Antioxidant defences in cybrids harboring mtDNA mutations associated with Leber's hereditary optic neuropathy

FEBS Journal

Volumn 272, Issue 5, 2005, Pages 1124-1135

  Floreani, Maura ^a   Napoli, Eleonora ^a,b   Martinuzzi, Andrea ^b   Pantano, Giorgia ^b   De Riva, Valentina ^b   Trevisan, Roberta ^a,b   Bisetto, Elena ^a,b   Valente, Lucia ^a   Carelli, Valerio ^c   Dabbeni Sala, Federica ^a  

^a UNIVERSITY OF PADOVA   (Italy)

^b SCIENTIFIC INSTITUTE   (Italy)

^c UNIVERSITY OF BOLOGNA   (Italy)

Author keywords

Antioxidant enzymes; Galactose medium; GSH and GSSG; Leber's hereditary optic neuropathy (LHON) cybrids; Oxidative stress

Indexed keywords

COPPER ZINC SUPEROXIDE DISMUTASE; FREE RADICAL; GALACTOSE; GLUCOSE; GLUTATHIONE; GLUTATHIONE DISULFIDE; GLUTATHIONE PEROXIDASE; GLUTATHIONE REDUCTASE; MANGANESE SUPEROXIDE DISMUTASE; MITOCHONDRIAL DNA; REACTIVE OXYGEN METABOLITE; SUPEROXIDE DISMUTASE;

ANTIOXIDANT ACTIVITY; APOPTOSIS; ARTICLE; CONTROLLED STUDY; CYBRID; ENZYME ACTIVITY; HUMAN; HUMAN CELL; LEBER HEREDITARY OPTIC NEUROPATHY; MITOCHONDRION; OXIDATIVE STRESS; POINT MUTATION; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; RESTRICTION FRAGMENT LENGTH POLYMORPHISM; WESTERN BLOTTING;

ANTIOXIDANTS; CASE-CONTROL STUDIES; CATALASE; CELLS, CULTURED; DNA MUTATIONAL ANALYSIS; DNA, MITOCHONDRIAL; FIBROBLASTS; GALACTOSE; GLUCOSE; GLUTATHIONE; GLUTATHIONE PEROXIDASE; GLUTATHIONE REDUCTASE; HUMANS; HYBRID CELLS; MITOCHONDRIA; MUTATION; OPTIC ATROPHY, HEREDITARY, LEBER; OXYGEN; SKIN; SUPEROXIDE DISMUTASE;

EID: 20044381305     PISSN: 1742464X     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1742-4658.2004.04542.x     Document Type: Article

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