Phytanoyl-CoA hydroxylase is present in human liver, located in peroxisomes, and deficient in Zellweger syndrome: Direct, unequivocal evidence for the new, revised pathway of phytanic acid α-oxidation in humans

Biochemical and Biophysical Research Communications

Volumn 229, Issue 1, 1996, Pages 205-210

  Jansen, G A ^a,b   Mihalik, S J ^c   Watkins, P A ^c   Moser, H W ^c   Jakobs, C ^d   Denis, S ^b   Wanders, R J A ^a,b  

^a EMMA CHILDREN S HOSPITAL   (Netherlands)

^b UNIVERSITY OF AMSTERDAM   (Netherlands)

^c JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d VU UNIVERSITY AMSTERDAM   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

OXYGENASE; PHYTANIC ACID; PHYTANOYL COENZYME A HYDROXYLASE; UNCLASSIFIED DRUG;

ARTICLE; CONTROLLED STUDY; FATTY ACID OXIDATION; HUMAN; HUMAN TISSUE; LIVER; PEROXISOME; PRIORITY JOURNAL; ZELLWEGER SYNDROME;

EID: 0030569533     PISSN: 0006291X     EISSN: None     Source Type: Journal    
DOI: 10.1006/bbrc.1996.1781     Document Type: Article

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