-
1
-
-
0028978668
-
Phytanic acid α-oxidation in rat liver peroxisomes. Production of α-hydroxyphytanoyl-CoA and formate is enhanced by dioxygenase cofactors
-
Mihalik, S. J., A. M. Rainville, and P. A. Watkins. 1995. Phytanic acid α-oxidation in rat liver peroxisomes. Production of α-hydroxyphytanoyl-CoA and formate is enhanced by dioxygenase cofactors. Eur. J. Biochem. 232: 545-551.
-
(1995)
Eur. J. Biochem.
, vol.232
, pp. 545-551
-
-
Mihalik, S.J.1
Rainville, A.M.2
Watkins, P.A.3
-
2
-
-
0029662167
-
2, cofactor requirements, subcellular localization and formation of a 2-hydroxy-3-methylacyl-CoA intermediate
-
2, cofactor requirements, subcellular localization and formation of a 2-hydroxy-3-methylacyl-CoA intermediate. Eur. J. Biochem. 240: 674-683.
-
(1996)
Eur. J. Biochem.
, vol.240
, pp. 674-683
-
-
Croes, K.1
Casteels, M.2
De Hoffmann, K.3
Mannaerts, G.P.4
Van Veldhoven, P.P.5
-
3
-
-
0030569533
-
Phytanoyl-CoA hydroxylase is present in human liver, located in peroxisomes, and deficient in Zellweger syndrome: Direct, unequivocal evidence for the new, revised pathway of phytanic acid α-oxidation in humans
-
Jansen, G. A., S. J. Mihalik, P. A. Watkins, H. W. Moser, C. Jacobs, S. Denis, and R. J. Wanders. 1996. Phytanoyl-CoA hydroxylase is present in human liver, located in peroxisomes, and deficient in Zellweger syndrome: direct, unequivocal evidence for the new, revised pathway of phytanic acid α-oxidation in humans. Biochem. Biophys. Res. Commun. 229: 205-210.
-
(1996)
Biochem. Biophys. Res. Commun.
, vol.229
, pp. 205-210
-
-
Jansen, G.A.1
Mihalik, S.J.2
Watkins, P.A.3
Moser, H.W.4
Jacobs, C.5
Denis, S.6
Wanders, R.J.7
-
4
-
-
0030882145
-
Peroxisomal localization of α-oxidation in human liver
-
Casteels, M., K. Croes, P. P. Van Veldhoven, and G. P. Mannaerts. 1997. Peroxisomal localization of α-oxidation in human liver. J. Inherited Metab. Dis. 20: 665-673.
-
(1997)
J. Inherited Metab. Dis.
, vol.20
, pp. 665-673
-
-
Casteels, M.1
Croes, K.2
Van Veldhoven, P.P.3
Mannaerts, G.P.4
-
5
-
-
0031589134
-
Production of formyl-CoA during peroxisomal α-oxidation of 3-methyl-branched fatty acids
-
Croes, K., P. P. Van Veldhoven, G. P. Mannaerts, and M. Casteels. 1997. Production of formyl-CoA during peroxisomal α-oxidation of 3-methyl-branched fatty acids. FEBS Lett. 407: 197-200.
-
(1997)
FEBS Lett.
, vol.407
, pp. 197-200
-
-
Croes, K.1
Van Veldhoven, P.P.2
Mannaerts, G.P.3
Casteels, M.4
-
6
-
-
0030876007
-
Formation of a 2-methyl-branched fatty aldehyde during peroxisomal α-oxidation
-
Croes, K., M. Casteels, S. Asselberghs, P. Herdewijn, G. P. Mannaerts, and P. P. Van Veldhoven. 1997. Formation of a 2-methyl-branched fatty aldehyde during peroxisomal α-oxidation. FEBS Lett. 412: 643-645.
-
(1997)
FEBS Lett.
, vol.412
, pp. 643-645
-
-
Croes, K.1
Casteels, M.2
Asselberghs, S.3
Herdewijn, P.4
Mannaerts, G.P.5
Van Veldhoven, P.P.6
-
7
-
-
0031559604
-
Resolution of the α-oxidation pathway: Identification of pristanal as product of the decarboxylation of 2-hydroxyphytanoyl-CoA
-
Verhoeven, N. M., D. S. M. Schor, H. J. ten Brink, R. J. A. Wanders, and C. Jakobs. 1997. Resolution of the α-oxidation pathway: identification of pristanal as product of the decarboxylation of 2-hydroxyphytanoyl-CoA. Biochem. Biophys. Res. Commun. 237: 33-36.
