-
1
-
-
0027319326
-
Mice devoid of PrP are resistant to scrapie
-
Bueler H., Aguzzi A., Sailer A., Greiner R.A., Autenried P., Aguet M., and Weissmann C. Mice devoid of PrP are resistant to scrapie. Cell 73 (1993) 1339-1347
-
(1993)
Cell
, vol.73
, pp. 1339-1347
-
-
Bueler, H.1
Aguzzi, A.2
Sailer, A.3
Greiner, R.A.4
Autenried, P.5
Aguet, M.6
Weissmann, C.7
-
2
-
-
0029825830
-
Normal host prion protein (PrPC) is required for scrapie spread within the central nervous system
-
Brandner S., Raeber A., Sailer A., Blattler T., Fischer M., Weissmann C., and Aguzzi A. Normal host prion protein (PrPC) is required for scrapie spread within the central nervous system. Proc. Natl. Acad. Sci. USA 93 (1996) 13148-13151
-
(1996)
Proc. Natl. Acad. Sci. USA
, vol.93
, pp. 13148-13151
-
-
Brandner, S.1
Raeber, A.2
Sailer, A.3
Blattler, T.4
Fischer, M.5
Weissmann, C.6
Aguzzi, A.7
-
3
-
-
0020321767
-
Novel proteinaceous infectious particles cause scrapie
-
Prusiner S.B. Novel proteinaceous infectious particles cause scrapie. Science 216 (1982) 136-144
-
(1982)
Science
, vol.216
, pp. 136-144
-
-
Prusiner, S.B.1
-
4
-
-
0026567814
-
Nearly ubiquitous tissue distribution of the scrapie agent precursor protein
-
Bendheim P.E., Brown H.R., Rudelli R.D., Scala L.J., Goller N.L., Wen G.Y., Kascsak R.J., Cashman N.R., and Bolton D.C. Nearly ubiquitous tissue distribution of the scrapie agent precursor protein. Neurology 42 (1992) 149-156
-
(1992)
Neurology
, vol.42
, pp. 149-156
-
-
Bendheim, P.E.1
Brown, H.R.2
Rudelli, R.D.3
Scala, L.J.4
Goller, N.L.5
Wen, G.Y.6
Kascsak, R.J.7
Cashman, N.R.8
Bolton, D.C.9
-
5
-
-
42049099020
-
Physiology of the prion protein
-
Linden R., Martins V.R., Prado M.A., Cammarota M., Izquierdo I., and Brentani R.R. Physiology of the prion protein. Physiol. Rev. 88 (2008) 673-728
-
(2008)
Physiol. Rev.
, vol.88
, pp. 673-728
-
-
Linden, R.1
Martins, V.R.2
Prado, M.A.3
Cammarota, M.4
Izquierdo, I.5
Brentani, R.R.6
-
6
-
-
0026637514
-
The prion protein gene: a role in mouse embryogenesis?
-
Manson J., West J.D., Thomson V., McBride P., Kaufman M.H., and Hope J. The prion protein gene: a role in mouse embryogenesis?. Development 115 (1992) 117-122
-
(1992)
Development
, vol.115
, pp. 117-122
-
-
Manson, J.1
West, J.D.2
Thomson, V.3
McBride, P.4
Kaufman, M.H.5
Hope, J.6
-
7
-
-
0037242707
-
Embryonic activation and developmental expression of the murine prion protein gene
-
Miele G., Alejo Blanco A.R., Baybutt H., Horvat S., Manson J., and Clinton M. Embryonic activation and developmental expression of the murine prion protein gene. Gene Expr. 11 (2003) 1-12
-
(2003)
Gene Expr.
, vol.11
, pp. 1-12
-
-
Miele, G.1
Alejo Blanco, A.R.2
Baybutt, H.3
Horvat, S.4
Manson, J.5
Clinton, M.6
-
8
-
-
33847295624
-
Developmental expression of PrP in the post-implantation embryo
-
Tremblay P., Bouzamondo-Bernstein E., Heinrich C., Prusiner S.B., and DeArmond S.J. Developmental expression of PrP in the post-implantation embryo. Brain Res. 1139 (2007) 60-67
-
(2007)
Brain Res.
