Phytanic acid α-oxidation in man: Identification of 2-hydroxyphytanoyl-CoA lyase, a peroxisomal enzyme with normal activity in Zellweger syndrome

Journal of Inherited Metabolic Disease

Volumn 23, Issue 4, 2000, Pages 421-424

  Jansen, G A ^a   Denis, S ^a   Verhoeven, N M ^b   Jakobs, C ^b   Wanders, R J A ^a  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

^b VU UNIVERSITY AMSTERDAM   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

2 HYDROXYPHYTANOYL COA LYASE; CATALASE; LYASE; PHYTANIC ACID; UNCLASSIFIED DRUG;

BIOGENESIS; CASE REPORT; CONFERENCE PAPER; CONTROLLED STUDY; ENZYME ACTIVITY; HUMAN; HUMAN TISSUE; IMMUNOFLUORESCENCE; LIVER; OXIDATION; PEROXISOME; ZELLWEGER SYNDROME;

CARBON-CARBON LYASES; HUMANS; LIVER; MALE; OXIDATION-REDUCTION; PEROXISOMES; PHYTANIC ACID; ZELLWEGER SYNDROME;

EID: 0034044461     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005672406773     Document Type: Conference Paper

References (11)

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