Alterations in desmosome size and number coincide with the loss of keratinocyte cohesion in skin with homozygous and heterozygous defects in the desmosomal protein plakophilin 1

Journal of Investigative Dermatology

Volumn 121, Issue 1, 2003, Pages 96-103

  McMillan, James R ^a   Haftek, Marek ^b   Akiyama, Masashi ^a   South, Andrew P ^c   Perrot, Henri ^d   McGrath, John A ^c   Eady, Robin A J ^c   Shimizu, Hiroshi ^a  

^a HOKKAIDO UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^b EDOUARD HERRIOT HOSPITAL   (France)

^c KING'S COLLEGE LONDON   (United Kingdom)

^d Clinical Psychology Unit   (France)

Author keywords

Cell cell adhesion; Desmosome; Electron microscopy; Genodermatosis; Intermediate filaments

Indexed keywords

DESMOGLEIN 1; MEMBRANE PROTEIN; PLAKOPHILIN 1; UNCLASSIFIED DRUG;

ARTICLE; CELL ADHESION; CLINICAL ARTICLE; CONTROLLED STUDY; DESMOSOME; ECTODERMAL DYSPLASIA; ELECTRON MICROSCOPY; HUMAN; HUMAN TISSUE; INTERMEDIATE FILAMENT; KERATINOCYTE; PRIORITY JOURNAL; PROTEIN DEFECT;

EID: 0041342100     PISSN: 0022202X     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1523-1747.2003.12324.x     Document Type: Article

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