Complementation between mouse Mfn1 and Mfn2 protects mitochondrial fusion defects caused by CMT2A disease mutations

Journal of Cell Biology

Volumn 176, Issue 4, 2007, Pages 405-414

  Detmer, Scott A ^a   Chan, David C ^a  

^a CALIFORNIA INSTITUTE OF TECHNOLOGY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MITOFUSIN 1; MITOFUSIN 2; PROTEIN; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; GENE MUTATION; GENETIC COMPLEMENTATION; HEREDITARY MOTOR SENSORY NEUROPATHY; MITOCHONDRION; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; WILD TYPE;

ANIMALS; AXONS; CELLS, CULTURED; CHARCOT-MARIE-TOOTH DISEASE; FIBROBLASTS; GENETIC PREDISPOSITION TO DISEASE; GTP PHOSPHOHYDROLASES; MACROMOLECULAR SUBSTANCES; MEMBRANE FUSION; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MITOCHONDRIA; MUTATION; PERIPHERAL NERVES; WALLERIAN DEGENERATION;

EID: 33846952150     PISSN: 00219525     EISSN: 00219525     Source Type: Journal    
DOI: 10.1083/jcb.200611080     Document Type: Article

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