Cellular and molecular aspects of Zellweger syndrome and other peroxisome biogenesis disorders

Cellular and Molecular Life Sciences

Volumn 59, Issue 6, 2002, Pages 1058-1069

  Brosius, U ^a   Gartner J ^a  

^a HEINRICH HEINE UNIVERSITY   (Germany)

Author keywords

Peroxin; Peroxisome; Peroxisome biogenesis; Peroxisome biogenesis disorder; PEX gene; Zellweger syndrome

Indexed keywords

BILE ACID; HYDROGEN PEROXIDE; PLASMALOGEN; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; AUTOSOMAL RECESSIVE DISORDER; CELL ORGANELLE; DISORDERS OF PEROXISOMAL FUNCTIONS; FATTY ACID OXIDATION; GENE MUTATION; HUMAN; PEROXISOME; REVIEW; X CHROMOSOME LINKED DISORDER; ZELLWEGER SYNDROME;

HUMANS; PEROXISOMAL DISORDERS; PEROXISOMES; ZELLWEGER SYNDROME;

EUKARYOTA;

EID: 0036305188     PISSN: 1420682X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00018-002-8486-7     Document Type: Review

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