Endoplasmic reticulum-associated degradation of mutant CFTR requires a guanine nucleotide-sensitive step

International Journal of Biochemistry and Cell Biology

Volumn 40, Issue 9, 2008, Pages 1729-1742

  De Keukeleire, Béatrice ^a,b,c   Micoud, Julien ^a,b,c   Biard, Julie ^a,b,c   Benharouga, Mohamed ^a,b,c  

^a CNRS   (France)

^b CEA GRENOBLE   (France)

^c UNIV GRENOBLE ALPES   (France)

Author keywords

ATP; CFTR; Cystic fibrosis; ERAD; GTP; Proteasome

Indexed keywords

ADENOSINE TRIPHOSPHATE; GUANINE NUCLEOTIDE BINDING PROTEIN; GUANOSINE TRIPHOSPHATE; PROTEASOME; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ARTICLE; CELL STRAIN BHK; CELL STRAIN COS1; ENDOPLASMIC RETICULUM; GOLGI COMPLEX; MICROSOME; PROTEIN DEGRADATION; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN METABOLISM; PROTEIN MISFOLDING;

ADENOSINE TRIPHOSPHATE; ALUMINUM COMPOUNDS; ANIMALS; CELL LINE; CRICETINAE; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; ENDOPLASMIC RETICULUM; FLUORIDES; GUANOSINE TRIPHOSPHATE; HUMANS; MUTATION; PROTEASOME ENDOPEPTIDASE COMPLEX; RECEPTORS, ANTIGEN, T-CELL, ALPHA-BETA; SENSITIVITY AND SPECIFICITY;

EID: 49949152552     PISSN: 13572725     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.biocel.2007.12.015     Document Type: Article

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