Interference of Crx-dependent transcription by ataxin-7 involves interaction between th glutamine regions and requires the ataxin-7 carboxy-terminal region for nuclear localization

Human Molecular Genetics

Volumn 13, Issue 1, 2004, Pages 53-67

  Chen, Shiming ^a   Peng, Guang Hua ^a   Wang, Xuejiao ^a,c   Smith, Annette C ^b   Grote, Sara K ^b   Sopher, Bryce L ^b   La Spada, Albert R ^b  

^a WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF WASHINGTON MEDICAL CENTER   (United States)

^c JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ATAXIN 7; BRAIN PROTEIN; GLUTAMINE; HOMEODOMAIN PROTEIN; MUTANT PROTEIN; POLYGLUTAMINE; TRANSCRIPTION FACTOR CRX; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BINDING SITE; CARBOXY TERMINAL SEQUENCE; CELL ASSAY; CELL NUCLEUS; CHROMATIN; CONTROLLED STUDY; CORRELATION ANALYSIS; ENHANCER REGION; GENE CONTROL; GENE EXPRESSION; GENE REPRESSION; GENETIC TRANSCRIPTION; IMMUNOPRECIPITATION; IN VIVO STUDY; MOUSE; MUTATION; NONHUMAN; PATHOGENESIS; PEPTIDE MAPPING; PHOTORECEPTOR; POINT MUTATION; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN ANALYSIS; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN PROTEIN INTERACTION; PROTEIN STABILITY; RETINA DEGENERATION; RETINA DYSTROPHY; SPINOCEREBELLAR DEGENERATION; TRANSACTIVATION; TRANSCRIPTION REGULATION; TRANSGENIC MOUSE;

ANIMALS; BETA-GALACTOSIDASE; BLOTTING, WESTERN; CELL NUCLEUS; CELLS, CULTURED; DISEASE MODELS, ANIMAL; DNA PRIMERS; GENE EXPRESSION REGULATION; GENETIC VECTORS; GLUTAMINE; HOMEODOMAIN PROTEINS; IMMUNOHISTOCHEMISTRY; LUCIFERASES; MICE; MUTAGENESIS; NERVE TISSUE PROTEINS; PHOTORECEPTORS, VERTEBRATE; PRECIPITIN TESTS; PROTEIN BINDING; PROTEIN STRUCTURE, TERTIARY; RETINAL DEGENERATION; SPINOCEREBELLAR ATAXIAS; TRANS-ACTIVATORS; TRANSCRIPTION, GENETIC; TWO-HYBRID SYSTEM TECHNIQUES;

ANIMALIA; EUKARYOTA; MUS MUSCULUS;

EID: 0347287040     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddh005     Document Type: Article

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