Neuropathologic features of frontotemporal lobar degeneration with ubiquitin-positive inclusions with progranulin gene (PGRN) mutations

Journal of Neuropathology and Experimental Neurology

Volumn 66, Issue 2, 2007, Pages 142-151

  Josephs, Keith A ^a   Ahmed, Zeshan ^b   Katsuse, Omi ^c   Parisi, Joseph F ^a   Boeve, Bradley F ^a   Knopman, David S ^a   Petersen, Ronald C ^a   Davies, Peter ^d   Duara, Ranjan ^e   Graff Radford, Neill R ^b   Uitti, Ryan J ^b   Rademakers, Rosa ^b   Adamson, Jennifer ^b   Baker, Matthew ^b   Hutton, Michael L ^b   Dickson, Dennis W ^b  

^a MAYO CLINIC   (United States)

^b MAYO CLINIC   (United States)

^c YOKOHAMA CITY UNIVERSITY   (Japan)

^d ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

^e MOUNT SINAI MEDICAL CENTER   (United States)

Author keywords

Frontotemporal dementia; Frontotemporal lobar degeneration; Progranulin; TDP 43; Ubiquitin

Indexed keywords

PROGRANULIN; UBIQUITIN;

ADULT; AGED; ARTICLE; BRAIN ATROPHY; BRAIN DEGENERATION; BRAIN SIZE; CELL DENSITY; CELL NUCLEUS INCLUSION BODY; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; FEMALE; FRONTAL LOBE; GENE MUTATION; HIPPOCAMPAL SCLEROSIS; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNOREACTIVITY; LANGUAGE DISABILITY; MALE; NEURITE; NEUROFIBRILLARY TANGLE; NEUROPATHOLOGY; PARKINSONISM; PRIORITY JOURNAL; TEMPORAL LOBE;

AGED; AGED, 80 AND OVER; ATROPHY; BRAIN; DEMENTIA; FEMALE; FRONTAL LOBE; HIPPOCAMPUS; HUMANS; INTERCELLULAR SIGNALING PEPTIDES AND PROTEINS; INTRANUCLEAR INCLUSION BODIES; MALE; MIDDLE AGED; MUTATION; NEURITES; NEURONS; RETROSPECTIVE STUDIES; UBIQUITIN;

EID: 33846794448     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1097/nen.0b013e31803020cf     Document Type: Article

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