Thiamine pyrophosphate: An essential cofactor for the α-oxidation in mammals - Implications for thiamine deficiencies?

Cellular and Molecular Life Sciences

Volumn 63, Issue 13, 2006, Pages 1553-1563

  Sniekers, M ^a   Foulon, V ^a   Mannaerts, G P ^a   Van Maldergem, L ^b   Mandel, H ^c   Gelb, B D ^d   Casteels, M ^a   Van Veldhoven, P P ^a  

^a UNIVERSITY OF LEUVEN   (Belgium)

^b UNIVERSITY OF LIÈGE   (Belgium)

^c RAMBAM MEDICAL CENTER   (Israel)

^d MOUNT SINAI SCHOOL OF MEDICINE   (United States)

Author keywords

2 hydroxyfatty acids; Beriberi; Peroxisomes; Phytanic acid; Thiamine responsive megaloblastic anemia; Vitamin B; Wernicke Korsakoff syndrome

Indexed keywords

2 HYDROXYPHYTANOYL COA LYASE; COCARBOXYLASE; HYDROXY FATTY ACID; THIAMINE; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL CELL CULTURE; BIOACCUMULATION; CONFERENCE PAPER; CONTROLLED STUDY; DISEASE ASSOCIATION; ESTERIFICATION; FATTY ACID OXIDATION; FIBROBLAST; HUMAN; HUMAN CELL; MAMMAL; MEGALOBLASTIC ANEMIA; MOUSE; NONHUMAN; PATHOGENESIS; PATHOPHYSIOLOGY; PEROXISOME; PROTEIN FUNCTION; RAT; THIAMINE DEFICIENCY;

ANEMIA, MEGALOBLASTIC; ANIMALS; CARBON-CARBON LYASES; FATTY ACIDS; FIBROBLASTS; HEPATOCYTES; HUMANS; MICE; OXIDATION-REDUCTION; PHYTANIC ACID; RATS; RATS, WISTAR; THIAMINE; THIAMINE DEFICIENCY; THIAMINE PYROPHOSPHATE;

ANIMALIA; MAMMALIA;

EID: 33746651557     PISSN: 1420682X     EISSN: 15691632     Source Type: Journal    
DOI: 10.1007/s00018-005-5603-4     Document Type: Conference Paper

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