Loss-of-function GJA12/Connexin47 mutations cause Pelizaeus-Merzbacher-like disease

Molecular and Cellular Neuroscience

Volumn 34, Issue 4, 2007, Pages 629-641

  Orthmann Murphy, Jennifer L ^a   Enriquez, Alan D ^a   Abrams, Charles K ^b   Scherer, Steven S ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

Author keywords

Connexin47; Gap junctions; Myelin; Oligodendrocytes; Pelizaeus Merzbacher like disease

Indexed keywords

CONNEXIN 47; GENE PRODUCT; LUCIFER YELLOW; M283T PROTEIN; MUTANT PROTEIN; NEUROBIOTIN; P87S PROTEIN; UNCLASSIFIED DRUG; Y269D PROTEIN;

ANIMAL CELL; ARTICLE; ASTROCYTE; CELL TRANSFER; CENTRAL NERVOUS SYSTEM; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; GAP JUNCTION; GENE FUNCTION; GENE MUTATION; HELA CELL; HUMAN; HUMAN CELL; IMMUNOHISTOCHEMISTRY; MYELIN DEFICIENCY; NONHUMAN; NUCLEOTIDE SEQUENCE; OLIGODENDROGLIA; PATCH CLAMP; PELIZAEUS MERZBACHER DISEASE; PRIMATE; PRIORITY JOURNAL; PROTEIN FUNCTION; WHOLE CELL; WILD TYPE;

AMINO ACID SEQUENCE; ANIMALS; ASTROCYTES; BLOTTING, WESTERN; BRAIN; CELL COMMUNICATION; CONNEXINS; ENDOPLASMIC RETICULUM; GAP JUNCTIONS; HELA CELLS; HUMANS; IMMUNOHISTOCHEMISTRY; MACACA MULATTA; MOLECULAR SEQUENCE DATA; MUTATION; OLIGODENDROGLIA; PATCH-CLAMP TECHNIQUES; PELIZAEUS-MERZBACHER DISEASE; POLYMERASE CHAIN REACTION; TRANSFECTION;

PRIMATES;

EID: 33947657477     PISSN: 10447431     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.mcn.2007.01.010     Document Type: Article

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