, vol.1139
, pp. 60-67
-
-
Tremblay, P.1
Bouzamondo-Bernstein, E.2
Heinrich, C.3
Prusiner, S.B.4
DeArmond, S.J.5
-
9
-
-
0026600865
-
Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein
-
Bueler H., Fischer M., Lang Y., Bluethmann H., Lipp H.P., DeArmond S.J., Prusiner S.B., Aguet M., and Weissmann C. Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein. Nature 356 (1992) 577-582
-
(1992)
Nature
, vol.356
, pp. 577-582
-
-
Bueler, H.1
Fischer, M.2
Lang, Y.3
Bluethmann, H.4
Lipp, H.P.5
DeArmond, S.J.6
Prusiner, S.B.7
Aguet, M.8
Weissmann, C.9
-
10
-
-
0028420937
-
129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal
-
Manson J.C., Clarke A.R., Hooper M.L., Aitchison L., McConnell I., and Hope J. 129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal. Mol. Neurobiol. 8 (1994) 121-127
-
(1994)
Mol. Neurobiol.
, vol.8
, pp. 121-127
-
-
Manson, J.C.1
Clarke, A.R.2
Hooper, M.L.3
Aitchison, L.4
McConnell, I.5
Hope, J.6
-
11
-
-
0027997387
-
Prion protein is necessary for normal synaptic function
-
Collinge J., Whittington M.A., Sidle K.C.L., Smith C.J., Palmer M.S., Clarke A.R., and Jefferys J.G.R. Prion protein is necessary for normal synaptic function. Nature 370 (1994) 295-297
-
(1994)
Nature
, vol.370
, pp. 295-297
-
-
Collinge, J.1
Whittington, M.A.2
Sidle, K.C.L.3
Smith, C.J.4
Palmer, M.S.5
Clarke, A.R.6
Jefferys, J.G.R.7
-
12
-
-
0029265461
-
PrP gene dosage and long term potentiation
-
Manson J.C., Hope J., Clarke A.R., Johnston A., Black C., and Macleod N. PrP gene dosage and long term potentiation. Neurodegeneration 4 (1995) 113-114
-
(1995)
Neurodegeneration
, vol.4
, pp. 113-114
-
-
Manson, J.C.1
Hope, J.2
Clarke, A.R.3
Johnston, A.4
Black, C.5
Macleod, N.6
-
14
-
-
0036470471
-
Post-natal knockout of prion protein alters hippocampal CA1 properties, but does not result in neurodegeneration
-
Mallucci G.R., Ratte S., Asante E.A., Linehan J., Gowland I., Jefferys J.G., and Collinge J. Post-natal knockout of prion protein alters hippocampal CA1 properties, but does not result in neurodegeneration. EMBO J. 21 (2002) 202-210
-
(2002)
EMBO J.
, vol.21
, pp. 202-210
-
-
Mallucci, G.R.1
Ratte, S.2
Asante, E.A.3
Linehan, J.4
Gowland, I.5
Jefferys, J.G.6
Collinge, J.7
-
15
-
-
33846172709
-
Production of cattle lacking prion protein
-
Richt J.A., Kasinathan P., Hamir A.N., Castilla J., Sathiyaseelan T., Vargas F., Sathiyaseelan J., Wu H., Matsushita H., Koster J., Kato S., Ishida I., Soto C., Robl J.M., and Kuroiwa Y. Production of cattle lacking prion protein. Nat. Biotechnol. 25 (2007) 132-138
-
(2007)
Nat. Biotechnol.
, vol.25
, pp. 132-138
-
-
Richt, J.A.1
Kasinathan, P.2
Hamir, A.N.3
Castilla, J.4
Sathiyaseelan, T.5
Vargas, F.6
Sathiyaseelan, J.7
Wu, H.8
Matsushita, H.9
Koster, J.10
Kato, S.11
Ishida, I.12
Soto, C.13
Robl, J.M.14
Kuroiwa, Y.15
-
16
-
-
58449100797
-
Generation of goats lacking prion protein
-
Yu G., Chen J., Xu Y., Zhu C., Yu H., Liu S., Sha H., Chen J., Xu X., Wu Y., Zhang A., Ma J., and Cheng G. Generation of goats lacking prion protein. Mol. Reprod. Dev. 76 (2009) 3
-
(2009)
Mol. Reprod. Dev.