-
(1997)
Biochem. Biophys. Res. Commun.
, vol.237
, pp. 33-36
-
-
Verhoeven, N.M.1
Schor, D.S.M.2
Ten Brink, H.J.3
Wanders, R.J.A.4
Jakobs, C.5
-
8
-
-
0025304695
-
A comparative study of straight chain and branched chain fatty acid oxidation in skin fibroblasts from patients with peroxisomal disorders
-
Singh, H., S. Usher, D. Johnson, and A. Poulos. 1990. A comparative study of straight chain and branched chain fatty acid oxidation in skin fibroblasts from patients with peroxisomal disorders. J. Lipid Res. 31: 217-225.
-
(1990)
J. Lipid Res.
, vol.31
, pp. 217-225
-
-
Singh, H.1
Usher, S.2
Johnson, D.3
Poulos, A.4
-
9
-
-
0026348109
-
Mitochondrial and peroxisomal β-oxidation of the branched chain fatty acid 2-methylpalmitate in rat liver
-
Vanhove, G., P. P. Van Veldhoven, F. Vanhoutte, G. Parmentier, H. J. Eyssen, and G. P. Mannaerts. 1991. Mitochondrial and peroxisomal β-oxidation of the branched chain fatty acid 2-methylpalmitate in rat liver. J. Biol. Chem. 266: 24670-24675.
-
(1991)
J. Biol. Chem.
, vol.266
, pp. 24670-24675
-
-
Vanhove, G.1
Van Veldhoven, P.P.2
Vanhoutte, F.3
Parmentier, G.4
Eyssen, H.J.5
Mannaerts, G.P.6
-
10
-
-
0027216304
-
The deficient degradation of synthetic 2-and 3-methyl-branched fatty acids in fibroblasts from patients with peroxisomal disorders
-
Van Veldhoven, P. P., S. Huang, H. J. Eyssen, and G. P. Mannaerts. 1993. The deficient degradation of synthetic 2-and 3-methyl-branched fatty acids in fibroblasts from patients with peroxisomal disorders. J. Inherited Metab. Dis. 16: 381-391.
-
(1993)
J. Inherited Metab. Dis.
, vol.16
, pp. 381-391
-
-
Van Veldhoven, P.P.1
Huang, S.2
Eyssen, H.J.3
Mannaerts, G.P.4
-
11
-
-
0028180291
-
β-Oxidation of fatty acids in cultured human skin fibroblasts devoid of the capacity for oxidative phosphorylation
-
Jakobs, B. S., C. van den Bogert, G. Dacremont, and R. J. A. Wanders. 1994. β-Oxidation of fatty acids in cultured human skin fibroblasts devoid of the capacity for oxidative phosphorylation. Biochim. Biophys. Acta. 1211: 37-43.
-
(1994)
Biochim. Biophys. Acta
, vol.1211
, pp. 37-43
-
-
Jakobs, B.S.1
Van Den Bogert, C.2
Dacremont, G.3
Wanders, R.J.A.4
-
12
-
-
0028177847
-
Peroxisomal β-oxidation of branched chain fatty acids in rat liver. Evidence that carnitine palmitoyltransferase I prevents transport of branched chain fatty acids into mitochondria
-
Singh, H., K. Beckman, and A. Poulos. 1994. Peroxisomal β-oxidation of branched chain fatty acids in rat liver. Evidence that carnitine palmitoyltransferase I prevents transport of branched chain fatty acids into mitochondria. J. Biol. Chem. 269: 9514-9520.
-
(1994)
J. Biol. Chem.
, vol.269
, pp. 9514-9520
-
-
Singh, H.1
Beckman, K.2
Poulos, A.3
-
13
-
-
0032537502
-
Involvement of microsomal fatty aldehyde dehydrogenase in the α-oxidation of phytanic acid
-
Verhoeven, N. M., C. Jacobs, G. Carney, M. P. Somers, R. J. A. Wanders, and W. B. Rizzo. 1998. Involvement of microsomal fatty aldehyde dehydrogenase in the α-oxidation of phytanic acid. FEBS Lett. 429: 225-228.
