Progressive abnormalities in skeletal muscle and neuromuscular junctions of transgenic mice expressing the Huntington's disease mutation

European Journal of Neuroscience

Volumn 20, Issue 11, 2004, Pages 3092-3114

  Ribchester, Richard R ^a   Thomson, Derek ^a   Wood, Nigel I ^b   Hinks, Tim ^b   Gillingwater, Thomas H ^a   Wishart, Thomas M ^a   Court, Felipe A ^a   Morton, A Jennifer ^b  

^a UNIVERSITY OF EDINBURGH   (United Kingdom)

^b UNIVERSITY OF CAMBRIDGE   (United Kingdom)

Author keywords

Atrophy; Electrophysiology; Huntington's disease; Neuromuscular junction; R6 2 mice; Skeletal muscle

Indexed keywords

HUNTINGTIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DEGENERATIVE DISEASE; DENERVATION; ELECTROPHYSIOLOGY; GENE MUTATION; HUNTINGTON CHOREA; MINIATURE ENDPLATE POTENTIAL; MOLECULAR CLONING; MOTONEURON; MOTOR DYSFUNCTION; MOUSE; MUSCLE INNERVATION; NERVE DEGENERATION; NERVE REGENERATION; NERVE SPROUTING; NEUROMUSCULAR SYNAPSE; NEUROTRANSMITTER RELEASE; NONHUMAN; PRIORITY JOURNAL; PROGRESSIVE MUSCULAR ATROPHY; SKELETAL MUSCLE;

ACETYLCHOLINE; AGE FACTORS; ANIMALS; ATROPINE; BUNGAROTOXINS; CALCIUM CHANNEL BLOCKERS; CHOLINESTERASES; CONOTOXINS; DIHYDROLIPOAMIDE DEHYDROGENASE; DISEASE MODELS, ANIMAL; ELECTRIC STIMULATION; ELECTROMYOGRAPHY; EXCITATORY POSTSYNAPTIC POTENTIALS; FEMALE; FLUORESCENT ANTIBODY TECHNIQUE; HUMANS; HUNTINGTON DISEASE; LORDOSIS; MALE; MEMBRANE GLYCOPROTEINS; MEMBRANE POTENTIALS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MICROSCOPY, ELECTRON, TRANSMISSION; MUSCARINIC ANTAGONISTS; MUSCLE FIBERS; MUSCLE, SKELETAL; MUTATION; NERVE TISSUE PROTEINS; NEUROFILAMENT PROTEINS; NEUROMUSCULAR JUNCTION; S100 PROTEINS; TIME FACTORS; TRINUCLEOTIDE REPEAT EXPANSION; UBIQUITIN;

EID: 10844273236     PISSN: 0953816X     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1460-9568.2004.03783.x     Document Type: Article

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