Creatine and antioxidant treatment prevent the inhibition of creatine kinase activity and the morphological alterations of C6 glioma cells induced by the branched-chain α-keto acids accumulating in maple syrup urine disease

Cellular and Molecular Neurobiology

Volumn 26, Issue 1, 2006, Pages 67-79

  Funchal, Cláudia ^a   Schuck, Patrícia Fernanda ^a   Santos, André Quincozes Dos ^a   Jacques Silva, Maria Caroline ^a   Gottfried, Carmem ^a   Pessoa Pureur, Regina ^a   Wajner, Moacir ^a  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

Author keywords

Antioxidants; Branched chain keto acids; Creatine; Creatine kinase; Maple syrup urine diasease

Indexed keywords

2 OXOACID; 2 OXOISOCAPROIC ACID; 2 OXOISOVALERIC ACID; 3 METHYL 2 OXOVALERIC ACID; ALPHA TOCOPHEROL; ANTIOXIDANT; BRANCHED CHAIN ALPHA KETOACID DERIVATIVE; BRANCHED CHAIN AMINO ACID; CREATINE; CREATINE KINASE; GLUTATHIONE; N(G) NITROARGININE METHYL ESTER; NITRIC OXIDE; NITRIC OXIDE SYNTHASE INHIBITOR; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; BODY FLUID; BRAIN METABOLISM; CELL STRUCTURE; CONTROLLED STUDY; ENERGY METABOLISM; ENZYME ACTIVITY; ENZYME INHIBITION; GLIOMA CELL; HOMEOSTASIS; MAPLE SYRUP URINE DISEASE; NERVE DEGENERATION; NONHUMAN; PRIORITY JOURNAL; RAT;

ACER;

EID: 33745624848     PISSN: 02724340     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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