, vol.76
, pp. 3
-
-
Yu, G.1
Chen, J.2
Xu, Y.3
Zhu, C.4
Yu, H.5
Liu, S.6
Sha, H.7
Chen, J.8
Xu, X.9
Wu, Y.10
Zhang, A.11
Ma, J.12
Cheng, G.13
-
17
-
-
0001552281
-
Expression of amino-terminally truncated PrP in the mouse leading to ataxia and specific cerebellar lesions
-
Shmerling D., Hegyi I., Fischer M., Blattler T., Brandner S., Gotz J., Rulicke T., Flechsig E., Cozzio A., von Mering C., Hangartner C., Aguzzi A., and Weissmann C. Expression of amino-terminally truncated PrP in the mouse leading to ataxia and specific cerebellar lesions. Cell 93 (1998) 203-214
-
(1998)
Cell
, vol.93
, pp. 203-214
-
-
Shmerling, D.1
Hegyi, I.2
Fischer, M.3
Blattler, T.4
Brandner, S.5
Gotz, J.6
Rulicke, T.7
Flechsig, E.8
Cozzio, A.9
von Mering, C.10
Hangartner, C.11
Aguzzi, A.12
Weissmann, C.13
-
18
-
-
33846498655
-
Lethal recessive myelin toxicity of prion protein lacking its central domain
-
Baumann F., Tolnay M., Brabeck C., Pahnke J., Kloz U., Niemann H.H., Heikenwalder M., Rulicke T., Burkle A., and Aguzzi A. Lethal recessive myelin toxicity of prion protein lacking its central domain. EMBO J. 26 (2007) 538-547
-
(2007)
EMBO J.
, vol.26
, pp. 538-547
-
-
Baumann, F.1
Tolnay, M.2
Brabeck, C.3
Pahnke, J.4
Kloz, U.5
Niemann, H.H.6
Heikenwalder, M.7
Rulicke, T.8
Burkle, A.9
Aguzzi, A.10
-
19
-
-
33846543360
-
Neonatal lethality in transgenic mice expressing prion protein with a deletion of residues 105-125
-
Li A., Christensen H.M., Stewart L.R., Roth K.A., Chiesa R., and Harris D.A. Neonatal lethality in transgenic mice expressing prion protein with a deletion of residues 105-125. EMBO J. 26 (2007) 548-558
-
(2007)
EMBO J.
, vol.26
, pp. 548-558
-
-
Li, A.1
Christensen, H.M.2
Stewart, L.R.3
Roth, K.A.4
Chiesa, R.5
Harris, D.A.6
-
20
-
-
8444247483
-
Evolution of vertebrate genes related to prion and Shadoo proteins-clues from comparative genomic analysis
-
Premzl M., Gready J.E., Jermiin L.S., Simonic T., and Marshall Graves J.A. Evolution of vertebrate genes related to prion and Shadoo proteins-clues from comparative genomic analysis. Mol. Biol. Evol. 21 (2004) 2210-2231
-
(2004)
Mol. Biol. Evol.
, vol.21
, pp. 2210-2231
-
-
Premzl, M.1
Gready, J.E.2
Jermiin, L.S.3
Simonic, T.4
Marshall Graves, J.A.5
-
21
-
-
0141760321
-
Shadoo, a new protein highly conserved from fish to mammals and with similarity to prion protein
-
Premzl M., Sangiorgio L., Strumbo B., Marshall Graves J.A., Simonic T., and Gready J.E. Shadoo, a new protein highly conserved from fish to mammals and with similarity to prion protein. Gene 314 (2003) 89-102
-
(2003)
Gene
, vol.314
, pp. 89-102
-
-
Premzl, M.1
Sangiorgio, L.2
Strumbo, B.3
Marshall Graves, J.A.4
Simonic, T.5
Gready, J.E.6
-
22
-
-
33751075179
-
Cloning of the bovine prion-like Shadoo (SPRN) gene by comparative analysis of the predicted genomic locus
-
Uboldi C., Paulis M., Guidi E., Bertoni A., Meo G.P., Perucatti A., Iannuzzi L., Raimondi E., Brunner R.M., Eggen A., and Ferretti L. Cloning of the bovine prion-like Shadoo (SPRN) gene by comparative analysis of the predicted genomic locus. Mamm. Genome 17 (2006) 1130-1139
-
(2006)
Mamm. Genome
, vol.17
, pp. 1130-1139
-
-
Uboldi, C.1
Paulis, M.2
Guidi, E.3
Bertoni, A.4
Meo, G.P.5
Perucatti, A.6
Iannuzzi, L.7
Raimondi, E.8
Brunner, R.M.9
Eggen, A.10
Ferretti, L.11
-
23
-
-
34347272316
-
Characterization of the genomic region containing the Shadow of Prion Protein (SPRN) gene in sheep
-
Lampo E., Van Poucke M., Hugot K., Hayes H., Van Zeveren A., and Peelman L.J. Characterization of the genomic region containing the Shadow of Prion Protein (SPRN) gene in sheep. BMC Genom. 8 (2007) 138
-
(2007)
BMC Genom.
