A common Dubin-Johnson syndrome mutation impairs protein maturation and transport activity of MRP2 (ABCC2)

American Journal of Physiology - Gastrointestinal and Liver Physiology

Volumn 284, Issue 1 47-1, 2003, Pages

  Keitel, Verena ^a   Nies, Anne T ^a   Brom, Manuela ^a   Hummel Eisenbeiss, Johanna ^a   Spring, Herbert ^a   Keppler, Dietrich ^a  

^a GERMAN CANCER RESEARCH CENTER DKFZ   (Germany)

Author keywords

ATP dependent transport; Deficient protein maturation; Multidrug resistance protein 2; Protein trafficking

Indexed keywords

ADENOSINE TRIPHOSPHATE; COMPLEMENTARY DNA; ISOLEUCINE; LEUKOTRIENE C4; MULTIDRUG RESISTANCE PROTEIN 2; MUTANT PROTEIN; PHENYLALANINE; PROTEASOME;

AMINO ACID SUBSTITUTION; APICAL MEMBRANE; ARTICLE; CELL MEMBRANE; CONTROLLED STUDY; DISEASE ASSOCIATION; DUBIN JOHNSON SYNDROME; ENDOPLASMIC RETICULUM; GENE MUTATION; HEPATOBILIARY SYSTEM; HUMAN; HUMAN CELL; HYPERBILIRUBINEMIA; LIVER CELL; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN LOCALIZATION; PROTEIN PROCESSING; PROTEIN TRANSPORT; QUANTITATIVE ANALYSIS;

EID: 0037229540     PISSN: 01931857     EISSN: None     Source Type: Journal    
DOI: 10.1152/ajpgi.00362.2002     Document Type: Article

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