Trafficking and Transporter Disorders in Pediatric Cholestasis

Clinics in Liver Disease

Volumn 14, Issue 4, 2010, Pages 619-633

  Knisely, A S ^a   Gissen, Paul ^b,c  

^a KING S COLLEGE HOSPITAL   (United Kingdom)

^b UNIVERSITY OF BIRMINGHAM   (United Kingdom)

^c BIRMINGHAM CHILDREN S HOSPITAL   (United Kingdom)

Author keywords

Bile salt export pump; Cell polarity; Genetic diagnosis; Multidrug resistance protein; Pediatric cholestasis

Indexed keywords

ABC TRANSPORTER; ABCB11 PROTEIN; ABCB2 PROTEIN; ABCB4 PROTEIN; BILE ACID; BILE SALT; CHENODEOXYCHOLIC ACID; CHOLIC ACID; DEOXYCHOLIC ACID; FARNESOID X RECEPTOR; GAMMA GLUTAMYLTRANSFERASE; LITHOCHOLIC ACID; MULTIDRUG RESISTANCE PROTEIN 2; MULTIDRUG RESISTANCE PROTEIN 3; UNCLASSIFIED DRUG;

AMINO ACID SEQUENCE; ANEMIA; BILE ACID SYNTHESIS; CHILDHOOD DISEASE; CHOLESTASIS; DISEASE MODEL; DUBIN JOHNSON SYNDROME; EXTRAHEPATIC BILE DUCT OBSTRUCTION; FAMILIAL DISEASE; GAMMA GLUTAMYL TRANSFERASE BLOOD LEVEL; GENE MUTATION; GENE SEQUENCE; GENETIC PREDISPOSITION; GENETIC VARIABILITY; HUMAN; HYPERCHOLANEMIA; IMMUNOHISTOCHEMISTRY; INTRAHEPATIC CHOLESTASIS; NONHUMAN; OBSTRUCTIVE JAUNDICE; PROTEIN FUNCTION; PROTEIN TRANSPORT; REVIEW; SODIUM RETENTION;

ANIMALS; ATP-BINDING CASSETTE TRANSPORTERS; BILE CANALICULI; CHILD; CHOLESTASIS; HUMANS; P-GLYCOPROTEINS;

EID: 78049472274     PISSN: 10893261     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.cld.2010.08.001     Document Type: Review

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