Cystic fibrosis F508del patients have apically localized CFTR in a reduced number of airway cells

Laboratory Investigation

Volumn 80, Issue 6, 2000, Pages 857-868

  Penque, Deborah ^a   Mendes, Filipa ^a   Beck, Sebastian ^a   Farinha, Carlos ^a,b   Pacheco, Paula ^a   Nogueira, Paulo ^a   Lavinha, João ^a   Malhó, Rui ^b   Amaral, Margarida D ^a,b  

^a NATIONAL INSTITUTE OF HEALTH DR RICARDO JORGE   (Portugal)

^b UNIVERSITY OF LISBON   (Portugal)

Author keywords

[No Author keywords available]

Indexed keywords

ANTIBODY; CALNEXIN; PROTEIN DERIVATIVE; TRANSMEMBRANE CONDUCTANCE REGULATOR; TUBULIN;

AIRWAY; ARTICLE; CELL COUNT; CELLULAR DISTRIBUTION; COLUMNAR EPITHELIUM; CONTROLLED STUDY; CYSTIC FIBROSIS; EPITHELIUM CELL; GENE MUTATION; HUMAN; HUMAN CELL; NOSE MUCOSA; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LOCALIZATION;

EID: 0033918281     PISSN: 00236837     EISSN: None     Source Type: Journal    
DOI: 10.1038/labinvest.3780090     Document Type: Article

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