

ALPHA 1-ANTITRYPSIN; BRONCHOALVEOLAR LAVAGE FLUID; CHILD; CHILD, PRESCHOOL; CROSS-SECTIONAL STUDIES; CYSTIC FIBROSIS; HUMANS; LEUKOCYTE ELASTASE; SERPINS;

EID: 79955656198     PISSN: 09031936     EISSN: 13993003     Source Type: Journal    
DOI: 10.1183/09031936.00073710     Document Type: Article

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