Immortalization of murine muscle cells from lysosomal α-glucosidase deficient mice: A new tool to study pathophysiology and assess therapeutic strategies for Pompe disease

Biochemical and Biophysical Research Communications

Volumn 388, Issue 2, 2009, Pages 333-338

  Douillard Guilloux, Gaëlle ^a,b   Mouly, Vincent ^c   Caillaud, Catherine ^a,b   Richard, Emmanuel ^a,b  

^a INSTITUT COCHIN   (France)

^b INSERM   (France)

^c SORBONNE UNIVERSITÉ   (France)

Author keywords

Glucosidase; CDK4; Glycogen storage disease type II; Myoblast immortalization; Pompe disease

Indexed keywords

CYCLIN DEPENDENT KINASE 4; GLUCAN 1,4 ALPHA GLUCOSIDASE; LENTIVIRUS VECTOR;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL IMMORTALIZATION; CELL ISOLATION; GENETIC DISORDER; GENETIC TRANSFECTION; GLYCOGEN STORAGE DISEASE TYPE 2; MOUSE; MUSCLE CELL; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; SATELLITE CELL; TIBIALIS ANTERIOR MUSCLE;

ALPHA-GLUCOSIDASES; ANIMALS; CELL LINE; DISEASE MODELS, ANIMAL; GLYCOGEN STORAGE DISEASE TYPE II; LYSOSOMES; MICE; MICE, KNOCKOUT; MUSCLE DEVELOPMENT; MYOBLASTS;

MURINAE; MUS;

EID: 69249217677     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2009.08.006     Document Type: Article

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