Alpha-oxidation of 3-methyl-substituted fatty acids and its thiamine dependence

European Journal of Biochemistry

Volumn 270, Issue 8, 2003, Pages 1619-1627

  Casteels, Minne ^a   Foulon, Veerle ^a   Mannaerts, Guy P ^a   Van Veldhoven, Paul P ^a  

^a UNIVERSITY OF LEUVEN   (Belgium)

Author keywords

Adult Refsum Disease; Alpha oxidation; Lyase; Peroxisomes; Thiamine pyrophosphate

Indexed keywords

2 HYDROXYPHYTANOYL COENZYME A LYASE; ACYL COENZYME A; ALDEHYDE; ALDEHYDE DEHYDROGENASE; COCARBOXYLASE; COENZYME A; COMPLEMENTARY DNA; FATTY ACID; LONG CHAIN FATTY ACID COENZYME A LIGASE; OXYTHIAMINE; PHYTANIC ACID; PHYTANOYL COENZYME A HYDROXYLASE; UNCLASSIFIED DRUG;

AMINO ACID SEQUENCE; DEGRADATION; ENZYME ACTIVITY; ENZYME SPECIFICITY; ENZYMOLOGY; GENE MAPPING; GENETIC CODE; HUMAN; HYDROGENATION; HYDROXYLATION; MITOCHONDRION; MUTATION; NONHUMAN; OXIDATION; PATHOPHYSIOLOGY; PEROXISOME; PRIORITY JOURNAL; REFSUM DISEASE; REVIEW; STEREOSPECIFICITY;

AMINO ACID SEQUENCE; ANIMALS; FATTY ACIDS; HUMANS; METHYLATION; MIXED FUNCTION OXYGENASES; MOLECULAR SEQUENCE DATA; OXIDATION-REDUCTION; PHYTANIC ACID; SEQUENCE ALIGNMENT; SEQUENCE HOMOLOGY, AMINO ACID; STEREOISOMERISM; THIAMINE;

MAMMALIA;

EID: 0038409903     PISSN: 00142956     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1432-1033.2003.03534.x     Document Type: Review

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