Axonal pathology precedes demyelination in a mouse model of X-linked demyelinating/type i Charcot-Marie Tooth neuropathy

Journal of Neuropathology and Experimental Neurology

Volumn 69, Issue 9, 2010, Pages 945-958

  Vavlitou, Natalie ^a   Sargiannidou, Irene ^a   Markoullis, Kyriaki ^a   Kyriacou, Kyriacos ^a   Scherer, Steven S ^b   Kleopa, Kleopas A ^a  

^a CYPRUS INSTITUTE OF NEUROLOGY AND GENETICS   (Cyprus)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

Axonal degeneration; Axonal transport; Charcot Marie Tooth; Connexin32; Cx32; Gap junctions; Neurofilaments

Indexed keywords

CONNEXIN 32; GAP JUNCTION PROTEIN; AMYLOID PRECURSOR PROTEIN; CNTNAP1 PROTEIN, MOUSE; NERVE CELL ADHESION MOLECULE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DEMYELINATING DISEASE; DEMYELINATION; DEPHOSPHORYLATION; GAP JUNCTION; IMMUNOHISTOCHEMISTRY; MOUSE; NERVE FIBER TRANSPORT; NEUROFILAMENT; NEUROPATHOLOGY; NONHUMAN; PERIPHERAL NEUROPATHY; PRIORITY JOURNAL; TRANSGENIC MOUSE; TYPE I CHARCOT MARIE TOOTH NEUROPATHY; X CHROMOSOME LINKED DISORDER; ANIMAL; DISEASE MODEL; GENETICS; HEREDITARY MOTOR SENSORY NEUROPATHY; KNOCKOUT MOUSE; METABOLISM; NERVE DEGENERATION; NERVE FIBER; PATHOLOGY; PATHOPHYSIOLOGY; ULTRASTRUCTURE;

AMYLOID BETA-PROTEIN PRECURSOR; ANIMALS; AXONS; CELL ADHESION MOLECULES, NEURONAL; CHARCOT-MARIE-TOOTH DISEASE; CONNEXINS; DEMYELINATING DISEASES; DISEASE MODELS, ANIMAL; MICE; MICE, KNOCKOUT; NERVE DEGENERATION;

EID: 77957287735     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1097/NEN.0b013e3181efa658     Document Type: Article

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