메뉴 건너뛰기




Volumn 40, Issue 4, 2009, Pages 385-387

Search and rescue finding ways to correct ΔF508 CFTR

Author keywords

[No Author keywords available]

Indexed keywords

4 PHENYLBUTYRIC ACID; CHAPERONE; CURCUMIN; MUTANT PROTEIN; NITRIC OXIDE DONOR; SALMETEROL; THAPSIGARGIN; TRANSMEMBRANE CONDUCTANCE REGULATOR; BETA 2 ADRENERGIC RECEPTOR; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR DELTA F508; DRUG DERIVATIVE; SALBUTAMOL;

EID: 63349109752     PISSN: 10441549     EISSN: None     Source Type: Journal    
DOI: 10.1165/rcmb.2008-0006ED     Document Type: Editorial
Times cited : (11)

References (35)
  • 1
    • 46749117136 scopus 로고    scopus 로고
    • Molecular and cellular aspects of protein misfolding and disease
    • Herczenik E, Gebbink MF. Molecular and cellular aspects of protein misfolding and disease. FASEB J 2008;22:2115-2133.
    • (2008) FASEB J , vol.22 , pp. 2115-2133
    • Herczenik, E.1    Gebbink, M.F.2
  • 3
    • 46149097167 scopus 로고    scopus 로고
    • What's new in cystic fibrosis? From treating symptoms to correction of the basic defect
    • Proesmans M, Vermeulen F, De Boeck K. What's new in cystic fibrosis? From treating symptoms to correction of the basic defect. Eur J Pediatr 2008;167:839-849.
    • (2008) Eur J Pediatr , vol.167 , pp. 839-849
    • Proesmans, M.1    Vermeulen, F.2    De Boeck, K.3
  • 4
    • 0026781952 scopus 로고
    • Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive
    • Denning GM, Anderson MP, Amara JF, Marshall J, Smith AE, Welsh MJ. Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive. Nature 1992;358:761-764.
    • (1992) Nature , vol.358 , pp. 761-764
    • Denning, G.M.1    Anderson, M.P.2    Amara, J.F.3    Marshall, J.4    Smith, A.E.5    Welsh, M.J.6
  • 6
    • 0030042386 scopus 로고    scopus 로고
    • Glycerol reverses the misfolding phenotype of the most common cystic fibrosis mutation
    • Sato S, Ward CL, Krouse ME, Wine JJ, Kopito RR. Glycerol reverses the misfolding phenotype of the most common cystic fibrosis mutation. J Biol Chem 1996;271:635-638.
    • (1996) J Biol Chem , vol.271 , pp. 635-638
    • Sato, S.1    Ward, C.L.2    Krouse, M.E.3    Wine, J.J.4    Kopito, R.R.5
  • 10
    • 33748944330 scopus 로고    scopus 로고
    • S-nitrosylating agents: A novel class of compounds that increase cystic fibrosis transmembrane conductance regulator expression and maturation in epithelial cells
    • Zaman K, Carraro S, Doherty J, Henderson EM, Lendermon E, Liu L, Verghese G, Zigler M, Ross M, Park E, et al. S-nitrosylating agents: a novel class of compounds that increase cystic fibrosis transmembrane conductance regulator expression and maturation in epithelial cells. Mol Pharmacol 2006;70:1435-1442.
    • (2006) Mol Pharmacol , vol.70 , pp. 1435-1442
    • Zaman, K.1    Carraro, S.2    Doherty, J.3    Henderson, E.M.4    Lendermon, E.5    Liu, L.6    Verghese, G.7    Zigler, M.8    Ross, M.9    Park, E.10
  • 11
    • 0034099743 scopus 로고    scopus 로고
    • Sodium 4-phenylbutryate downregulates HSC70: Implications for intracellular trafficking of ΔF508-CFTR
    • Rubenstein RC, Zeitlin PL. Sodium 4-phenylbutryate downregulates HSC70: implications for intracellular trafficking of ΔF508-CFTR. Am J Physiol 2000;278:C259-C267.
    • (2000) Am J Physiol , vol.278
    • Rubenstein, R.C.1    Zeitlin, P.L.2
  • 12
    • 24644464284 scopus 로고    scopus 로고
    • Small-molecule correctors of defective deltaF508-CFTR cellular processing identified by high-throughput screening
    • Pedemonte N, Lukacs GL, Du K, Caci E, Zegarra-Moran O, Galietta LJ, Verkman AS. Small-molecule correctors of defective deltaF508-CFTR cellular processing identified by high-throughput screening. J Clin Invest 2005;115:2564-2571.
