PABPN1 polyalanine tract deletion and long expansions modify its aggregation pattern and expression

Experimental Cell Research

Volumn 314, Issue 8, 2008, Pages 1652-1666

  Klein, Arnaud F ^a   Ebihara, Mitsuru ^a   Alexander, Christine ^a   Dicaire, Marie Josée ^a   Sasseville, A Marie Josée ^a,b   Langelier, Yves ^b,c   Rouleau, Guy A ^a   Brais, Bernard ^a  

^a UNIVERSITY OF MONTREAL   (Canada)

^b CENTRE HOSPITALIER DE L UNIVERSITÉ DE MONTRÉAL   (Canada)

^c UNIVERSITÉ DE MONTRÉAL   (Canada)

Author keywords

Aggregate; Intranuclear inclusions; OPMD; PABPN1; Polyalanine

Indexed keywords

ALANINE; MUTANT PROTEIN; POLYADENYLIC ACID BINDING PROTEIN;

AMINO TERMINAL SEQUENCE; ANIMAL CELL; ARTICLE; AUTOSOMAL DOMINANT DISORDER; CELL NUCLEUS INCLUSION BODY; CELL NUCLEUS MEMBRANE; CELL SURVIVAL; CELLULAR DISTRIBUTION; CONTROLLED STUDY; CYTOPLASM; GENE OVEREXPRESSION; HUMAN; HUMAN CELL; NONHUMAN; OCULOPHARYNGEAL MUSCULAR DYSTROPHY; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN EXPRESSION;

EID: 43049151758     PISSN: 00144827     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.yexcr.2008.02.005     Document Type: Article

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