Structural and functional alterations of muscle fibres in the novel mouse model of facioscapulohumeral muscular dystrophy

Journal of Physiology

Volumn 584, Issue 3, 2007, Pages 997-1009

  D'antona, Giuseppe ^a   Brocca, Lorenza ^a   Pansarasa, Orietta ^a   Rinaldi, Chiara ^a   Tupler, Rossella ^b   Bottinelli, Roberto ^a  

^a UNIVERSITY OF PAVIA   (Italy)

^b UNIVERSITY OF MODENA AND REGGIO EMILIA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

GENE PRODUCT; MAJOR HISTOCOMPATIBILITY ANTIGEN; PROTEIN FRG1; UNCLASSIFIED DRUG; MYOSIN HEAVY CHAIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; CROSS-SECTIONAL STUDY; FACIOSCAPULOHUMERAL MUSCULAR DYSTROPHY; FAST MUSCLE FIBER; FEMALE; GENE OVEREXPRESSION; HISTOPATHOLOGY; IN VITRO STUDY; IN VIVO STUDY; MORPHOLOGY; MOUSE; MUSCLE CONTRACTION; MUSCLE FORCE; MUSCLE FUNCTION; NONHUMAN; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; SLOW MUSCLE FIBER; SOLEUS MUSCLE; WILD TYPE; CELL FUNCTION; CELL STRUCTURE; DISEASE ACTIVITY; DISEASE ASSOCIATION; FRG1 GENE; GENE; MOLECULAR DYNAMICS; MOLECULAR PATHOLOGY; MUSCLE CELL; MUSCLE STRENGTH; STRUCTURE ANALYSIS;

AGING; ANIMALS; DISEASE MODELS, ANIMAL; GENE EXPRESSION REGULATION; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MUSCLE FIBERS; MUSCULAR DYSTROPHIES; MYOSIN HEAVY CHAINS; PROTEIN ISOFORMS; PROTEINS;

EID: 35648963574     PISSN: 00223751     EISSN: 14697793     Source Type: Journal    
DOI: 10.1113/jphysiol.2007.141481     Document Type: Article

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