    • (2005) J Clin Invest , vol.115 , pp. 2564-2571
    • Pedemonte, N.1    Lukacs, G.L.2    Du, K.3    Caci, E.4    Zegarra-Moran, O.5    Galietta, L.J.6    Verkman, A.S.7
  • 14
  • 18
    • 18244377969 scopus 로고    scopus 로고
    • Characterization of wild-type and deltaF508 cystic fibrosis transmembrane regulator in human respiratory epithelia
    • Kreda SM, Mall M, Mengos A, Rochelle L, Yankaskas J, Riordan JR, Boucher RC. Characterization of wild-type and deltaF508 cystic fibrosis transmembrane regulator in human respiratory epithelia. Mol Biol Cell 2005;16:2154-2167.
    • (2005) Mol Biol Cell , vol.16 , pp. 2154-2167
    • Kreda, S.M.1    Mall, M.2    Mengos, A.3    Rochelle, L.4    Yankaskas, J.5    Riordan, J.R.6    Boucher, R.C.7
  • 19
    • 33846245581 scopus 로고    scopus 로고
    • Acinar origin of CFTR-dependent airway submucosal gland fluid secretion
    • Wu JV, Krouse ME, Wine JJ. Acinar origin of CFTR-dependent airway submucosal gland fluid secretion. Am J Physiol 2007;292:L304-L311.
    • (2007) Am J Physiol , vol.292
    • Wu, J.V.1    Krouse, M.E.2    Wine, J.J.3
  • 22
    • 0023025504 scopus 로고
    • Cystic fibrosis and beta-adrenergic response of airway epithelial cell cultures
    • Widdicombe JH. Cystic fibrosis and beta-adrenergic response of airway epithelial cell cultures. Am J Physiol 1986;251:R818-R822.
    • (1986) Am J Physiol , vol.251
    • Widdicombe, J.H.1
  • 23
  • 24
    • 0037930844 scopus 로고    scopus 로고
    • Stimulation of beta 2-adrenergic receptor increases cystic fibrosis transmembrane conductance regulator expression in human airway epithelial cells through a cAMP/protein kinase a-independent pathway
    • Taouil K, Hinnrasky J, Hologne C, Corlieu P, Klossek JM, Puchelle E. Stimulation of beta 2-adrenergic receptor increases cystic fibrosis transmembrane conductance regulator expression in human airway epithelial cells through a cAMP/protein kinase a-independent pathway. J Biol Chem 2003;278:17320-17327.
    • (2003) J Biol Chem , vol.278 , pp. 17320-17327
    • Taouil, K.1    Hinnrasky, J.2    Hologne, C.3    Corlieu, P.4    Klossek, J.M.5    Puchelle, E.6
  • 26
    • 0032555156 scopus 로고    scopus 로고
    • + exchanger regulator factor family of PDZ proteins. Proc Natl Acad Sci USA 1998;95:8496-8501.
    • + exchanger regulator factor family of PDZ proteins. Proc Natl Acad Sci USA 1998;95:8496-8501.
  • 31
    • 0029841642 scopus 로고    scopus 로고
    • Sustained activation of a G protein-coupled receptor via ''anchored'' agonist binding: Molecular localization of the salmeterol exosite within the 2-adrenergic receptor
    • Green SA, Spasoff AP, Coleman RA, Johnson M, Liggett SB. Sustained activation of a G protein-coupled receptor via ''anchored'' agonist binding: molecular localization of the salmeterol exosite within the 2-adrenergic receptor. J Biol Chem 1996;271:24029-24035.
    • (1996) J Biol Chem , vol.271 , pp. 24029-24035
    • Green, S.A.1    Spasoff, A.P.2    Coleman, R.A.3    Johnson, M.4    Liggett, S.B.5
  • 34
    • 0028236014 scopus 로고
    • Rapid endocytosis of the cystic fibrosis transmembrane conductance regulator chloride channel
    • Prince LS, Workman RB Jr, Marchase RB. Rapid endocytosis of the cystic fibrosis transmembrane conductance regulator chloride channel. Proc Natl Acad Sci USA 1994;91:5192-5196.
    • (1994) Proc Natl Acad Sci USA , vol.91 , pp. 5192-5196
    • Prince, L.S.1    Workman Jr, R.B.2    Marchase, R.B.3
  • 35


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.