Characterization of Cln3p, the gene product responsible for juvenile neuronal ceroid lipofuscinosis, as a lysosomal integral membrane glycoprotein

Journal of Neurochemistry

Volumn 87, Issue 5, 2003, Pages 1296-1308

  Ezaki, Junji ^a   Takeda Ezaki, Mitsue ^a   Koike, Masato ^b   Ohsawa, Yoshiyuki ^b   Taka, Hikari ^a   Mineki, Reiko ^a   Murayama, Kimie ^a   Uchiyama, Yasuo ^b   Ueno, Takashi ^a   Kominami, Eiki ^a  

^a JUNTENDO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b OSAKA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

CLN3; LC MS; Lectin; Lysosomes; MS MS; Neuronal ceroid lipofuscinosis

Indexed keywords

BRAIN PROTEIN; CLN3P PROTEIN; GENE PRODUCT; LIVER PROTEIN; MEMBRANE PROTEIN; PEPTIDE ANTIBODY; UNCLASSIFIED DRUG;

AMINO ACID SEQUENCE; AMINO TERMINAL SEQUENCE; ANALYTIC METHOD; ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CELL LINE; CONTROLLED STUDY; CYTOSOL; EMBRYO; ENDOPLASMIC RETICULUM; GOLGI COMPLEX; HUMAN; HUMAN CELL; LIVER LYSOSOME; LYSOSOME MEMBRANE; MOLECULAR WEIGHT; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN BLOOD LEVEL; PROTEIN LOCALIZATION; PROTEIN PURIFICATION; RAT; TANDEM MASS SPECTROMETRY;

ANIMALS; BRAIN CHEMISTRY; CELL LINE; GLYCOPROTEINS; HUMANS; IMMUNOSORBENT TECHNIQUES; INTRACELLULAR MEMBRANES; KIDNEY; LIVER; MASS SPECTROMETRY; MEMBRANE GLYCOPROTEINS; MEMBRANE PROTEINS; MICE; MOLECULAR CHAPERONES; MOLECULAR WEIGHT; NEURONAL CEROID-LIPOFUSCINOSES; OLIGOSACCHARIDES; ORGAN SPECIFICITY; PROTEINS; SUBCELLULAR FRACTIONS;

ANIMALIA; MURINAE;

EID: 0344011621     PISSN: 00223042     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1471-4159.2003.02132.x     Document Type: Article

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