, vol.8
, pp. 138
-
-
Lampo, E.1
Van Poucke, M.2
Hugot, K.3
Hayes, H.4
Van Zeveren, A.5
Peelman, L.J.6
-
24
-
-
34548384916
-
The CNS glycoprotein Shadoo has PrP(C)-like protective properties and displays reduced levels in prion infections
-
Watts J.C., Drisaldi B., Ng V., Yang J., Strome B., Horne P., Sy M.S., Yoong L., Young R., Mastrangelo P., Bergeron C., Fraser P.E., Carlson G.A., Mount H.T., Schmitt-Ulms G., and Westaway D. The CNS glycoprotein Shadoo has PrP(C)-like protective properties and displays reduced levels in prion infections. EMBO J. 26 (2007) 4038-4050
-
(2007)
EMBO J.
, vol.26
, pp. 4038-4050
-
-
Watts, J.C.1
Drisaldi, B.2
Ng, V.3
Yang, J.4
Strome, B.5
Horne, P.6
Sy, M.S.7
Yoong, L.8
Young, R.9
Mastrangelo, P.10
Bergeron, C.11
Fraser, P.E.12
Carlson, G.A.13
Mount, H.T.14
Schmitt-Ulms, G.15
Westaway, D.16
-
25
-
-
59049096630
-
Positive correlation between relative mRNA expression of PRNP and SPRN in cerebral and cerebellar cortex of sheep
-
Lampo E., Van Poucke M., Vandesompele J., Erkens T., Van Zeveren A., and Peelman L.J. Positive correlation between relative mRNA expression of PRNP and SPRN in cerebral and cerebellar cortex of sheep. Mol. Cell. Probe 23 (2009) 60-64
-
(2009)
Mol. Cell. Probe
, vol.23
, pp. 60-64
-
-
Lampo, E.1
Van Poucke, M.2
Vandesompele, J.3
Erkens, T.4
Van Zeveren, A.5
Peelman, L.J.6
-
26
-
-
57349086072
-
Association of a null allele of SPRN with variant Creutzfeldt-Jakob disease
-
Beck J.A., Campbell T.A., Adamson G., Poulter M., Uphill J.B., Molou E., Collinge J., and Mead S. Association of a null allele of SPRN with variant Creutzfeldt-Jakob disease. J. Med. Genet. 45 (2008) 813-817
-
(2008)
J. Med. Genet.
, vol.45
, pp. 813-817
-
-
Beck, J.A.1
Campbell, T.A.2
Adamson, G.3
Poulter, M.4
Uphill, J.B.5
Molou, E.6
Collinge, J.7
Mead, S.8
-
27
-
-
34249937435
-
The prion protein family: diversity, rivalry, and dysfunction
-
Watts J.C., and Westaway D. The prion protein family: diversity, rivalry, and dysfunction. Biochim. Biophys. Acta 1772 (2007) 654-672
-
(2007)
Biochim. Biophys. Acta
, vol.1772
, pp. 654-672
-
-
Watts, J.C.1
Westaway, D.2
-
28
-
-
0036468677
-
Germline transmission and tissue-specific expression of transgenes delivered by lentiviral vectors
-
Lois C., Hong E.J., Pease S., Brown E.J., and Baltimore D. Germline transmission and tissue-specific expression of transgenes delivered by lentiviral vectors. Science 295 (2002) 868-872
-
(2002)
Science
, vol.295
, pp. 868-872
-
-
Lois, C.1
Hong, E.J.2
Pease, S.3
Brown, E.J.4
Baltimore, D.5
-
29
-
-
33644850940
-
Prion infection of mouse neurospheres
-
Giri R.K., Young R., Pitstick R., DeArmond S.J., Prusiner S.B., and Carlson G.A. Prion infection of mouse neurospheres. Proc. Natl. Acad. Sci. USA 103 (2006) 3875-3880
-
(2006)
Proc. Natl. Acad. Sci. USA
, vol.103
, pp. 3875-3880
-
-
Giri, R.K.1
Young, R.2
Pitstick, R.3
DeArmond, S.J.4
Prusiner, S.B.5
Carlson, G.A.6
-
30
-
-
2942750361
-
Foxl2 disruption causes mouse ovarian failure by pervasive blockage of follicle development
-
Uda M., Ottolenghi C., Crisponi L., Garcia J.E., Deiana M., Kimber W., Forabosco A., Cao A., Schlessinger D., and Pilia G. Foxl2 disruption causes mouse ovarian failure by pervasive blockage of follicle development. Hum. Mol. Genet. 13 (2004) 1171-1181
-
(2004)
Hum. Mol. Genet.
