Lovastatin and sodium phenylacetate normalize the levels of very long chain fatty acids in skin fibroblasts of X-adrenoleukodystrophy

FEBS Letters

Volumn 426, Issue 3, 1998, Pages 342-346

  Singh, Inderjit ^a   Pahan, Kalipada ^a   Khan, Mushfiquddin ^a  

^a MEDICAL UNIVERSITY OF SOUTH CAROLINA   (United States)

Author keywords

Adrenoleukodystrophy; Beta oxidation; Lovastatin; Phenylacetate; Very long chain fatty acid

Indexed keywords

MEVINOLIN; PHENYLACETIC ACID DERIVATIVE; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; ARTICLE; CONTROLLED STUDY; FATTY ACID OXIDATION; GENE DELETION; HUMAN; HUMAN CELL; PRIORITY JOURNAL; SKIN FIBROBLAST;

ADRENOLEUKODYSTROPHY; CELLS, CULTURED; DRUG SYNERGISM; FATTY ACIDS; FIBROBLASTS; GENE DELETION; HUMANS; INTRACELLULAR FLUID; LOVASTATIN; MEVALONIC ACID; OXIDATION-REDUCTION; PHENYLACETATES; SKIN; X CHROMOSOME;

EID: 0032562653     PISSN: 00145793     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0014-5793(98)00370-6     Document Type: Article

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