Reconstitution of defective protein trafficking rescues Long-QT syndrome in zebrafish

Biochemical and Biophysical Research Communications

Volumn 408, Issue 2, 2011, Pages 218-224

  Meder, Benjamin ^a   Scholz, Eberhard P ^a   Hassel, David ^b   Wolff, Christoph ^a   Just, Steffen ^a   Berger, Ina M ^a   Patzel, Eva ^a   Karle, Christoph ^a   Katus, Hugo A ^a   Rottbauer, Wolfgang ^a,c  

^a UNIVERSITY HOSPITAL HEIDELBERG   (Germany)

^b GLADSTONE INSTITUTE OF CARDIOVASCULAR DISEASE   (United States)

^c UNIVERSITY OF ULM   (Germany)

Author keywords

Arrhythmia; Genetics; Ion channels; Long QT syndrome; Protein trafficking

Indexed keywords

CISAPRIDE; DIMETHYL SULFOXIDE; POTASSIUM CHANNEL; TRANSCRIPTION FACTOR ERG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL MEMBRANE; CONTROLLED STUDY; ELECTROCARDIOGRAPHY; GENOTYPE; HEART ARRHYTHMIA; HEART REPOLARIZATION; HEART VENTRICLE; LONG QT SYNDROME; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; QT PROLONGATION; ZEBRA FISH;

ANIMALS; DISEASE MODELS, ANIMAL; ETHER-A-GO-GO POTASSIUM CHANNELS; HEART RATE; HEK293 CELLS; HUMANS; LONG QT SYNDROME; MUTATION; PROTEIN TRANSPORT; VENTRICULAR DYSFUNCTION; ZEBRAFISH; ZEBRAFISH PROTEINS;

DANIO RERIO;

EID: 79955644302     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2011.03.121     Document Type: Article

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