, vol.13
, pp. 1171-1181
-
-
Uda, M.1
Ottolenghi, C.2
Crisponi, L.3
Garcia, J.E.4
Deiana, M.5
Kimber, W.6
Forabosco, A.7
Cao, A.8
Schlessinger, D.9
Pilia, G.10
-
31
-
-
22144499640
-
Long-term persistence of a nonintegrated lentiviral vector in mouse hematopoietic stem cells
-
Terskikh A.V., Ershler M.A., Drize N.J., Nifontova I.N., and Chertkov J.L. Long-term persistence of a nonintegrated lentiviral vector in mouse hematopoietic stem cells. Exp. Hematol. 33 (2005) 873-882
-
(2005)
Exp. Hematol.
, vol.33
, pp. 873-882
-
-
Terskikh, A.V.1
Ershler, M.A.2
Drize, N.J.3
Nifontova, I.N.4
Chertkov, J.L.5
-
32
-
-
0141632798
-
Early transcription from nonintegrated DNA in human immunodeficiency virus infection
-
Wu Y., and Marsh J.W. Early transcription from nonintegrated DNA in human immunodeficiency virus infection. J. Virol. 77 (2003) 10376-10382
-
(2003)
J. Virol.
, vol.77
, pp. 10376-10382
-
-
Wu, Y.1
Marsh, J.W.2
-
33
-
-
33845187432
-
Lentiviral vectors with a defective integrase allow efficient and sustained transgene expression in vitro and in vivo
-
Philippe S., Sarkis C., Barkats M., Mammeri H., Ladroue C., Petit C., Mallet J., and Serguera C. Lentiviral vectors with a defective integrase allow efficient and sustained transgene expression in vitro and in vivo. Proc. Natl. Acad. Sci. USA 103 (2006) 17684-17689
-
(2006)
Proc. Natl. Acad. Sci. USA
, vol.103
, pp. 17684-17689
-
-
Philippe, S.1
Sarkis, C.2
Barkats, M.3
Mammeri, H.4
Ladroue, C.5
Petit, C.6
Mallet, J.7
Serguera, C.8
-
34
-
-
34247146896
-
Stable gene expression occurs from a minority of integrated HIV-1-based vectors: transcriptional silencing is present in the majority
-
Mok H.P., Javed S., and Lever A. Stable gene expression occurs from a minority of integrated HIV-1-based vectors: transcriptional silencing is present in the majority. Gene Ther. 14 (2007) 741-751
-
(2007)
Gene Ther.
, vol.14
, pp. 741-751
-
-
Mok, H.P.1
Javed, S.2
Lever, A.3
-
35
-
-
28444460247
-
Neurulation in the cranial region-normal and abnormal
-
Copp A.J. Neurulation in the cranial region-normal and abnormal. J. Anat. 207 (2005) 623-635
-
(2005)
J. Anat.
, vol.207
, pp. 623-635
-
-
Copp, A.J.1
-
36
-
-
33644766915
-
Prion protein (PrPc) positively regulates neural precursor proliferation during developmental and adult mammalian neurogenesis
-
Steele A.D., Emsley J.G., Ozdinler P.H., Lindquist S., and Macklis J.D. Prion protein (PrPc) positively regulates neural precursor proliferation during developmental and adult mammalian neurogenesis. Proc. Natl. Acad. Sci. USA 103 (2006) 3416-3421
-
(2006)
Proc. Natl. Acad. Sci. USA
, vol.103
, pp. 3416-3421
-
-
Steele, A.D.1
Emsley, J.G.2
Ozdinler, P.H.3
Lindquist, S.4
Macklis, J.D.5
-
37
-
-
65949115708
-
Regulation of embryonic cell adhesion by the prion protein
-
Malaga-Trillo E., Solis G.P., Schrock Y., Geiss C., Luncz L., Thomanetz V., and Stuermer C.A. Regulation of embryonic cell adhesion by the prion protein. PLoS Biol. 7 (2009) e55
-
(2009)
PLoS Biol.
, vol.7
-
-
Malaga-Trillo, E.1
Solis, G.P.2
Schrock, Y.3
Geiss, C.4
Luncz, L.5
Thomanetz, V.6
Stuermer, C.A.7
|