Neurofilament inclusion body disease: A new proteinopathy?

Brain

Volumn 126, Issue 10, 2003, Pages 2291-2303

  Josephs, Keith A ^a,d   Holton, Janice L ^d   Rossor, Martin N ^d   Braendgaard, Hans ^e   Ozawa, Tetsutaro ^d   Fox, Nick C ^d   Petersen, Ronald C ^a   Pearl, Gary S ^c   Ganguly, Milan ^d   Rosa, Pedro ^e   Laursen, Henning ^f   Parisi, Joseph E ^a   Waldemar, Gunhild ^f   Quinn, Niall P ^d   Dickson, Dennis W ^a,b   Revesz, Tamas ^d  

^a MAYO CLINIC   (United States)

^b MAYO CLINIC   (United States)

^c ORLANDO REGIONAL MEDICAL CENTER   (United States)

^d UNIVERSITY COLLEGE LONDON   (United Kingdom)

^e AARHUS UNIVERSITY HOSPITAL   (Denmark)

^f Mental Health Services CPH   (Denmark)

Author keywords

Corticobasal degeneration; Frontotemporal dementia; Neurofilament; Neurofilament inclusion body disease; Ubiquitin

Indexed keywords

ALPHA SYNUCLEIN; HYALIN; NEUROFILAMENT PROTEIN; PROTEIN ANTIBODY; PROTEIN SUBUNIT; SILVER; TAU PROTEIN; UBIQUITIN;

ADULT; ARTICLE; BASAL GANGLION; BASOPHIL; BRAIN ATROPHY; BRAIN BIOPSY; BRAIN STEM; CASE REPORT; CAUDATE NUCLEUS; CELL INCLUSION; CELL NUCLEUS; CLINICAL FEATURE; CORTICOBASAL DEGENERATION; DEATH; DISEASE COURSE; DISEASE DURATION; EOSINOPHIL; FEMALE; FRONTAL CORTEX; FRONTAL LOBE; FRONTOTEMPORAL DEMENTIA; GRANULAR CELL; HUMAN; IMMOBILIZATION; IMMUNOCOMPETENT CELL; IMMUNOHISTOCHEMISTRY; MALE; MEDICAL EXAMINATION; NERVE CELL; NEUROFILAMENT; NEUROFILAMENT INCLUSION BODY; NEUROPATHOLOGY; NUCLEAR MAGNETIC RESONANCE IMAGING; ONSET AGE; POSITRON EMISSION TOMOGRAPHY; PRIORITY JOURNAL; PROTEIN DEFECT; PROTEIN LOCALIZATION; PROTEINOPATHY; SILVER STAINING; SINGLE PHOTON EMISSION COMPUTER TOMOGRAPHY; STAINING; TECHNIQUE; TEMPORAL CORTEX; TEMPORAL LOBE; CHEMISTRY; COMPUTER ASSISTED EMISSION TOMOGRAPHY; DEGENERATIVE DISEASE; DEMENTIA; ELECTRON MICROSCOPY; FATALITY; METABOLISM; METHODOLOGY; MIDDLE AGED; PATHOLOGY; RADIOGRAPHY;

ADULT; BASAL GANGLIA; BRAIN STEM; DEMENTIA; FATAL OUTCOME; FEMALE; FRONTAL LOBE; HUMANS; IMMUNOHISTOCHEMISTRY; INCLUSION BODIES; MAGNETIC RESONANCE IMAGING; MALE; MICROSCOPY, ELECTRON; MIDDLE AGED; NEURODEGENERATIVE DISEASES; NEUROFILAMENT PROTEINS; NEURONS; TEMPORAL LOBE; TOMOGRAPHY, EMISSION-COMPUTED; TOMOGRAPHY, EMISSION-COMPUTED, SINGLE-PHOTON; UBIQUITIN;

EID: 0242336433     PISSN: 00068950     EISSN: None     Source Type: Journal    
DOI: 10.1093/brain/awg231     Document Type: Article

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