Basal bioenergetic abnormalities in skeletal muscle from ryanodine receptor malignant hyperthermia-susceptible R163C knock-in mice

Journal of Biological Chemistry

Volumn 286, Issue 1, 2011, Pages 99-113

  Giulivi, Cecilia ^a   Ross Inta, Catherine ^a   Omanska Klusek, Alicja ^a   Napoli, Eleonora ^a   Sakaguchi, Danielle ^a   Barrientos, Genaro ^a   Allen, Paul D ^b   Pessah, Isaac N ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b BRIGHAM AND WOMEN S HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CALCINEURIN; CENTRAL CORE DISEASE; COPY NUMBER; HEAT STRESS; INSULIN RESISTANCE; MALIGNANT HYPERTHERMIAS; MATRIX; METABOLIC ACIDOSIS; METABOLIC ADAPTATION; MITOCHONDRIAL DYSFUNCTION; MITOCHONDRIAL PROTEIN; OXIDATIVE PHOSPHORYLATION; REACTIVE OXYGEN SPECIES; RYANODINE RECEPTORS; SIGNALING PATHWAYS; SKELETAL MUSCLE; TRANSCRIPT LEVEL; WILD TYPES;

CALCIUM; DRUG PRODUCTS; ENZYME INHIBITION; GLUCOSE; INSECTICIDES; METABOLISM; MITOCHONDRIA; OXYGEN; PHOSPHORYLATION;

MUSCLE;

CALCINEURIN; CITRATE SYNTHASE; GLYCERALDEHYDE 3 PHOSPHATE DEHYDROGENASE; GLYCOGEN; MITOCHONDRIAL PROTEIN; MYOGLOBIN; MYOSIN HEAVY CHAIN; MYOSIN HEAVY CHAIN 4; RYANODINE RECEPTOR 1; UNCLASSIFIED DRUG;

ADAPTATION; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BIOENERGY; CALCIUM CELL LEVEL; CONTROLLED STUDY; ENZYME ACTIVITY; GENE DOSAGE; GENE MUTATION; GENETIC SUSCEPTIBILITY; GENETIC TRANSCRIPTION; GLUCOSE UTILIZATION; GLYCOLYSIS; INSULIN RESISTANCE; MALIGNANT HYPERTHERMIA; MOUSE; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PHENOTYPE; PRIORITY JOURNAL; PROTEIN CONTENT; PROTEIN EXPRESSION; SIGNAL TRANSDUCTION; SKELETAL MUSCLE;

ANIMALS; BASAL METABOLISM; CALCINEURIN; CALCIUM; DIAPHRAGM; FEMALE; GENE EXPRESSION REGULATION; GENE KNOCK-IN TECHNIQUES; GENETIC PREDISPOSITION TO DISEASE; HUMANS; KINETICS; MALIGNANT HYPERTHERMIA; MICE; MITOCHONDRIA; MUSCLE, SKELETAL; MUTATION; OXIDATIVE STRESS; OXYGEN; PERMEABILITY; RATS; RYANODINE RECEPTOR CALCIUM RELEASE CHANNEL; SIGNAL TRANSDUCTION;

MUS;

EID: 78650961290     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M110.153247     Document Type: Article

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