Morphological alterations and cell death provoked by the branched-chain α-amino acids accumulating in maple syrup urine disease in astrocytes from rat cerebral cortex

Cellular and Molecular Neurobiology

Volumn 25, Issue 5, 2005, Pages 851-867

  Funchal, Cláudia ^a   Gottfried, Carmem ^a   Vieira De Almeida, Lúcia Maria ^a   Dos Santos, André Quincozes ^a   Wajner, Moacir ^a   Pessoa Pureur, Regina ^a  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

Author keywords

Actin; Branched chain amino acids; Creatine; Cytoskeleton; Lysophosphatidic acid; Maple syrup urine disease

Indexed keywords

ALPHA AMINO ACID; BRANCHED CHAIN AMINO ACID; CREATINE; ISOLEUCINE; LEUCINE; LYSOPHOSPHATIDIC ACID; RHOA GUANINE NUCLEOTIDE BINDING PROTEIN; VALINE;

ANIMAL CELL; ARTICLE; ASTROCYTE; BRAIN CORTEX; CELL DEATH; CELL NUCLEUS; CELL SHAPE; CELL STRUCTURE; CELL VIABILITY; CONCENTRATION RESPONSE; CONTROLLED STUDY; CYTOSKELETON; IMMUNOHISTOCHEMISTRY; MAPLE SYRUP URINE DISEASE; NEWBORN; NONHUMAN; PRIORITY JOURNAL; RAT;

AMINO ACIDS, BRANCHED-CHAIN; ANIMALS; ASTROCYTES; CELL DEATH; CELL NUCLEUS; CELL SURVIVAL; CELLS, CULTURED; CEREBRAL CORTEX; CREATINE; IMMUNOHISTOCHEMISTRY; LYSOPHOSPHOLIPIDS; MAPLE SYRUP URINE DISEASE; RATS;

ACER;

EID: 23844540128     PISSN: 02724340     EISSN: None     Source Type: Journal    
DOI: 10.1007/s10571-005-4938-6     Document Type: Article

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