Nuclear inclusions in oculopharyngeal muscular dystrophy consist of poly(A) binding protein 2 aggregates which sequester poly(A) RNA

Human Molecular Genetics

Volumn 9, Issue 15, 2000, Pages 2321-2328

  Calado, Angelo ^a   Tomé, Fernando M S ^b   Brais, Bernard ^c   Rouleau, G A ^d   Kühn, Uwe ^e   Wahle, Elmar ^e   Carmo Fonseca, Maria ^a  

^a INSTITUTO DE MEDICINA MOLECULAR   (Portugal)

^b PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

^c CENTRE HOSPITALIER DE L UNIVERSITÉ DE MONTRÉAL   (Canada)

^d MCGILL UNIVERSITY   (Canada)

^e MARTIN LUTHER UNIVERSITY HALLE WITTENBERG   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ALANINE; BINDING PROTEIN; POLYADENYLATED RNA; POLYADENYLIC ACID; PROTEASOME; PROTEIN ANTIBODY; PROTEIN SUBUNIT; SODIUM CHLORIDE; UBIQUITIN;

ANTIBODY LABELING; ARTICLE; CELL ACTIVITY; CELL NUCLEUS INCLUSION BODY; CONFOCAL MICROSCOPY; CONTROLLED STUDY; EXTRACTION; FLUORESCENCE MICROSCOPY; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOELECTRON MICROSCOPY; MYOBLAST; OCULOPHARYNGEAL MUSCULAR DYSTROPHY; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN FOLDING; PROTEIN LOCALIZATION;

EID: 0034703413     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/oxfordjournals.hmg.a018924     Document Type: Article

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