-
(1998)
FEBS Lett.
, vol.429
, pp. 225-228
-
-
Verhoeven, N.M.1
Jacobs, C.2
Carney, G.3
Somers, M.P.4
Wanders, R.J.A.5
Rizzo, W.B.6
-
14
-
-
51249187265
-
The occurrence of diastereoisomers of phytanic and pristanic acids and their determination by gas-liquid chromatography
-
Ackman, R. G., and R. P. Hansen. 1967. The occurrence of diastereoisomers of phytanic and pristanic acids and their determination by gas-liquid chromatography. Lipids. 2: 357-362.
-
(1967)
Lipids
, vol.2
, pp. 357-362
-
-
Ackman, R.G.1
Hansen, R.P.2
-
15
-
-
0015874214
-
The chemistry and biochemistry og phytanic, pristanic and related acids
-
Lough, A. K. 1973. The chemistry and biochemistry og phytanic, pristanic and related acids. Prog. Chem. Fats Other Lipids. 14: 1-48.
-
(1973)
Prog. Chem. Fats Other Lipids
, vol.14
, pp. 1-48
-
-
Lough, A.K.1
-
17
-
-
0027217062
-
Accumulation of phytanic acid α-oxidation intermediates in Zellweger fibroblasts
-
Fingerhut, R., W. Schmitz, and E. Conzelmann. 1993. Accumulation of phytanic acid α-oxidation intermediates in Zellweger fibroblasts. J. Inher. Metab. Dis. 16: 591-594.
-
(1993)
J. Inher. Metab. Dis.
, vol.16
, pp. 591-594
-
-
Fingerhut, R.1
Schmitz, W.2
Conzelmann, E.3
-
18
-
-
0029898658
-
Peroxisomal β-oxidation of 2-methyl-branched acyl-CoA esters: Stereospecific recognition of the 2S-methyl compounds by trihydroxycoprostanoyl-CoA oxidase and pristanoyl-CoA oxidase
-
Van Veldhoven, P. P., K. Croes, S. Asselberghs, P. Herdewijn, and G. P. Mannaerts. 1996. Peroxisomal β-oxidation of 2-methyl-branched acyl-CoA esters: stereospecific recognition of the 2S-methyl compounds by trihydroxycoprostanoyl-CoA oxidase and pristanoyl-CoA oxidase. FEBS Lett. 388: 80-84.
-
(1996)
FEBS Lett.
, vol.388
, pp. 80-84
-
-
Van Veldhoven, P.P.1
Croes, K.2
Asselberghs, S.3
Herdewijn, P.4
Mannaerts, G.P.5
-
19
-
-
0031053480
-
Stereochemistry of peroxisomal and mitochondrial β-oxidation of α-methylacyl-CoAs
-
Schmitz, W., and E. Conzelmann. 1997. Stereochemistry of peroxisomal and mitochondrial β-oxidation of α-methylacyl-CoAs. Eur. J. Biochem. 244: 434-440.
-
(1997)
Eur. J. Biochem.
, vol.244
, pp. 434-440
-
-
Schmitz, W.1
Conzelmann, E.2
-
20
-
-
0028176487
-
Purification and properties of an α-methylacyl-CoA racemase from rat liver
-
Schmitz, W., R. Fingerhut, and F. Conzelmann. 1991. Purification and properties of an α-methylacyl-CoA racemase from rat liver. Eur. J. Biochem. 222: 313-323.
-
(1991)
Eur. J. Biochem.
, vol.222
, pp. 313-323
-
-
Schmitz, W.1
Fingerhut, R.2
Conzelmann, F.3
-
21
-
-
0015919202
-
Studies on the stereospecificity of mitochondrial oxidation of phytanic acid and of α-hydroxyphytanic acid
-
Tsai, S. C., D. Steinberg, J. Avigan, and H. M. Fales. 1973. Studies on the stereospecificity of mitochondrial oxidation of phytanic acid and of α-hydroxyphytanic acid. J. Biol. Chem. 248: 1091-1097.
