Cytoskeleton as a potential target in the neuropathology of maple syrup urine disease: Insight from animal studies

Journal of Inherited Metabolic Disease

Volumn 30, Issue 5, 2007, Pages 664-672

  Pessoa Pureur, R ^a   Wajner, M ^a  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA TOCOPHEROL; CREATINE; ETHYLENE GLYCOL 1,2 BIS(2 AMINOPHENYL) ETHER N,N,N',N' TETRAACETIC ACID; GLUTAMATE RECEPTOR ANTAGONIST; N METHYL DEXTRO ASPARTIC ACID RECEPTOR BLOCKING AGENT; NIFEDIPINE; OXOACID;

CELL ENERGY; CELL FUNCTION; CELL VIABILITY; CYTOSKELETON; DEVELOPMENT; DRUG TARGETING; EXCITOTOXICITY; HUMAN; MAPLE SYRUP URINE DISEASE; METABOLIC DISORDER; METABOLITE; NERVE CELL NECROSIS; NEUROLOGIC DISEASE; NONHUMAN; OXIDATIVE STRESS; PROTEIN PHOSPHORYLATION; REVIEW;

AMINO ACIDS, BRANCHED-CHAIN; ANIMALS; BRAIN; CELL SURVIVAL; CYTOSKELETON; ENERGY METABOLISM; EXCITATORY AMINO ACID AGONISTS; MAPLE SYRUP URINE DISEASE; OXIDATIVE STRESS; PHOSPHORYLATION; RATS; RHO GTP-BINDING PROTEINS; SIGNAL TRANSDUCTION;

EID: 35248856380     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-007-0562-6     Document Type: Review

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