Evaluation of the therapeutic potential of PPARα agonists for X-linked adrenoleukodystrophy

Molecular Genetics and Metabolism

Volumn 80, Issue 4, 2003, Pages 398-407

  Rampler, Heidelinde ^a   Weinhofer, Isabelle ^a   Netik, Angela ^a   Forss Petter, Sonja ^a   Brown, Peter J ^b   Oplinger, Jeffrey A ^b   Bugaut, Maurice ^c   Berger, Johannes ^a  

^a UNIVERSITY OF VIENNA   (Austria)

^b GLAXOSMITHKLINE   (United States)

^c UNIVERSITÉ DE BOURGOGNE   (France)

Author keywords

Abcd2; Adrenal glands; Brain; Fibrates; GW 6867; GW 7647; PPAR ; PPAR deficient mice; SREBP; Tetradecylthioacetic acid

Indexed keywords

ADRENOLEUKODYSTROPHY RELATED PROTEIN; BEZAFIBRATE; CLOFIBRIC ACID; FENOFIBRATE; FENOFIBRIC ACID; FIBRIC ACID DERIVATIVE; GW 6867; GW 7647; LUCIFERASE; MEMBRANE PROTEIN; MESSENGER RNA; PEROXISOME PROLIFERATOR; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR AGONIST; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR ALPHA; STEROL REGULATORY ELEMENT BINDING PROTEIN; TETRADECYLTHIOACETIC ACID; UNCLASSIFIED DRUG;

ADRENAL GLAND; ADRENOLEUKODYSTROPHY; AMINO ACID SEQUENCE; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; ASSAY; BRAIN; CONTROLLED STUDY; DNA FLANKING REGION; DOWN REGULATION; DRUG POTENCY; DRUG SELECTIVITY; GENE EXPRESSION; INTRON; LIVER; MALE; MOUSE; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN DEFICIENCY; PROTEIN DETERMINATION; PROTEIN EXPRESSION; PROTEIN INDUCTION; TESTIS; X CHROMOSOME LINKAGE;

RODENTIA;

EID: 0344493778     PISSN: 10967192     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ymgme.2003.09.002     Document Type: Article

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