-
(1973)
J. Biol. Chem.
, vol.248
, pp. 1091-1097
-
-
Tsai, S.C.1
Steinberg, D.2
Avigan, J.3
Fales, H.M.4
-
22
-
-
0026770948
-
α-Oxidation of 3-methyl-substituted fatty acids in rat liver
-
Huang, S., P. P. Van Veldhoven, F. Vanhoutte, G. Parmentier, H. J. Eyssen, and G. P. Mannaerts. 1992. α-Oxidation of 3-methyl-substituted fatty acids in rat liver. Arch. Biochem. Biophys. 296: 214-223.
-
(1992)
Arch. Biochem. Biophys.
, vol.296
, pp. 214-223
-
-
Huang, S.1
Van Veldhoven, P.P.2
Vanhoutte, F.3
Parmentier, G.4
Eyssen, H.J.5
Mannaerts, G.P.6
-
23
-
-
0030851630
-
Evidence that multifunctional protein 2, and not multifunctional protein 1, is involved in the peroxisomal β-oxidation of pristanic acid
-
Dieuaide-Noubhani, M., S. Asselberghs, G. P. Mannaerts, and P. P. Van Veldhoven. 1997. Evidence that multifunctional protein 2, and not multifunctional protein 1, is involved in the peroxisomal β-oxidation of pristanic acid. Biochem. J. 325: 367-373.
-
(1997)
Biochem. J.
, vol.325
, pp. 367-373
-
-
Dieuaide-Noubhani, M.1
Asselberghs, S.2
Mannaerts, G.P.3
Van Veldhoven, P.P.4
-
24
-
-
0016162986
-
The isolation of hormone-sensitive rat hepatocytes by a modified enzymatic technique
-
Zahlten, R. N., and F. W. Stratman. 1974. The isolation of hormone-sensitive rat hepatocytes by a modified enzymatic technique. Arch. Biochem. Biophys. 163: 600-608.
-
(1974)
Arch. Biochem. Biophys.
, vol.163
, pp. 600-608
-
-
Zahlten, R.N.1
Stratman, F.W.2
-
25
-
-
0027993403
-
Aminotriazole is a potent inhibitor of α-oxidation of 3-methyl-substituted fatty acids in rat liver
-
Casteels, M., K. Croes, P. P. Van Veldhoven, and G. P. Mannaerts. 1994. Aminotriazole is a potent inhibitor of α-oxidation of 3-methyl-substituted fatty acids in rat liver. Biochem. Pharmacol. 48: 1973-1975.
-
(1994)
Biochem. Pharmacol.
, vol.48
, pp. 1973-1975
-
-
Casteels, M.1
Croes, K.2
Van Veldhoven, P.P.3
Mannaerts, G.P.4
-
26
-
-
0031565663
-
2-methylacyl racemase: A coupled assay based on the use of pristanoyl-CoA oxidase/peroxidase and reinvestigation of its subcellular distribution in rat and human liver
-
Van Veldhoven, P. P., K. Croes, M. Casteels, and G. P. Mannaerts. 1997. 2-Methylacyl racemase: a coupled assay based on the use of pristanoyl-CoA oxidase/peroxidase and reinvestigation of its subcellular distribution in rat and human liver. Biochem. Biophys. Acta. 1347: 62-68.
-
(1997)
Biochem. Biophys. Acta
, vol.1347
, pp. 62-68
-
-
Van Veldhoven, P.P.1
Croes, K.2
Casteels, M.3
Mannaerts, G.P.4
-
27
-
-
0017168453
-
Phosphorus in organic synthesis XI. Amino acids and peptides XXI. Reaction of diethyl phosphorocyanidate (DEPC) with carboxylic acids. A new synthesis of carboxylic esters and amides
-
Shioiri, T., Y. Yokoyama, Y. Kasai, and S. Yamada. 1976. Phosphorus in organic synthesis XI. Amino acids and peptides XXI. Reaction of diethyl phosphorocyanidate (DEPC) with carboxylic acids. A new synthesis of carboxylic esters and amides. Tetrahedron. 32: 2211-2217.
-
(1976)
Tetrahedron
, vol.32
, pp. 2211-2217
-
-
Shioiri, T.1
Yokoyama, Y.2
Kasai, Y.3
Yamada, S.4
-
28
-
-
0022648097
-
Capillary gas-liquid or thin-layer chromatographic resolution of 2-hydroxy-fatty acid enantiomers
-
Beneytout, J. L., M. Tixier, and M. Rigaud. 1986. Capillary gas-liquid or thin-layer chromatographic resolution of 2-hydroxy-fatty acid enantiomers. J. Chromatogr. 351: 363-365.
-
(1986)
J. Chromatogr.
, vol.351
, pp. 363-365
-
-
Beneytout, J.L.1
Tixier, M.2
Rigaud, M.3
-
29
-
-
0017660489
-
Peroxisomes: New aspects of cell physiology and biochemistry
-
Masters, C., and R. Holmes. 1977. Peroxisomes: new aspects of cell physiology and biochemistry. Physiol. Rev. 57: 816-882.
-
(1977)
Physiol. Rev.
, vol.57
, pp. 816-882
-
-
Masters, C.1
Holmes, R.2
-
31
-
-
0016370298
-
Stereochemical aspects of synthetic and naturally occurring 2-hydroxy fatty acids. Their absolute configurations and assays of optical purity
-
Tatsumi, K., Y. Kishimoto, and C. Hignite. 1974. Stereochemical aspects of synthetic and naturally occurring 2-hydroxy fatty acids. Their absolute configurations and assays of optical purity. Arch. Biochem. Biophys. 165: 656-664.
-
(1974)
Arch. Biochem. Biophys.
, vol.165
, pp. 656-664
-
-
Tatsumi, K.1
Kishimoto, Y.2
Hignite, C.3
-
32
-
-
0014332178
-
Lipid composition of the nervous system in Refsum's disease
-
MacBrinn, M., and J. S. O'Brien. 1968. Lipid composition of the nervous system in Refsum's disease. J. Lipid Res. 9: 552-561.
-
(1968)
J. Lipid Res.
, vol.9
, pp. 552-561
-
-
MacBrinn, M.1
O'Brien, J.S.2
-
33
-
-
0030745425
-
Phytanoyl-coenzyme A hydroxylase deficiency - The enzyme defect in Refsum's disease
-
Jansen, G. A., R. J. A. Wanders, P. A. Watkins, and S. J. Mihalik. 1997. Phytanoyl-coenzyme A hydroxylase deficiency - the enzyme defect in Refsum's disease. N. Engl. J. Med. 337: 133-134.
-
(1997)
N. Engl. J. Med.
, vol.337
, pp. 133-134
-
-
Jansen, G.A.1
Wanders, R.J.A.2
Watkins, P.A.3
Mihalik, S.J.4
-
34
-
-
0027289172
-
Identification of phytanoyl-CoA ligase as a distinct acyl-CoA ligase in peroxisomes from cultured human skin fibroblasts
-
Pahan, K., J. Cofer, P. Baliga, and I. Singh. 1993. Identification of phytanoyl-CoA ligase as a distinct acyl-CoA ligase in peroxisomes from cultured human skin fibroblasts. FEBS Lett. 322: 101-104.
-
(1993)
FEBS Lett.
, vol.322
, pp. 101-104
-
-
Pahan, K.1
Cofer, J.2
Baliga, P.3
Singh, I.4
-
35
-
-
0028168473
-
Activation of 3-methyl-branched fatty acids in rat liver
-
Vanhooren, J. C. T., S. Asselberghs, H. J. Eyssen, G. P. Mannaerts, and P. P. Van Veldhoven. 1994. Activation of 3-methyl-branched fatty acids in rat liver. Int. J. Biochem. 26: 1095-1101.
-
(1994)
Int. J. Biochem.
, vol.26
, pp. 1095-1101
-
-
Vanhooren, J.C.T.1
Asselberghs, S.2
Eyssen, H.J.3
Mannaerts, G.P.4
Van Veldhoven, P.P.5
-
36
-
-
0030482318
-
Phytanic activation in rat liver peroxisomes is catalyzed by long-chain acyl-CoA synthetase
-
Watkins, P. A., A. E. Howard, S. J. Gould, J. Avigan, and S. J. Mihalik. 1996. Phytanic activation in rat liver peroxisomes is catalyzed by long-chain acyl-CoA synthetase. J. Lipid Res. 37: 2288-2295.
-
(1996)
J. Lipid Res.
, vol.37
, pp. 2288-2295
-
-
Watkins, P.A.1
Howard, A.E.2
Gould, S.J.3
Avigan, J.4
Mihalik, S.J.5
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